{"id":"https://openalex.org/W2170947711","doi":"https://doi.org/10.2215/cjn.01271005","title":"Spectrum of Renal Diseases Associated with Extreme Forms of Insulin Resistance","display_name":"Spectrum of Renal Diseases Associated with Extreme Forms of Insulin Resistance","publication_year":2006,"publication_date":"2006-04-26","ids":{"openalex":"https://openalex.org/W2170947711","doi":"https://doi.org/10.2215/cjn.01271005","mag":"2170947711","pmid":"https://pubmed.ncbi.nlm.nih.gov/17699267"},"language":"en","primary_location":{"id":"doi:10.2215/cjn.01271005","doi":"https://doi.org/10.2215/cjn.01271005","is_oa":false,"landing_page_url":"https://doi.org/10.2215/cjn.01271005","pdf_url":null,"source":{"id":"https://openalex.org/S184267533","display_name":"Clinical Journal of the American Society of Nephrology","issn_l":"1555-9041","issn":["1555-9041","1555-905X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical Journal of the American Society of Nephrology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5087336523","display_name":"Carla Musso","orcid":"https://orcid.org/0000-0002-0567-3656","observed_orcids":["https://orcid.org/0000-0002-0567-3656"]},"institutions":[{"id":"https://openalex.org/I1299303238","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88","country_code":"US","type":"government","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238"]},{"id":"https://openalex.org/I4210090567","display_name":"National Institute of Diabetes and Digestive and Kidney Diseases","ror":"https://ror.org/00adh9b73","country_code":"US","type":"facility","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Carla Musso","raw_affiliation_strings":["Clinical Endocrinology Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland 20892-1770, USA","*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Clinical Endocrinology Branch, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland 20892-1770, USA","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]},{"raw_affiliation_string":"*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5063234229","display_name":"Edward D. Javor","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1299303238","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88","country_code":"US","type":"government","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238"]},{"id":"https://openalex.org/I4210090567","display_name":"National Institute of Diabetes and Digestive and Kidney Diseases","ror":"https://ror.org/00adh9b73","country_code":"US","type":"facility","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Edward Javor","raw_affiliation_strings":["*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5000884587","display_name":"Elaine K. Cochran","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1299303238","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88","country_code":"US","type":"government","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238"]},{"id":"https://openalex.org/I4210090567","display_name":"National Institute of Diabetes and Digestive and Kidney Diseases","ror":"https://ror.org/00adh9b73","country_code":"US","type":"facility","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Elaine Cochran","raw_affiliation_strings":["*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5028072510","display_name":"James E. Balow","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1299303238","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88","country_code":"US","type":"government","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238"]},{"id":"https://openalex.org/I4210090567","display_name":"National Institute of Diabetes and Digestive and Kidney Diseases","ror":"https://ror.org/00adh9b73","country_code":"US","type":"facility","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"James E Balow","raw_affiliation_strings":["*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5070064147","display_name":"Phillip G\u00f6rden","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1299303238","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88","country_code":"US","type":"government","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238"]},{"id":"https://openalex.org/I4210090567","display_name":"National Institute of Diabetes and Digestive and Kidney Diseases","ror":"https://ror.org/00adh9b73","country_code":"US","type":"facility","lineage":["https://openalex.org/I1299022934","https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Phillip Gorden","raw_affiliation_strings":["Dr. Phillip Gorden, CEB/NIDDK/NIH, 9000 Rockville Pike, CRC Room 6-5952, Bethesda, MD 20892-1770. Phone: 301-402-7340; Fax: 301-435-5873; E-mail: [email\u00a0protected]","*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Dr. Phillip Gorden, CEB/NIDDK/NIH, 9000 Rockville Pike, CRC Room 6-5952, Bethesda, MD 20892-1770. Phone: 301-402-7340; Fax: 301-435-5873; E-mail: [email\u00a0protected]","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]},{"raw_affiliation_string":"*Clinical Endocrinology Branch and \u2020Kidney Disease Section, National Institute of Diabetes and Digestive and Kidney Diseases, National Institutes of Health, Bethesda, Maryland","institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5070064147"],"corresponding_institution_ids":["https://openalex.org/I1299303238","https://openalex.org/I4210090567"],"apc_list":null,"apc_paid":null,"fwci":1.1642,"has_fulltext":false,"cited_by_count":56,"citation_normalized_percentile":{"value":0.81864898,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":99},"biblio":{"volume":"1","issue":"4","first_page":"616","last_page":"622"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.6650000214576721,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.6650000214576721,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10408","display_name":"Chronic Kidney Disease and Diabetes","score":0.32839998602867126,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10308","display_name":"Systemic Lupus Erythematosus Research","score":0.000699999975040555,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/insulin-resistance","display_name":"insulin resistance","score":0.8709999918937683},{"id":"https://openalex.org/keywords/diabetic-nephropathy","display_name":"diabetic nephropathy","score":0.8669999837875366},{"id":"https://openalex.org/keywords/proteinuric-nephropathy","display_name":"proteinuric nephropathy","score":0.8709999918937683},{"id":"https://openalex.org/keywords/lipodystrophy","display_name":"lipodystrophy","score":0.8880000114440918},{"id":"https://openalex.org/keywords/membranoproliferative-glomerulonephritis","display_name":"membranoproliferative glomerulonephritis","score":0.9800000190734863},{"id":"https://openalex.org/keywords/focal-segmental-glomerulosclerosis","display_name":"focal segmental glomerulosclerosis","score":0.9990000128746033},{"id":"https://openalex.org/keywords/insulin-receptor-antibodies","display_name":"insulin receptor antibodies","score":0.9290000200271606},{"id":"https://openalex.org/keywords/lupus-glomerulonephritis","display_name":"lupus glomerulonephritis","score":0.9440000057220459},{"id":"https://openalex.org/keywords/type-2-diabetes","display_name":"type 2 diabetes","score":0.8659999966621399},{"id":"https://openalex.org/keywords/type-1-diabetes","display_name":"type 1 diabetes","score":0.843999981880188},{"id":"https://openalex.org/keywords/kidney-biopsy","display_name":"renal biopsy","score":0.8119999766349792},{"id":"https://openalex.org/keywords/end-stage-renal-disease","display_name":"end-stage renal disease","score":0.8149999976158142},{"id":"https://openalex.org/keywords/hyperglycemia","display_name":"hyperglycemia","score":0.8059999942779541},{"id":"https://openalex.org/keywords/glomerular-hyperfiltration","display_name":"glomerular hyperfiltration","score":0.9900000095367432}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9225163459777832},{"id":"https://openalex.org/C2779922275","wikidata":"https://www.wikidata.org/wiki/Q1129105","display_name":"Diabetic nephropathy","level":3,"score":0.6922255754470825},{"id":"https://openalex.org/C2777391703","wikidata":"https://www.wikidata.org/wiki/Q1053470","display_name":"Insulin resistance","level":3,"score":0.6754347681999207},{"id":"https://openalex.org/C2775946357","wikidata":"https://www.wikidata.org/wiki/Q1713037","display_name":"Membranous nephropathy","level":4,"score":0.5759185552597046},{"id":"https://openalex.org/C2781184683","wikidata":"https://www.wikidata.org/wiki/Q1054718","display_name":"Nephropathy","level":3,"score":0.5592026114463806},{"id":"https://openalex.org/C2781087799","wikidata":"https://www.wikidata.org/wiki/Q7312483","display_name":"Renal biopsy","level":3,"score":0.5376909971237183},{"id":"https://openalex.org/C555293320","wikidata":"https://www.wikidata.org/wiki/Q12206","display_name":"Diabetes mellitus","level":2,"score":0.5054965019226074},{"id":"https://openalex.org/C2781036514","wikidata":"https://www.wikidata.org/wiki/Q2299379","display_name":"Membranoproliferative glomerulonephritis","level":4,"score":0.478456974029541},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.4699525833129883},{"id":"https://openalex.org/C2777180221","wikidata":"https://www.wikidata.org/wiki/Q3025883","display_name":"Type 2 diabetes","level":3,"score":0.45370548963546753},{"id":"https://openalex.org/C133397671","wikidata":"https://www.wikidata.org/wiki/Q3347171","display_name":"Renal pathology","level":3,"score":0.43820756673812866},{"id":"https://openalex.org/C2780368995","wikidata":"https://www.wikidata.org/wiki/Q605006","display_name":"Glomerulonephritis","level":3,"score":0.4172350764274597},{"id":"https://openalex.org/C134018914","wikidata":"https://www.wikidata.org/wiki/Q162606","display_name":"Endocrinology","level":1,"score":0.31867003440856934},{"id":"https://openalex.org/C2780091579","wikidata":"https://www.wikidata.org/wiki/Q9377","display_name":"Kidney","level":2,"score":0.23126578330993652}],"mesh":[{"descriptor_ui":"D003928","descriptor_name":"Diabetic Nephropathies","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D003928","descriptor_name":"Diabetic Nephropathies","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007333","descriptor_name":"Insulin Resistance","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D007674","descriptor_name":"Kidney Diseases","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D007674","descriptor_name":"Kidney Diseases","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":true},{"descriptor_ui":"D012720","descriptor_name":"Severity of Illness Index","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.2215/cjn.01271005","doi":"https://doi.org/10.2215/cjn.01271005","is_oa":false,"landing_page_url":"https://doi.org/10.2215/cjn.01271005","pdf_url":null,"source":{"id":"https://openalex.org/S184267533","display_name":"Clinical Journal of the American Society of Nephrology","issn_l":"1555-9041","issn":["1555-9041","1555-905X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical Journal of the American Society of Nephrology","raw_type":"journal-article"},{"id":"pmid:17699267","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/17699267","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical journal of the American Society of Nephrology : CJASN","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","score":0.98580002784729,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[{"id":"https://openalex.org/F4320332161","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88"}],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":40,"referenced_works":["https://openalex.org/W1626021911","https://openalex.org/W1920565561","https://openalex.org/W1965310933","https://openalex.org/W1967393173","https://openalex.org/W1973464824","https://openalex.org/W2003772020","https://openalex.org/W2010887039","https://openalex.org/W2014435320","https://openalex.org/W2022749561","https://openalex.org/W2027542164","https://openalex.org/W2028135332","https://openalex.org/W2033169469","https://openalex.org/W2034971680","https://openalex.org/W2056976690","https://openalex.org/W2057292957","https://openalex.org/W2059792416","https://openalex.org/W2064309380","https://openalex.org/W2066961578","https://openalex.org/W2082404441","https://openalex.org/W2083986466","https://openalex.org/W2087454504","https://openalex.org/W2100364658","https://openalex.org/W2112256909","https://openalex.org/W2113142131","https://openalex.org/W2118796405","https://openalex.org/W2125434093","https://openalex.org/W2137262712","https://openalex.org/W2142706916","https://openalex.org/W2143146488","https://openalex.org/W2144737888","https://openalex.org/W2186098454","https://openalex.org/W2275139239","https://openalex.org/W2324062964","https://openalex.org/W2337454357","https://openalex.org/W2443668198","https://openalex.org/W2471605942","https://openalex.org/W2615684303","https://openalex.org/W2769264260","https://openalex.org/W4237181509","https://openalex.org/W4256636055"],"related_works":["https://openalex.org/W135127122","https://openalex.org/W2008717039","https://openalex.org/W4306313766","https://openalex.org/W2327989975","https://openalex.org/W3118275933","https://openalex.org/W1518162194","https://openalex.org/W2397281108","https://openalex.org/W7160185259","https://openalex.org/W4416866927","https://openalex.org/W3042034162"],"abstract_inverted_index":{"Diabetic":[0],"nephropathy":[1,18,94,156,177],"is":[2,31,35,62,71,164],"the":[3,9,13,67,78,98,103,106,121,150,165],"leading":[4],"cause":[5],"of":[6,49,55,100,109,135,167,175],"ESRD":[7],"in":[8,19,77,115,130,148,158,178],"United":[10],"States.":[11],"Why":[12],"pathogenic":[14],"mechanisms":[15],"lead":[16],"to":[17,64,102,154,170],"certain":[20],"patients":[21,46,116,131,179],"with":[22,47,117,132,180],"type":[23,83,86,118,139],"1":[24,84],"and":[25,28,39,85,91,138,157],"2":[26,119,140],"diabetes":[27],"spare":[29],"others":[30],"unclear,":[32],"but":[33,60],"it":[34,61],"clear":[36],"that":[37,66,152],"hyperglycemia":[38],"glomerular":[40],"hyperfiltration":[41],"are":[42,58,95,112],"important":[43,146],"factors.":[44],"In":[45,97],"syndromes":[48,99],"extreme":[50],"insulin":[51,104,136],"resistance,":[52],"proteinuric":[53,155,176],"forms":[54,108,134],"renal":[56,68,122,142],"disease":[57],"common,":[59],"surprising":[63],"find":[65],"pathology":[69,123,151],"usually":[70],"not":[72,125],"diabetic":[73,93,127],"nephropathy.":[74,128],"For":[75],"instance,":[76],"lipodystrophy":[79],"syndromes,":[80],"membranoproliferative":[81],"glomerulonephritis":[82,111],"2,":[87],"focal":[88],"segmental":[89],"glomerulosclerosis,":[90],"also":[92],"seen.":[96,113],"autoantibodies":[101],"receptor,":[105],"various":[107],"lupus":[110],"Even":[114],"diabetes,":[120,141],"may":[124],"be":[126],"Therefore,":[129],"syndromic":[133],"resistance":[137],"biopsy":[143],"has":[144],"an":[145],"role":[147],"defining":[149],"leads":[153],"formulating":[159],"a":[160],"therapeutic":[161],"approach.":[162],"It":[163],"purpose":[166],"this":[168],"article":[169],"review":[171],"these":[172],"unusual":[173],"aspects":[174],"diabetes.":[181]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":2},{"year":2024,"cited_by_count":1},{"year":2023,"cited_by_count":1},{"year":2022,"cited_by_count":2},{"year":2021,"cited_by_count":1},{"year":2020,"cited_by_count":2},{"year":2019,"cited_by_count":5},{"year":2018,"cited_by_count":8},{"year":2017,"cited_by_count":4},{"year":2016,"cited_by_count":3},{"year":2015,"cited_by_count":2},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":4},{"year":2012,"cited_by_count":4}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
