{"id":"https://openalex.org/W2397414229","doi":null,"title":"[Treatment of juvenile pemphigus vulgaris with intravenous immunoglobulins].","display_name":"[Treatment of juvenile pemphigus vulgaris with intravenous immunoglobulins].","publication_year":2005,"publication_date":"2005-01-01","ids":{"openalex":"https://openalex.org/W2397414229","mag":"2397414229","pmid":"https://pubmed.ncbi.nlm.nih.gov/16279438"},"language":"sk","primary_location":{"id":"pmid:16279438","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/16279438","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Casopis lekaru ceskych","raw_type":"Case Reports"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5082631560","display_name":"Z Sz\u00e9p","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210100771","display_name":"N\u00e1rodn\u00fd \u00fastav detsk\u00fdch chor\u00f4b","ror":"https://ror.org/0166xf875","country_code":"SK","type":"healthcare","lineage":["https://openalex.org/I4210100771"]}],"countries":["SK"],"is_corresponding":false,"raw_author_name":"Z Sz\u00e9p","raw_affiliation_strings":["Detsk\u00e1 kon\u00e1 klinika LFUK a DFNsP, Bratislava, SR. zoltanszep@atlas.cz","Detsk\u00e1 kon\u00e1 klinika LFUK a DFNsP, Bratislava, SR"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Detsk\u00e1 kon\u00e1 klinika LFUK a DFNsP, Bratislava, SR. zoltanszep@atlas.cz","institution_ids":["https://openalex.org/I4210100771"]},{"raw_affiliation_string":"Detsk\u00e1 kon\u00e1 klinika LFUK a DFNsP, Bratislava, SR","institution_ids":["https://openalex.org/I4210100771"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5000466859","display_name":"T Danilla","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"T Danilla","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5078147432","display_name":"D Buchvald","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"D Buchvald","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.7925,"has_fulltext":false,"cited_by_count":10,"citation_normalized_percentile":{"value":0.76412231,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"144","issue":"10","first_page":"700","last_page":"3"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11730","display_name":"Autoimmune Bullous Skin Diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11730","display_name":"Autoimmune Bullous Skin Diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11650","display_name":"Skin and Cellular Biology Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/1307","display_name":"Cell Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11117","display_name":"Drug-Induced Adverse Reactions","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2736","display_name":"Pharmacology (medical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/intravenous-immunoglobulin","display_name":"intravenous immunoglobulin","score":0.890999972820282},{"id":"https://openalex.org/keywords/prednisone","display_name":"prednisone","score":0.8899999856948853},{"id":"https://openalex.org/keywords/azathioprine","display_name":"azathioprine","score":0.9390000104904175},{"id":"https://openalex.org/keywords/dapsone","display_name":"dapsone","score":0.9990000128746033},{"id":"https://openalex.org/keywords/immunosuppressive-therapy","display_name":"immunosuppressive therapy","score":0.9269999861717224},{"id":"https://openalex.org/keywords/autoimmune-blistering-disease","display_name":"autoimmune blistering disease","score":0.8389999866485596},{"id":"https://openalex.org/keywords/pediatric-autoimmune-disease","display_name":"pediatric autoimmune disease","score":0.6100000143051147},{"id":"https://openalex.org/keywords/remission","display_name":"remission","score":0.6010000109672546}],"concepts":[{"id":"https://openalex.org/C2776760755","wikidata":"https://www.wikidata.org/wiki/Q18939","display_name":"Azathioprine","level":3,"score":0.9363468885421753},{"id":"https://openalex.org/C2778720950","wikidata":"https://www.wikidata.org/wiki/Q424972","display_name":"Prednisone","level":2,"score":0.932725191116333},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9172238707542419},{"id":"https://openalex.org/C2781313415","wikidata":"https://www.wikidata.org/wiki/Q3899001","display_name":"Pemphigus vulgaris","level":2,"score":0.7684471607208252},{"id":"https://openalex.org/C197934379","wikidata":"https://www.wikidata.org/wiki/Q2047938","display_name":"Adverse effect","level":2,"score":0.6723249554634094},{"id":"https://openalex.org/C2777640609","wikidata":"https://www.wikidata.org/wiki/Q422226","display_name":"Dapsone","level":2,"score":0.6305018663406372},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.4514349102973938},{"id":"https://openalex.org/C115961737","wikidata":"https://www.wikidata.org/wiki/Q1516282","display_name":"Juvenile","level":2,"score":0.4359106719493866},{"id":"https://openalex.org/C500440147","wikidata":"https://www.wikidata.org/wiki/Q701216","display_name":"Pharmacotherapy","level":2,"score":0.43090397119522095},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.38566315174102783},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.3655095398426056},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.32494354248046875},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.28377753496170044},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.2438739836215973},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.0},{"id":"https://openalex.org/C54355233","wikidata":"https://www.wikidata.org/wiki/Q7162","display_name":"Genetics","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000293","descriptor_name":"Adolescent","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001379","descriptor_name":"Azathioprine","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D004334","descriptor_name":"Drug Administration Schedule","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D004359","descriptor_name":"Drug Therapy, Combination","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005938","descriptor_name":"Glucocorticoids","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007166","descriptor_name":"Immunosuppressive Agents","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D010392","descriptor_name":"Pemphigus","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":true},{"descriptor_ui":"D011241","descriptor_name":"Prednisone","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D016756","descriptor_name":"Immunoglobulins, Intravenous","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":true}],"locations_count":2,"locations":[{"id":"pmid:16279438","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/16279438","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Casopis lekaru ceskych","raw_type":"Case Reports"},{"id":"mag:2397414229","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/16279438","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W3024129816","https://openalex.org/W1967293052","https://openalex.org/W2125076165","https://openalex.org/W2158319513","https://openalex.org/W1512160773","https://openalex.org/W2053730359","https://openalex.org/W3031370091","https://openalex.org/W2073248850","https://openalex.org/W2397006494","https://openalex.org/W7054577184"],"abstract_inverted_index":{"Juvenile":[0],"pemphigus":[1],"vulgaris":[2],"(JPV)":[3],"is":[4,10,40],"a":[5,41,90],"rare":[6],"autoimmune":[7],"disease.":[8,168],"It":[9],"treated":[11],"by":[12],"different":[13],"immunosuppressive":[14,60,228],"drugs,":[15],"which":[16,218],"may":[17],"have":[18],"serious":[19,233],"side":[20],"effects.":[21,235],"Such":[22],"problems":[23],"are":[24],"most":[25],"apparent":[26],"in":[27,73,89,165,217],"the":[28,55,58,67,100,133,147,151,167,197,203,223],"therapy":[29,69,131,154,220],"of":[30,36,57,70,80,92,102,135,149,155,170,176,191,199,212,227,232],"children":[31],"and":[32,43,46,82,125,157,183,193,214],"adolescents.":[33],"The":[34,62,77,110],"use":[35,207],"intravenous":[37],"immunoglobulins":[38],"(IVIG)":[39],"safe":[42],"effective":[44],"method":[45],"therefore":[47],"it":[48,115,121,162],"can":[49,221],"replace":[50],"or":[51],"at":[52],"least":[53],"postpone":[54],"initiation":[56],"combined":[59],"therapy.":[61],"article":[63],"reports":[64],"experience":[65,202],"with":[66,99,173,230],"IVIG":[68,81,86,130,192,208],"severe":[71],"JPV":[72,171],"16-year-old":[74],"female":[75],"patient.":[76],"double":[78,152],"combination":[79,153,175],"prednisone":[83,136,156,177,194],"was":[84,113,122,159,163,187],"used.":[85],"were":[87,108],"administered":[88],"dose":[91,134],"400":[93],"mg/kg/day":[94],"during":[95],"three":[96],"consecutive":[97],"days":[98],"intervals":[101],"1-2":[103,128],"months.":[104,129],"Totally":[105],"5":[106],"cycles":[107],"applied.":[109],"therapeutic":[111],"effect":[112],"excellent,":[114],"started":[116],"within":[117],"few":[118],"days,":[119],"but":[120,161],"only":[123],"temporary":[124],"lasted":[126],"for":[127,210,225],"enabled":[132],"to":[137,143,189,206],"be":[138],"reduced":[139],"from":[140],"50":[141],"mg/day":[142],"15":[144],"mg/day.":[145],"Following":[146],"cessation":[148],"IVIG,":[150],"azathioprine":[158,180],"initiated,":[160],"unsuccessful":[164],"controlling":[166],"Remission":[169],"achieved":[172],"triple":[174],"(25":[178],"mg/day),":[179],"(100":[181],"mg/day)":[182,186],"dapsone":[184],"(50":[185],"comparable":[188],"that":[190],"combination.":[195],"On":[196],"basis":[198],"their":[200],"positive":[201],"authors":[204],"recommend":[205],"also":[209],"cases":[211],"childhood":[213],"juvenile":[215],"pemphigus,":[216],"this":[219],"delay":[222],"need":[224],"administration":[226],"drugs":[229],"potential":[231],"adverse":[234]},"counts_by_year":[{"year":2022,"cited_by_count":1},{"year":2017,"cited_by_count":1},{"year":2014,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
