{"id":"https://openalex.org/W2310695844","doi":"https://doi.org/10.1302/0301-620x.76b5.8083268","title":"Spinal deformity in Ehlers-Danlos syndrome. Five patients treated by spinal fusion","display_name":"Spinal deformity in Ehlers-Danlos syndrome. Five patients treated by spinal fusion","publication_year":1994,"publication_date":"1994-09-01","ids":{"openalex":"https://openalex.org/W2310695844","doi":"https://doi.org/10.1302/0301-620x.76b5.8083268","mag":"2310695844","pmid":"https://pubmed.ncbi.nlm.nih.gov/8083268"},"language":"en","primary_location":{"id":"doi:10.1302/0301-620x.76b5.8083268","doi":"https://doi.org/10.1302/0301-620x.76b5.8083268","is_oa":false,"landing_page_url":"https://doi.org/10.1302/0301-620x.76b5.8083268","pdf_url":null,"source":{"id":"https://openalex.org/S4210168313","display_name":"Journal of Bone and Joint Surgery - British Volume","issn_l":"0301-620X","issn":["0301-620X","0968-7300","2044-5377"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310311815","host_organization_name":"British Editorial Society of Bone & Joint Surgery","host_organization_lineage":["https://openalex.org/P4310311815"],"host_organization_lineage_names":["British Editorial Society of Bone & Joint Surgery"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of Bone and Joint Surgery. British volume","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5029310963","display_name":"MJ McMaster","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2800936732","display_name":"Princess Margaret Rose Orthopaedic Hospital","ror":"https://ror.org/01ha5h612","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I2800936732"]}],"countries":["GB"],"is_corresponding":true,"raw_author_name":"MJ McMaster","raw_affiliation_strings":["Consultant Spine Surgeon Princess Margaret Rose Orthopaedic Hospital, Fairmilehead, Edinburgh EH1O 7ED, UK","From the Princess Margaret Rose Orthopaedic Hospital, Edinburgh, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Consultant Spine Surgeon Princess Margaret Rose Orthopaedic Hospital, Fairmilehead, Edinburgh EH1O 7ED, UK","institution_ids":["https://openalex.org/I2800936732"]},{"raw_affiliation_string":"From the Princess Margaret Rose Orthopaedic Hospital, Edinburgh, Scotland","institution_ids":["https://openalex.org/I2800936732"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5029310963"],"corresponding_institution_ids":["https://openalex.org/I2800936732"],"apc_list":null,"apc_paid":null,"fwci":0.8697,"has_fulltext":false,"cited_by_count":54,"citation_normalized_percentile":{"value":0.77215365,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":97},"biblio":{"volume":"76-B","issue":"5","first_page":"773","last_page":"777"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11030","display_name":"Scoliosis diagnosis and treatment","score":0.9951000213623047,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11030","display_name":"Scoliosis diagnosis and treatment","score":0.9951000213623047,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11310","display_name":"Connective tissue disorders research","score":0.003800000064074993,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12830","display_name":"Pectus Deformity Diagnosis and Treatment","score":0.00039999998989515007,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/ehlers-danlos-syndrome","display_name":"Ehlers-Danlos syndrome","score":0.9919999837875366},{"id":"https://openalex.org/keywords/spinal-deformity","display_name":"spinal deformity","score":0.9829999804496765},{"id":"https://openalex.org/keywords/scoliosis","display_name":"scoliosis","score":0.9480000138282776},{"id":"https://openalex.org/keywords/thoracic-kyphosis","display_name":"thoracic kyphosis","score":0.8709999918937683},{"id":"https://openalex.org/keywords/spinal-fusion","display_name":"spinal fusion","score":0.843999981880188},{"id":"https://openalex.org/keywords/posterior-spinal-fusion","display_name":"posterior spinal fusion","score":0.7179999947547913},{"id":"https://openalex.org/keywords/collagen-vi","display_name":"collagen VI","score":0.6970000267028809},{"id":"https://openalex.org/keywords/connective-tissue-diseases","display_name":"connective tissue diseases","score":0.6230000257492065},{"id":"https://openalex.org/keywords/surgical-complications","display_name":"surgical complications","score":0.3840000033378601},{"id":"https://openalex.org/keywords/hematoma","display_name":"hematoma","score":0.6499999761581421},{"id":"https://openalex.org/keywords/wound-dehiscence","display_name":"wound dehiscence","score":0.8489999771118164}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9023212790489197},{"id":"https://openalex.org/C2780955175","wikidata":"https://www.wikidata.org/wiki/Q174857","display_name":"Scoliosis","level":2,"score":0.7635335326194763},{"id":"https://openalex.org/C2778333328","wikidata":"https://www.wikidata.org/wiki/Q1141499","display_name":"Ehlers\u2013Danlos syndrome","level":2,"score":0.7208555936813354},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.7086150050163269},{"id":"https://openalex.org/C2780375110","wikidata":"https://www.wikidata.org/wiki/Q770609","display_name":"Spinal fusion","level":2,"score":0.5581595301628113},{"id":"https://openalex.org/C139812875","wikidata":"https://www.wikidata.org/wiki/Q3704821","display_name":"Dehiscence","level":2,"score":0.5482490658760071},{"id":"https://openalex.org/C2779418094","wikidata":"https://www.wikidata.org/wiki/Q478389","display_name":"Kyphosis","level":3,"score":0.5184061527252197},{"id":"https://openalex.org/C44575665","wikidata":"https://www.wikidata.org/wiki/Q1293405","display_name":"Lumbar","level":2,"score":0.49125975370407104},{"id":"https://openalex.org/C2779982284","wikidata":"https://www.wikidata.org/wiki/Q1182746","display_name":"Deformity","level":2,"score":0.4760732054710388},{"id":"https://openalex.org/C2780913275","wikidata":"https://www.wikidata.org/wiki/Q578786","display_name":"Thoracic vertebrae","level":4,"score":0.43005406856536865},{"id":"https://openalex.org/C2779835254","wikidata":"https://www.wikidata.org/wiki/Q405478","display_name":"Lumbar vertebrae","level":3,"score":0.27305519580841064},{"id":"https://openalex.org/C36454342","wikidata":"https://www.wikidata.org/wiki/Q245341","display_name":"Radiography","level":2,"score":0.1125132143497467}],"mesh":[{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D004535","descriptor_name":"Ehlers-Danlos Syndrome","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005500","descriptor_name":"Follow-Up Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007223","descriptor_name":"Infant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007738","descriptor_name":"Kyphosis","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D007738","descriptor_name":"Kyphosis","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D007738","descriptor_name":"Kyphosis","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":true},{"descriptor_ui":"D012600","descriptor_name":"Scoliosis","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D012600","descriptor_name":"Scoliosis","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D012600","descriptor_name":"Scoliosis","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":true},{"descriptor_ui":"D013123","descriptor_name":"Spinal Fusion","qualifier_ui":"Q000379","qualifier_name":"methods","is_major_topic":true},{"descriptor_ui":"D014945","descriptor_name":"Wound Healing","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016063","descriptor_name":"Blood Loss, Surgical","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1302/0301-620x.76b5.8083268","doi":"https://doi.org/10.1302/0301-620x.76b5.8083268","is_oa":false,"landing_page_url":"https://doi.org/10.1302/0301-620x.76b5.8083268","pdf_url":null,"source":{"id":"https://openalex.org/S4210168313","display_name":"Journal of Bone and Joint Surgery - British Volume","issn_l":"0301-620X","issn":["0301-620X","0968-7300","2044-5377"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310311815","host_organization_name":"British Editorial Society of Bone & Joint Surgery","host_organization_lineage":["https://openalex.org/P4310311815"],"host_organization_lineage_names":["British Editorial Society of Bone & Joint Surgery"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of Bone and Joint Surgery. British volume","raw_type":"journal-article"},{"id":"pmid:8083268","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/8083268","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of bone and joint surgery. British volume","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","score":0.98580002784729,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2047516096","https://openalex.org/W2109502932","https://openalex.org/W2503162852","https://openalex.org/W4313198243","https://openalex.org/W4321112862","https://openalex.org/W132074892","https://openalex.org/W1995154910","https://openalex.org/W2412470338","https://openalex.org/W2065669676","https://openalex.org/W2411252775"],"abstract_inverted_index":{"Five":[0],"patients":[1],"with":[2,61],"classical":[3],"Ehlers-Danlos":[4],"syndrome":[5],"developed":[6,45],"severe":[7],"spinal":[8,96],"deformities.":[9],"Two":[10],"were":[11,53,87],"shown":[12],"to":[13],"have":[14],"type-VI":[15],"collagen":[16],"abnormalities.":[17],"Three":[18],"had":[19,31,38],"a":[20,32,39,67],"double":[21],"structural":[22],"scoliosis":[23,35],"of":[24,49,70],"the":[25,47],"thoracic":[26,34,40],"and":[27,36,52,81,85],"lumbar":[28],"regions,":[29],"one":[30,37],"single":[33],"kyphosis.":[41],"The":[42,95],"curves":[43],"first":[44],"before":[46],"age":[48,69],"four":[50],"years,":[51],"not":[54,91],"controlled":[55,80],"by":[56],"bracing.":[57],"Major":[58],"corrective":[59],"surgery":[60],"posterior":[62],"fusion":[63],"was":[64],"performed":[65],"at":[66],"mean":[68],"11":[71],"years":[72],"8":[73],"months.":[74],"Excessive":[75],"blood":[76],"loss":[77],"could":[78],"be":[79],"although":[82],"wound":[83],"haematoma":[84],"dehiscence":[86],"common,":[88],"they":[89],"did":[90],"provide":[92],"major":[93],"problems.":[94],"fusions":[97],"healed":[98],"satisfactorily.":[99]},"counts_by_year":[{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":3},{"year":2023,"cited_by_count":4},{"year":2022,"cited_by_count":4},{"year":2021,"cited_by_count":1},{"year":2020,"cited_by_count":2},{"year":2019,"cited_by_count":2},{"year":2018,"cited_by_count":2},{"year":2017,"cited_by_count":1},{"year":2016,"cited_by_count":1},{"year":2015,"cited_by_count":3},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":1},{"year":2012,"cited_by_count":3}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
