{"id":"https://openalex.org/W2139229231","doi":"https://doi.org/10.1002/ajh.24225","title":"Lenalidomide in the treatment of Rosai Dorfman disease\u2014a first in use report","display_name":"Lenalidomide in the treatment of Rosai Dorfman disease\u2014a first in use report","publication_year":2015,"publication_date":"2015-10-26","ids":{"openalex":"https://openalex.org/W2139229231","doi":"https://doi.org/10.1002/ajh.24225","mag":"2139229231","pmid":"https://pubmed.ncbi.nlm.nih.gov/26502013"},"language":"en","primary_location":{"id":"doi:10.1002/ajh.24225","doi":"https://doi.org/10.1002/ajh.24225","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ajh.24225","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24225","source":{"id":"https://openalex.org/S199810014","display_name":"American Journal of Hematology","issn_l":"0361-8609","issn":["0361-8609","1096-8652"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Hematology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24225","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5025321281","display_name":"Maria M Zlobinsky Rubinstein","orcid":"https://orcid.org/0000-0002-7943-8245","observed_orcids":["https://orcid.org/0000-0002-7943-8245"]},"institutions":[{"id":"https://openalex.org/I1335289525","display_name":"Montefiore Medical Center","ror":"https://ror.org/044ntvm43","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1335289525","https://openalex.org/I19772626"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Maria Rubinstein","raw_affiliation_strings":["Montefiore Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Montefiore Medical Center, New York","institution_ids":["https://openalex.org/I1335289525"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5052100524","display_name":"Amer Assal","orcid":"https://orcid.org/0000-0003-4707-9265","observed_orcids":["https://orcid.org/0000-0003-4707-9265"]},"institutions":[{"id":"https://openalex.org/I129975664","display_name":"Albert Einstein College of Medicine","ror":"https://ror.org/05cf8a891","country_code":"US","type":"education","lineage":["https://openalex.org/I129975664","https://openalex.org/I4210112371"]},{"id":"https://openalex.org/I1335289525","display_name":"Montefiore Medical Center","ror":"https://ror.org/044ntvm43","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1335289525","https://openalex.org/I19772626"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Amer Assal","raw_affiliation_strings":["Albert Einstein College of Medicine, New York","Montefiore Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Albert Einstein College of Medicine, New York","institution_ids":["https://openalex.org/I129975664"]},{"raw_affiliation_string":"Montefiore Medical Center, New York","institution_ids":["https://openalex.org/I1335289525"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5088547719","display_name":"Marina Scherba","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1334819555","display_name":"Memorial Sloan Kettering Cancer Center","ror":"https://ror.org/02yrq0923","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1334819555"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Marina Scherba","raw_affiliation_strings":["Memorial Sloan Kettering Cancer Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Memorial Sloan Kettering Cancer Center, New York","institution_ids":["https://openalex.org/I1334819555"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5018113432","display_name":"Jordan Elman","orcid":"https://orcid.org/0000-0002-5823-9896","observed_orcids":["https://orcid.org/0000-0002-5823-9896"]},"institutions":[{"id":"https://openalex.org/I129975664","display_name":"Albert Einstein College of Medicine","ror":"https://ror.org/05cf8a891","country_code":"US","type":"education","lineage":["https://openalex.org/I129975664","https://openalex.org/I4210112371"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Jordan Elman","raw_affiliation_strings":["Albert Einstein College of Medicine, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Albert Einstein College of Medicine, New York","institution_ids":["https://openalex.org/I129975664"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Robert White","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4405272987","display_name":"Weill Cornell Medical Center","ror":"https://ror.org/052v90092","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I205783295","https://openalex.org/I4387153466","https://openalex.org/I4405272987"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Robert White","raw_affiliation_strings":["Weill Cornell Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Weill Cornell Medical Center, New York","institution_ids":["https://openalex.org/I4405272987"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5101669870","display_name":"Amit K. Verma","orcid":"https://orcid.org/0000-0001-7592-7693","observed_orcids":["https://orcid.org/0000-0001-7592-7693","https://orcid.org/0000-0002-5408-1673"]},"institutions":[{"id":"https://openalex.org/I129975664","display_name":"Albert Einstein College of Medicine","ror":"https://ror.org/05cf8a891","country_code":"US","type":"education","lineage":["https://openalex.org/I129975664","https://openalex.org/I4210112371"]},{"id":"https://openalex.org/I1335289525","display_name":"Montefiore Medical Center","ror":"https://ror.org/044ntvm43","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1335289525","https://openalex.org/I19772626"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Amit Verma","raw_affiliation_strings":["Albert Einstein College of Medicine, New York","Montefiore Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Albert Einstein College of Medicine, New York","institution_ids":["https://openalex.org/I129975664"]},{"raw_affiliation_string":"Montefiore Medical Center, New York","institution_ids":["https://openalex.org/I1335289525"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5034958687","display_name":"Marianna Strakhan","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I129975664","display_name":"Albert Einstein College of Medicine","ror":"https://ror.org/05cf8a891","country_code":"US","type":"education","lineage":["https://openalex.org/I129975664","https://openalex.org/I4210112371"]},{"id":"https://openalex.org/I2800364127","display_name":"Jacobi Medical Center","ror":"https://ror.org/05hcfns23","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I2800364127"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Marianna Strakhan","raw_affiliation_strings":["Albert Einstein College of Medicine, New York","Jacobi Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Albert Einstein College of Medicine, New York","institution_ids":["https://openalex.org/I129975664"]},{"raw_affiliation_string":"Jacobi Medical Center, New York","institution_ids":["https://openalex.org/I2800364127"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022914051","display_name":"Farnoush Mohammadi","orcid":"https://orcid.org/0000-0002-5840-1988","observed_orcids":["https://orcid.org/0000-0002-5840-1988","https://orcid.org/0000-0002-2347-5039"]},"institutions":[{"id":"https://openalex.org/I129975664","display_name":"Albert Einstein College of Medicine","ror":"https://ror.org/05cf8a891","country_code":"US","type":"education","lineage":["https://openalex.org/I129975664","https://openalex.org/I4210112371"]},{"id":"https://openalex.org/I2800364127","display_name":"Jacobi Medical Center","ror":"https://ror.org/05hcfns23","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I2800364127"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Farnoush Mohammadi","raw_affiliation_strings":["Albert Einstein College of Medicine, New York","Jacobi Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Albert Einstein College of Medicine, New York","institution_ids":["https://openalex.org/I129975664"]},{"raw_affiliation_string":"Jacobi Medical Center, New York","institution_ids":["https://openalex.org/I2800364127"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5048939308","display_name":"Murali Janakiram","orcid":"https://orcid.org/0000-0001-9323-8007","observed_orcids":["https://orcid.org/0000-0001-9323-8007"]},"institutions":[{"id":"https://openalex.org/I129975664","display_name":"Albert Einstein College of Medicine","ror":"https://ror.org/05cf8a891","country_code":"US","type":"education","lineage":["https://openalex.org/I129975664","https://openalex.org/I4210112371"]},{"id":"https://openalex.org/I1335289525","display_name":"Montefiore Medical Center","ror":"https://ror.org/044ntvm43","country_code":"US","type":"healthcare","lineage":["https://openalex.org/I1335289525","https://openalex.org/I19772626"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Murali Janakiram","raw_affiliation_strings":["Albert Einstein College of Medicine, New York","Montefiore Medical Center, New York"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Albert Einstein College of Medicine, New York","institution_ids":["https://openalex.org/I129975664"]},{"raw_affiliation_string":"Montefiore Medical Center, New York","institution_ids":["https://openalex.org/I1335289525"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":5,"corresponding_author_ids":["https://openalex.org/A5048939308"],"corresponding_institution_ids":["https://openalex.org/I129975664","https://openalex.org/I1335289525"],"apc_list":{"value":5450,"currency":"USD","value_usd":5450},"apc_paid":null,"fwci":0.4911,"has_fulltext":true,"cited_by_count":24,"citation_normalized_percentile":{"value":0.69716615,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":98},"biblio":{"volume":"91","issue":"2","first_page":"E1","last_page":"E1"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11909","display_name":"Histiocytic Disorders and Treatments","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10185","display_name":"Lymphoma Diagnosis and Treatment","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2734","display_name":"Pathology and Forensic Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11571","display_name":"Sarcoidosis and Beryllium Toxicity Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/rosai-dorfman-disease","display_name":"Rosai-Dorfman disease","score":0.9309999942779541},{"id":"https://openalex.org/keywords/lenalidomide","display_name":"lenalidomide","score":0.9940000176429749},{"id":"https://openalex.org/keywords/thalidomide","display_name":"thalidomide","score":0.8429999947547913},{"id":"https://openalex.org/keywords/relapse","display_name":"relapse","score":0.37599998712539673},{"id":"https://openalex.org/keywords/immunomodulators","display_name":"immunomodulators","score":0.6050000190734863},{"id":"https://openalex.org/keywords/azathioprine","display_name":"azathioprine","score":0.5550000071525574},{"id":"https://openalex.org/keywords/rituximab","display_name":"rituximab","score":0.7039999961853027},{"id":"https://openalex.org/keywords/cvp-chemotherapy","display_name":"CVP chemotherapy","score":0.7760000228881836},{"id":"https://openalex.org/keywords/corticosteroid-tapering","display_name":"corticosteroid tapering","score":0.5659999847412109},{"id":"https://openalex.org/keywords/relapse-prevention","display_name":"relapse prevention","score":0.3449999988079071},{"id":"https://openalex.org/keywords/immunosuppression","display_name":"immunosuppression","score":0.5770000219345093},{"id":"https://openalex.org/keywords/s100-protein","display_name":"S-100 protein","score":0.515999972820282},{"id":"https://openalex.org/keywords/cd1a","display_name":"CD1a","score":0.7239999771118164}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9018900394439697},{"id":"https://openalex.org/C43100952","wikidata":"https://www.wikidata.org/wiki/Q654612","display_name":"Histiocyte","level":2,"score":0.6779791116714478},{"id":"https://openalex.org/C2777968768","wikidata":"https://www.wikidata.org/wiki/Q1280161","display_name":"Emperipolesis","level":4,"score":0.675113320350647},{"id":"https://openalex.org/C2778923028","wikidata":"https://www.wikidata.org/wiki/Q974869","display_name":"Leukocytosis","level":2,"score":0.5834391117095947},{"id":"https://openalex.org/C2781192723","wikidata":"https://www.wikidata.org/wiki/Q1567631","display_name":"Rosai\u2013Dorfman disease","level":3,"score":0.5732834935188293},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.4878368675708771},{"id":"https://openalex.org/C2778143017","wikidata":"https://www.wikidata.org/wiki/Q111208","display_name":"Erythrocyte sedimentation rate","level":2,"score":0.4289490282535553},{"id":"https://openalex.org/C2780653079","wikidata":"https://www.wikidata.org/wiki/Q412323","display_name":"Rituximab","level":3,"score":0.4226856827735901},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.41796964406967163},{"id":"https://openalex.org/C2910246740","wikidata":"https://www.wikidata.org/wiki/Q1567631","display_name":"Sinus Histiocytosis with Massive Lymphadenopathy","level":4,"score":0.41544046998023987},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.360970675945282},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.35016244649887085},{"id":"https://openalex.org/C2779338263","wikidata":"https://www.wikidata.org/wiki/Q208414","display_name":"Lymphoma","level":2,"score":0.26584118604660034}],"mesh":[{"descriptor_ui":"D000077269","descriptor_name":"Lenalidomide","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000077269","descriptor_name":"Lenalidomide","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000077269","descriptor_name":"Lenalidomide","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007155","descriptor_name":"Immunologic Factors","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D007155","descriptor_name":"Immunologic Factors","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D007155","descriptor_name":"Immunologic Factors","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D007155","descriptor_name":"Immunologic Factors","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D007155","descriptor_name":"Immunologic Factors","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D007155","descriptor_name":"Immunologic Factors","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000008","qualifier_name":"administration & dosage","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000031","qualifier_name":"analogs & derivatives","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000031","qualifier_name":"analogs & derivatives","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000031","qualifier_name":"analogs & derivatives","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D013792","descriptor_name":"Thalidomide","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D015618","descriptor_name":"Histiocytosis, Sinus","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D016896","descriptor_name":"Treatment Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016896","descriptor_name":"Treatment Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016896","descriptor_name":"Treatment Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1002/ajh.24225","doi":"https://doi.org/10.1002/ajh.24225","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ajh.24225","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24225","source":{"id":"https://openalex.org/S199810014","display_name":"American Journal of Hematology","issn_l":"0361-8609","issn":["0361-8609","1096-8652"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Hematology","raw_type":"journal-article"},{"id":"pmid:26502013","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/26502013","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American journal of hematology","raw_type":"Case Reports"}],"best_oa_location":{"id":"doi:10.1002/ajh.24225","doi":"https://doi.org/10.1002/ajh.24225","is_oa":true,"landing_page_url":"https://doi.org/10.1002/ajh.24225","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1002/ajh.24225","source":{"id":"https://openalex.org/S199810014","display_name":"American Journal of Hematology","issn_l":"0361-8609","issn":["0361-8609","1096-8652"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Hematology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9922999739646912,"display_name":"Good health and well-being"}],"sustainable_development_goals_aurora":[],"study_designs":[],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2139229231.pdf","grobid_xml":"https://content.openalex.org/works/W2139229231.grobid-xml"},"referenced_works_count":5,"referenced_works":["https://openalex.org/W19653836","https://openalex.org/W2027620575","https://openalex.org/W2076746365","https://openalex.org/W2141053481","https://openalex.org/W2145192216"],"related_works":["https://openalex.org/W2173884486","https://openalex.org/W4386278268","https://openalex.org/W4399882774","https://openalex.org/W4226325912","https://openalex.org/W4389259552","https://openalex.org/W3213595405","https://openalex.org/W2005494387","https://openalex.org/W4226443004","https://openalex.org/W2910967165","https://openalex.org/W4415670981"],"abstract_inverted_index":{"disease-a":[0],"first":[1,569],"in":[2,50,141,158,186,292,328,353,422,489,498,564,576],"use":[3,532],"reportTo":[4],"the":[5,51,78,110,142,173,199,206,249,253,267,275,280,337,373,376,394,403,464,483,522,531,540,568],"Editor:":[6],"A":[7],"43-year-old":[8],"Hispanic":[9],"male":[10],"was":[11,66,87,164,208,257,286,304,321],"evaluated":[12],"waxing":[13],"and":[14,27,43,59,63,90,118,131,155,183,194,212,221,236,320,325,387,406,435,438,446,469,485,503,526,539,567],"waning":[15],"bilateral":[16,24],"submandibular":[17],"masses,":[18],"associated":[19,165,342,429],"with":[20,46,72,84,94,138,166,176,204,218,259,331,343,391,399,402,430,473,491,515,521,530],"fevers,":[21,180],"night":[22],"sweats,":[23],"flank":[25],"pain,":[26],"a":[28,47,69,135,139,148,167,293,315,370,412,556],"20pound":[29],"weight":[30,153,181],"loss.The":[31],"complete":[32,329],"blood":[33],"count":[34],"revealed":[35],"mild":[36],"leukocytosis":[37],"(13.6":[38],"3":[39,55,270,317],"10":[40,56],"9":[41,57],"/l),":[42],"normocytic":[44],"anemia":[45],"left":[48],"shift":[49],"granulocyte":[52],"series":[53],"(11.7":[54],"/l).ESR":[58],"CRP":[60],"were":[61],"90":[62],"210,":[64],"respectively.Electrophoresis":[65],"notable":[67],"for":[68,109,201,467],"polyclonal":[70],"hypergammaglobulinemia":[71],"free":[73],"lambda":[74],"chains.Excisional":[75],"biopsy":[76],"of":[77,105,112,124,144,150,169,216,252,375,383,418,420,433,456,478,487,533,536,572],"supraclavicular":[79],"nodes":[80],"showed":[81],"sinus":[82],"histiocytosis":[83],"emperipolesis":[85,468],"which":[86,261,290,462,508],"S-100":[88],"positive":[89],"CD1a":[91],"negative":[92],"consistent":[93],"Rosai":[95],"Dorfman":[96],"disease":[97,367,553,566],"(RDD)":[98],"(Fig.":[99],"1).There":[100],"have":[101,246,453],"been":[102],"various":[103],"reports":[104],"different":[106],"agents":[107],"used":[108],"treatment":[111,122],"RDD;":[113],"including":[114],"corticosteroids,":[115],"rituximab,":[116],"chemotherapy,":[117],"radiotherapy":[119],"[1].Typical":[120],"initial":[121],"consists":[123],"high":[125,431,476],"dose":[126],"steroids":[127,400],"at":[128],"1":[129],"mg/kg":[130],"our":[132],"patient":[133,174,207,224,256,276,281,395,514],"achieved":[134,225,238,528],"quick":[136],"remission":[137,226,235,330,520,529,575],"reduction":[140,149],"size":[143],"cervical":[145],"lymph":[146,178],"nodes,":[147,179],"inflammatory":[151,187],"markers,":[152],"gain,":[154],"an":[156,184,308,363,551,561],"improvement":[157],"his":[159],"lytic":[160],"lesions.Unfortunately,":[161],"steroid":[162],"tapering":[163],"relapse":[168,237],"RDD.During":[170],"every":[171],"relapse,":[172],"presented":[175],"increasing":[177],"loss,":[182,302],"increase":[185],"markers":[188],"namely":[189],"erythrocyte":[190],"sedimentation":[191],"rate":[192],"(ESR)":[193],"C-reactive":[195],"protein":[196],"(CRP).Due":[197],"to":[198,248,264,283,288,306,323,397,442,542],"concern":[200],"long-term":[202],"toxicity":[203],"steroids,":[205],"started":[209],"on":[210],"Rituximab":[211],"underwent":[213],"six":[214],"cycles":[215],"chemotherapy":[217],"Cyclophosphamide,":[219],"Vincristine,":[220],"Prednisone":[222],"(CVP).The":[223],"but":[227,269,408],"relapsed":[228,277],"again":[229],"after":[230,272],"2":[231],"months.The":[232],"relatively":[233],"short":[234],"by":[239,511],"administering":[240],"CVP":[241,254],"suggested":[242],"that":[243,335,350,359,494,547],"RDD":[244,339,360,423,427,451,516],"could":[245,361,549],"responded":[247,282,396],"immunosuppressive":[250],"component":[251],"regimen.The":[255],"treated":[258,472],"Cladribine":[260],"is":[262,326,340,428,440,463,509],"known":[263,441],"markedly":[265],"immunosuppress":[266],"lymphocytes":[268],"months":[271],"such":[273],"treatment,":[274],"once":[278],"again.Since":[279],"immunosuppression,":[284],"he":[285,297,303,313],"switched":[287,305,322],"Azathioprine,":[289],"resulted":[291],"partial":[294],"response.But":[295],"since":[296],"developed":[298,314],"azathioprine":[299,407],"induced":[300],"visual":[301],"thalidomide,":[307,312],"immunomodulating":[309],"(Imid)":[310],"agent.With":[311],"Grade":[316],"skin":[318],"rash":[319],"Lenalidomide":[324,439,512,573],"currently":[327],"Lenalidomide.Recent":[332],"studies":[333],"indicate":[334],"among":[336],"histiocytosis,":[338],"not":[341,410,518],"BRAF":[344],"mutations":[345,538],"or":[346],"other":[347,354],"clonal":[348,371,537,557],"abnormalities":[349],"are":[351],"seen":[352],"histiocytic":[355],"disorders":[356],"[2].This":[357],"suggests":[358],"be":[362,425,550,560],"aberrant":[364],"immune":[365,506,543],"mediated":[366],"rather":[368,554],"than":[369,555],"disorder.On":[372],"basis":[374],"above":[377],"response,":[378],"we":[379],"hypothesize":[380,493],"two":[381],"mechanisms":[382,417],"control":[384],"(1)":[385],"immunosuppression":[386,398],"(2)":[388],"immunomodulation.In":[389],"keeping":[390],"this":[392,548],"hypothesis,":[393],"(consistent":[401],"literature),":[404],"cyclophosphamide":[405],"did":[409,517],"achieve":[411,519],"remission.Why":[413],"should":[414],"immunomodulation":[415],"work?Two":[416],"action":[419],"Imids":[421],"can":[424],"postulated.(1)":[426],"levels":[432,449,477],"TNF-a":[434,444],"IL-6":[436,448],"[3]":[437],"decrease":[443,447],"expression":[445,455,480],"[4].(2)":[450],"cells":[452],"strong":[454],"macrophage":[457],"colony-stimulating":[458],"factor":[459],"(M-CSF)":[460],"[5],":[461],"suspected":[465],"mechanism":[466],"human":[470],"monocytes":[471,488],"M-CSF":[474,495],"produced":[475],"IL-10.IL-10":[479],"positively":[481],"regulates":[482],"proliferation":[484],"differentiation":[486],"conjunction":[490],"M-CSF.We":[492],"activated":[496],"macrophages":[497],"RDD,":[499],"induce":[500],"IL-10":[501],"release":[502],"alter":[504],"T-cell-mediated":[505],"response":[507,541],"abrogated":[510],"[4].Our":[513],"previously":[523],"studied":[524],"treatments":[525],"only":[527],"Lenalidomide.The":[534],"lack":[535],"suppression/immune":[544],"modulation":[545],"suggest":[546],"immune-mediated":[552],"disorder.Lenalidomide":[558],"may":[559],"appropriate":[562],"therapy":[563],"refractory":[565],"reported":[570],"case":[571],"inducing":[574],"RDD.":[577]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":6},{"year":2023,"cited_by_count":3},{"year":2022,"cited_by_count":4},{"year":2021,"cited_by_count":2},{"year":2020,"cited_by_count":1},{"year":2019,"cited_by_count":4},{"year":2018,"cited_by_count":1},{"year":2017,"cited_by_count":1}],"updated_date":"2026-10-30T12:39:25.321706","created_date":"2016-06-24T00:00:00"}
