{"id":"https://openalex.org/W2284005203","doi":"https://doi.org/10.1186/s12969-016-0070-z","title":"Beh\u00e7et\u2019s disease in children, an overview","display_name":"Beh\u00e7et\u2019s disease in children, an overview","publication_year":2016,"publication_date":"2016-02-18","ids":{"openalex":"https://openalex.org/W2284005203","doi":"https://doi.org/10.1186/s12969-016-0070-z","mag":"2284005203","pmid":"https://pubmed.ncbi.nlm.nih.gov/26887984","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/4758175"},"language":"en","primary_location":{"id":"doi:10.1186/s12969-016-0070-z","doi":"https://doi.org/10.1186/s12969-016-0070-z","is_oa":true,"landing_page_url":"https://doi.org/10.1186/s12969-016-0070-z","pdf_url":"https://ped-rheum.biomedcentral.com/track/pdf/10.1186/s12969-016-0070-z","source":{"id":"https://openalex.org/S121831025","display_name":"Pediatric Rheumatology","issn_l":"1546-0096","issn":["1546-0096"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320256","host_organization_name":"BioMed Central","host_organization_lineage":["https://openalex.org/P4310320256","https://openalex.org/P4310319965"],"host_organization_lineage_names":["BioMed Central","Springer Nature"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Rheumatology","raw_type":"journal-article"},"volume":null,"type":"review","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"gold","oa_url":"https://ped-rheum.biomedcentral.com/track/pdf/10.1186/s12969-016-0070-z","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5036816060","display_name":"Isabelle Kon\u00e9\u2010Paut","orcid":"https://orcid.org/0000-0001-8939-5763","observed_orcids":["https://orcid.org/0000-0001-8939-5763"]},"institutions":[{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210162942","display_name":"Bic\u00eatre Hospital","ror":"https://ror.org/05c9p1x46","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210162942","https://openalex.org/I4405259118"]}],"countries":["FR"],"is_corresponding":true,"raw_author_name":"Isabelle Kon\u00e9-Paut","raw_affiliation_strings":["Paediatric Rheumatology, CEREMAI, Bic\u00eatre University Hospital, APHP, Paris SUD, Kremlin bic\u00eatre, France. isabelle.kone-paut@aphp.fr","Paediatric Rheumatology, CEREMAI, Bic\u00eatre University Hospital, APHP, Paris SUD, Kremlin bic\u00eatre, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Paediatric Rheumatology, CEREMAI, Bic\u00eatre University Hospital, APHP, Paris SUD, Kremlin bic\u00eatre, France. isabelle.kone-paut@aphp.fr","institution_ids":["https://openalex.org/I4210097159","https://openalex.org/I4210162942"]},{"raw_affiliation_string":"Paediatric Rheumatology, CEREMAI, Bic\u00eatre University Hospital, APHP, Paris SUD, Kremlin bic\u00eatre, France","institution_ids":["https://openalex.org/I4210097159","https://openalex.org/I4210162942"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5036816060"],"corresponding_institution_ids":["https://openalex.org/I4210097159","https://openalex.org/I4210162942"],"apc_list":{"value":3090,"currency":"USD","value_usd":3090},"apc_paid":{"value":3090,"currency":"USD","value_usd":3090},"fwci":2.5757,"has_fulltext":true,"cited_by_count":177,"citation_normalized_percentile":{"value":0.92449664,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":89,"max":100},"biblio":{"volume":"14","issue":"1","first_page":"10","last_page":"10"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11194","display_name":"Ocular Diseases and Beh\u00e7et\u2019s Syndrome","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11194","display_name":"Ocular Diseases and Beh\u00e7et\u2019s Syndrome","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11571","display_name":"Sarcoidosis and Beryllium Toxicity Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/behcet-s-disease","display_name":"Beh\u00e7et's disease","score":0.9929999709129333},{"id":"https://openalex.org/keywords/pediatric-behcet-s-disease","display_name":"pediatric Beh\u00e7et's disease","score":0.871999979019165},{"id":"https://openalex.org/keywords/vasculitis","display_name":"vasculitis","score":0.9580000042915344},{"id":"https://openalex.org/keywords/oral-ulcers","display_name":"oral ulcers","score":0.9509999752044678},{"id":"https://openalex.org/keywords/fever-of-unknown-origin","display_name":"fever of unknown origin","score":0.996999979019165},{"id":"https://openalex.org/keywords/classification-criteria","display_name":"classification criteria","score":0.746999979019165},{"id":"https://openalex.org/keywords/genetic-susceptibility","display_name":"genetic susceptibility","score":0.5759999752044678},{"id":"https://openalex.org/keywords/neurological-involvement","display_name":"neurological involvement","score":0.7450000047683716},{"id":"https://openalex.org/keywords/ocular-manifestations","display_name":"ocular manifestations","score":0.9919999837875366},{"id":"https://openalex.org/keywords/vascular-involvement","display_name":"vascular involvement","score":0.9010000228881836},{"id":"https://openalex.org/keywords/tnf-alpha-inhibitors","display_name":"TNF-alpha inhibitors","score":0.9150000214576721},{"id":"https://openalex.org/keywords/prognosis","display_name":"prognosis","score":0.5529999732971191},{"id":"https://openalex.org/keywords/sex-differences","display_name":"sex differences","score":0.6150000095367432}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9414587020874023},{"id":"https://openalex.org/C3020580240","wikidata":"https://www.wikidata.org/wiki/Q663272","display_name":"Expert opinion","level":2,"score":0.6610684394836426},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.6428989171981812},{"id":"https://openalex.org/C198451711","wikidata":"https://www.wikidata.org/wiki/Q327657","display_name":"Rheumatology","level":2,"score":0.6260232329368591},{"id":"https://openalex.org/C2776015282","wikidata":"https://www.wikidata.org/wiki/Q644318","display_name":"Vasculitis","level":3,"score":0.6180756092071533},{"id":"https://openalex.org/C2778328719","wikidata":"https://www.wikidata.org/wiki/Q7316771","display_name":"Retinal vasculitis","level":4,"score":0.5717759132385254},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.4841083288192749},{"id":"https://openalex.org/C2781428731","wikidata":"https://www.wikidata.org/wiki/Q911427","display_name":"Behcet's disease","level":3,"score":0.4597061276435852},{"id":"https://openalex.org/C3018415437","wikidata":"https://www.wikidata.org/wiki/Q911427","display_name":"Behcet disease","level":3,"score":0.45551034808158875},{"id":"https://openalex.org/C2781423770","wikidata":"https://www.wikidata.org/wiki/Q265936","display_name":"Kawasaki disease","level":3,"score":0.43617475032806396},{"id":"https://openalex.org/C2776194053","wikidata":"https://www.wikidata.org/wiki/Q280027","display_name":"Uveitis","level":2,"score":0.42820000648498535},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.32449015974998474},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.319859117269516},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.3079599142074585},{"id":"https://openalex.org/C2776820930","wikidata":"https://www.wikidata.org/wiki/Q9655","display_name":"Artery","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D001528","descriptor_name":"Behcet Syndrome","qualifier_ui":"Q000145","qualifier_name":"classification","is_major_topic":true},{"descriptor_ui":"D001528","descriptor_name":"Behcet Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D001528","descriptor_name":"Behcet Syndrome","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":true},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009017","descriptor_name":"Morbidity","qualifier_ui":"Q000639","qualifier_name":"trends","is_major_topic":false},{"descriptor_ui":"D014943","descriptor_name":"Global Health","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D019468","descriptor_name":"Disease Management","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true}],"locations_count":3,"locations":[{"id":"doi:10.1186/s12969-016-0070-z","doi":"https://doi.org/10.1186/s12969-016-0070-z","is_oa":true,"landing_page_url":"https://doi.org/10.1186/s12969-016-0070-z","pdf_url":"https://ped-rheum.biomedcentral.com/track/pdf/10.1186/s12969-016-0070-z","source":{"id":"https://openalex.org/S121831025","display_name":"Pediatric Rheumatology","issn_l":"1546-0096","issn":["1546-0096"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320256","host_organization_name":"BioMed Central","host_organization_lineage":["https://openalex.org/P4310320256","https://openalex.org/P4310319965"],"host_organization_lineage_names":["BioMed Central","Springer Nature"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Rheumatology","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:4758175","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/4758175","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatr Rheumatol Online J","raw_type":"Text"},{"id":"pmid:26887984","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/26887984","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric rheumatology online journal","raw_type":"Journal Article"}],"best_oa_location":{"id":"doi:10.1186/s12969-016-0070-z","doi":"https://doi.org/10.1186/s12969-016-0070-z","is_oa":true,"landing_page_url":"https://doi.org/10.1186/s12969-016-0070-z","pdf_url":"https://ped-rheum.biomedcentral.com/track/pdf/10.1186/s12969-016-0070-z","source":{"id":"https://openalex.org/S121831025","display_name":"Pediatric Rheumatology","issn_l":"1546-0096","issn":["1546-0096"],"is_oa":true,"is_in_doaj":true,"is_core":true,"listed_in":["cwts-core","doaj","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","oarl","poland-70","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320256","host_organization_name":"BioMed Central","host_organization_lineage":["https://openalex.org/P4310320256","https://openalex.org/P4310319965"],"host_organization_lineage_names":["BioMed Central","Springer Nature"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Rheumatology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2284005203.pdf","grobid_xml":"https://content.openalex.org/works/W2284005203.grobid-xml"},"referenced_works_count":71,"referenced_works":["https://openalex.org/W682190","https://openalex.org/W62013721","https://openalex.org/W72363705","https://openalex.org/W204557717","https://openalex.org/W998070158","https://openalex.org/W1500623867","https://openalex.org/W1828038520","https://openalex.org/W1871499212","https://openalex.org/W1968540198","https://openalex.org/W1972240373","https://openalex.org/W1973423968","https://openalex.org/W1977889239","https://openalex.org/W1982351193","https://openalex.org/W1985929139","https://openalex.org/W1991438165","https://openalex.org/W1992047269","https://openalex.org/W1998677128","https://openalex.org/W1999802485","https://openalex.org/W2004887893","https://openalex.org/W2006150593","https://openalex.org/W2010722948","https://openalex.org/W2018398196","https://openalex.org/W2022237635","https://openalex.org/W2027738506","https://openalex.org/W2031517139","https://openalex.org/W2035677339","https://openalex.org/W2036666544","https://openalex.org/W2051258714","https://openalex.org/W2062687560","https://openalex.org/W2063323018","https://openalex.org/W2064729318","https://openalex.org/W2065059951","https://openalex.org/W2074892708","https://openalex.org/W2078284710","https://openalex.org/W2079028206","https://openalex.org/W2081647486","https://openalex.org/W2082255177","https://openalex.org/W2089588732","https://openalex.org/W2093156856","https://openalex.org/W2093217973","https://openalex.org/W2096787265","https://openalex.org/W2099496753","https://openalex.org/W2099545738","https://openalex.org/W2102334004","https://openalex.org/W2104613102","https://openalex.org/W2110820931","https://openalex.org/W2113735272","https://openalex.org/W2116271315","https://openalex.org/W2119147758","https://openalex.org/W2121745904","https://openalex.org/W2139116384","https://openalex.org/W2139925607","https://openalex.org/W2143190437","https://openalex.org/W2149603490","https://openalex.org/W2154534238","https://openalex.org/W2156796253","https://openalex.org/W2169375209","https://openalex.org/W2194309244","https://openalex.org/W2268988891","https://openalex.org/W2307254252","https://openalex.org/W2322292974","https://openalex.org/W2325125286","https://openalex.org/W2411979079","https://openalex.org/W2414521412","https://openalex.org/W2460516514","https://openalex.org/W2465473254","https://openalex.org/W2473433727","https://openalex.org/W2780238682","https://openalex.org/W4230929943","https://openalex.org/W4235673640","https://openalex.org/W4300492363"],"related_works":["https://openalex.org/W3034983756","https://openalex.org/W3047755338","https://openalex.org/W4280558773","https://openalex.org/W2955512517","https://openalex.org/W2233903537","https://openalex.org/W4403098314","https://openalex.org/W2748990729","https://openalex.org/W4248833727","https://openalex.org/W4206306289","https://openalex.org/W2254327427"],"abstract_inverted_index":{"BD":[0,69,96],"is":[1,12,43,70,98],"a":[2,7,17,110],"systemic":[3],"inflammatory":[4,38],"disease":[5,49],"with":[6,63,87],"variable":[8],"vasculitis.":[9],"Paediatric":[10],"onset":[11,31],"very":[13],"rare":[14],"and":[15,23,32,72,77,93,117],"carries":[16],"strong":[18],"genetic":[19],"component.":[20],"Oral":[21],"ulcers":[22],"fever":[24],"of":[25,68,79],"unknown":[26],"origin":[27],"are":[28],"frequent":[29,90],"at":[30,100],"difficult":[33],"to":[34,46,112],"distinguish":[35],"from":[36],"other":[37],"disorders;":[39],"therefore,":[40],"expert":[41,53],"opinion":[42],"still":[44],"mandatory":[45],"recognize":[47],"the":[48,84],"early.":[50],"An":[51],"international":[52],"consensus":[54],"has":[55],"recently":[56],"proposed":[57],"new":[58],"classification":[59],"criteria":[60],"for":[61],"children":[62],"BD.":[64],"The":[65],"clinical":[66],"spectrum":[67],"heterogeneous":[71],"influenced":[73],"by":[74],"gender,":[75],"ethnicity":[76],"country":[78],"residence.":[80],"Young":[81],"males":[82],"have":[83,108],"worst":[85],"prognosis":[86],"significantly":[88],"more":[89],"neurological,":[91],"ocular":[92],"vascular":[94],"involvement.":[95,120],"treatment":[97],"aimed":[99],"alleviating":[101],"inflammation.":[102],"Among":[103],"all":[104],"drugs,":[105],"TNF\u03b1":[106],"inhibitors":[107],"become":[109],"standard":[111],"control":[113],"severe":[114],"ocular,":[115],"neurological":[116],"digestive":[118],"system":[119]},"counts_by_year":[{"year":2026,"cited_by_count":7},{"year":2025,"cited_by_count":18},{"year":2024,"cited_by_count":38},{"year":2023,"cited_by_count":13},{"year":2022,"cited_by_count":18},{"year":2021,"cited_by_count":24},{"year":2020,"cited_by_count":17},{"year":2019,"cited_by_count":16},{"year":2018,"cited_by_count":12},{"year":2017,"cited_by_count":12},{"year":2016,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
