{"id":"https://openalex.org/W2136990647","doi":null,"title":"Alexander disease: diagnosis with MR imaging.","display_name":"Alexander disease: diagnosis with MR imaging.","publication_year":2001,"publication_date":"2001-03-01","ids":{"openalex":"https://openalex.org/W2136990647","mag":"2136990647","pmid":"https://pubmed.ncbi.nlm.nih.gov/11237983","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/7976831"},"language":"en","primary_location":{"id":"pmh:oai:pubmedcentral.nih.gov:7976831","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/7976831","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"AJNR Am J Neuroradiol","raw_type":"Text"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":true,"oa_status":"green","oa_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/7976831","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5064045676","display_name":"Marjo S. van der Knaap","orcid":"https://orcid.org/0000-0001-8912-0954","observed_orcids":["https://orcid.org/0000-0001-8912-0954"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"M S van der Knaap","raw_affiliation_strings":["Department of Child Neurology, Free University Hospital, Amsterdam, the Netherlands"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Child Neurology, Free University Hospital, Amsterdam, the Netherlands","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111811756","display_name":"Sakkubai Naidu","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"S Naidu","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110132429","display_name":"Steven N. Breiter","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"S N Breiter","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5017178425","display_name":"Susan Blas\u00e9r","orcid":"https://orcid.org/0000-0001-8891-5106","observed_orcids":["https://orcid.org/0000-0001-8891-5106"]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"S Blaser","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5051053838","display_name":"Hans Stroink","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"H Stroink","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5086701410","display_name":"Stephan Springer","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"S Springer","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5032351075","display_name":"Jacobus C. Begeer","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"J C Begeer","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5078576230","display_name":"Rudy Van Coster","orcid":"https://orcid.org/0000-0003-0665-1843","observed_orcids":["https://orcid.org/0000-0003-0665-1843"]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"R van Coster","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5025943767","display_name":"Peter G. Barth","orcid":"https://orcid.org/0000-0002-9025-5677","observed_orcids":["https://orcid.org/0000-0002-9025-5677"]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"P G Barth","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110004058","display_name":"Neil H. Thomas","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"N H Thomas","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5108948654","display_name":"Jacob Valk","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"J Valk","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5104045576","display_name":"James M. Powers","orcid":"https://orcid.org/0000-0002-6107-0569","observed_orcids":["https://orcid.org/0000-0002-6107-0569"]},"institutions":[{"id":"https://openalex.org/I865915315","display_name":"Vrije Universiteit Amsterdam","ror":"https://ror.org/008xxew50","country_code":"NL","type":"education","lineage":["https://openalex.org/I865915315"]}],"countries":["NL"],"is_corresponding":false,"raw_author_name":"J M Powers","raw_affiliation_strings":["Vrije Universiteit Amsterdam ,"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Vrije Universiteit Amsterdam ,","institution_ids":["https://openalex.org/I865915315"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":5.1564,"has_fulltext":false,"cited_by_count":333,"citation_normalized_percentile":{"value":0.97222222,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":91,"max":100},"biblio":{"volume":"22","issue":"3","first_page":"541","last_page":"52"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11027","display_name":"Metabolism and Genetic Disorders","score":0.6122999787330627,"subfield":{"id":"https://openalex.org/subfields/1308","display_name":"Clinical Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11027","display_name":"Metabolism and Genetic Disorders","score":0.6122999787330627,"subfield":{"id":"https://openalex.org/subfields/1308","display_name":"Clinical Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12552","display_name":"Fetal and Pediatric Neurological Disorders","score":0.22529999911785126,"subfield":{"id":"https://openalex.org/subfields/2735","display_name":"Pediatrics, Perinatology and Child Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T13481","display_name":"Neurological diseases and metabolism","score":0.048700001090765,"subfield":{"id":"https://openalex.org/subfields/2808","display_name":"Neurology"},"field":{"id":"https://openalex.org/fields/28","display_name":"Neuroscience"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/alexander-disease","display_name":"Alexander disease","score":1.0},{"id":"https://openalex.org/keywords/rosenthal-fibers","display_name":"Rosenthal fibers","score":0.8190000057220459},{"id":"https://openalex.org/keywords/mri-diagnosis","display_name":"MRI diagnosis","score":0.8510000109672546},{"id":"https://openalex.org/keywords/leukoencephalopathy","display_name":"leukoencephalopathy","score":0.8870000243186951},{"id":"https://openalex.org/keywords/white-matter-changes","display_name":"white matter changes","score":0.6439999938011169},{"id":"https://openalex.org/keywords/basal-ganglia-abnormalities","display_name":"basal ganglia abnormalities","score":0.9629999995231628},{"id":"https://openalex.org/keywords/contrast-enhancement","display_name":"contrast enhancement","score":0.828000009059906},{"id":"https://openalex.org/keywords/pediatric-neurology","display_name":"pediatric neurology","score":0.5230000019073486},{"id":"https://openalex.org/keywords/histopathological-correlation","display_name":"histopathological correlation","score":0.640999972820282}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8792539834976196},{"id":"https://openalex.org/C2781192897","wikidata":"https://www.wikidata.org/wiki/Q822050","display_name":"White matter","level":3,"score":0.6788506507873535},{"id":"https://openalex.org/C2779504383","wikidata":"https://www.wikidata.org/wiki/Q41482","display_name":"Autopsy","level":2,"score":0.5766981840133667},{"id":"https://openalex.org/C143409427","wikidata":"https://www.wikidata.org/wiki/Q161238","display_name":"Magnetic resonance imaging","level":2,"score":0.5612490773200989},{"id":"https://openalex.org/C126838900","wikidata":"https://www.wikidata.org/wiki/Q77604","display_name":"Radiology","level":1,"score":0.5128427147865295},{"id":"https://openalex.org/C2778187257","wikidata":"https://www.wikidata.org/wiki/Q464210","display_name":"Basal ganglia","level":3,"score":0.49460265040397644},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.4855191707611084},{"id":"https://openalex.org/C2779281540","wikidata":"https://www.wikidata.org/wiki/Q5062122","display_name":"Central nervous system disease","level":2,"score":0.4446464776992798},{"id":"https://openalex.org/C2775934546","wikidata":"https://www.wikidata.org/wiki/Q179991","display_name":"Biopsy","level":2,"score":0.43864452838897705},{"id":"https://openalex.org/C2778583010","wikidata":"https://www.wikidata.org/wiki/Q3237081","display_name":"Leukoencephalopathy","level":3,"score":0.43149951100349426},{"id":"https://openalex.org/C2778256017","wikidata":"https://www.wikidata.org/wiki/Q3640183","display_name":"Stereotactic biopsy","level":3,"score":0.4223438501358032},{"id":"https://openalex.org/C529278444","wikidata":"https://www.wikidata.org/wiki/Q47273","display_name":"Central nervous system","level":2,"score":0.166416198015213},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.10021787881851196},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.06153425574302673}],"mesh":[{"descriptor_ui":"D001921","descriptor_name":"Brain","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D001933","descriptor_name":"Brain Stem","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007223","descriptor_name":"Infant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007231","descriptor_name":"Infant, Newborn","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008279","descriptor_name":"Magnetic Resonance Imaging","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D012189","descriptor_name":"Retrospective Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013788","descriptor_name":"Thalamus","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D019636","descriptor_name":"Neurodegenerative Diseases","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true}],"locations_count":10,"locations":[{"id":"pmh:oai:pubmedcentral.nih.gov:7976831","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/7976831","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"AJNR Am J Neuroradiol","raw_type":"Text"},{"id":"pmid:11237983","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/11237983","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"AJNR. American journal of neuroradiology","raw_type":"Journal Article"},{"id":"pmh:oai:CiteSeerX.psu:10.1.1.494.8343","doi":null,"is_oa":false,"landing_page_url":"http://citeseerx.ist.psu.edu/viewdoc/summary?doi=10.1.1.494.8343","pdf_url":null,"source":null,"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"http://www.ajnr.org/content/22/3/541.full.pdf","raw_type":"text"},{"id":"pmh:amcpub:oai:pure.amc.nl:publications/4d645195-d88b-4a3c-8013-afa7c8d3d94e","doi":null,"is_oa":false,"landing_page_url":"https://pure.amc.nl/en/publications/alexander-disease-diagnosis-with-mr-imaging(4d645195-d88b-4a3c-8013-afa7c8d3d94e).html","pdf_url":null,"source":{"id":"https://openalex.org/S4306401843","display_name":"Data Archiving and Networked Services (DANS)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1322597698","host_organization_name":"Royal Netherlands Academy of Arts and Sciences","host_organization_lineage":["https://openalex.org/I1322597698"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"AJNR. American journal of neuroradiology, 22(3), 541 - 552. American Society of Neuroradiology","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:archive.ugent.be:141205","doi":null,"is_oa":false,"landing_page_url":"https://biblio.ugent.be/publication/141205","pdf_url":null,"source":{"id":"https://openalex.org/S4306400478","display_name":"Ghent University Academic Bibliography (Ghent University)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I32597200","host_organization_name":"Ghent University","host_organization_lineage":["https://openalex.org/I32597200"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"ISSN: 0195-6108","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:pure.atira.dk:openaire_cris_publications/35aaa3df-4927-48f4-986b-f8bcce03f968","doi":null,"is_oa":false,"landing_page_url":"https://www.scopus.com/pages/publications/0035100718","pdf_url":null,"source":{"id":"https://openalex.org/S7407055350","display_name":"Amsterdam UMC (VU Amsterdam) - Institutional Repository","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Van der Knaap, M S, Naidu, S, Breiter, S N, Blaser, S, Stroink, H, Springer, S, Begeer, J C, Van Coster, R, Barth, P G, Thomas, N H, Valk, J & Powers, J M 2001, 'Alexander disease : Diagnosis with MR imaging', American Journal of Neuroradiology, vol. 22, no. 3, pp. 541-552.","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:pure.rug.nl:openaire_cris_publications/19a4fb2c-ea6b-4813-9f84-75a9d4543bb0","doi":null,"is_oa":false,"landing_page_url":"https://research.rug.nl/en/publications/19a4fb2c-ea6b-4813-9f84-75a9d4543bb0","pdf_url":null,"source":{"id":"https://openalex.org/S4306400420","display_name":"University of Groningen research database (University of Groningen / Centre for Information Technology)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I169381384","host_organization_name":"University of Groningen","host_organization_lineage":["https://openalex.org/I169381384"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"van der Knaap, MS, Naidu, S, Breiter, SN, Blaser, S, Stroink, H, Spinger, S, Begeer, JC, van Coster, R, Barth, PG, Thomas, NH, Powers, JM & Valk, J 2001, 'Alexander disease : Diagnosis with MR imaging', American Journal of Neuroradiology, vol. 22, no. 3, pp. 541-552.","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:rug:oai:pure.rug.nl:publications/19a4fb2c-ea6b-4813-9f84-75a9d4543bb0","doi":null,"is_oa":false,"landing_page_url":"https://research.rug.nl/en/publications/19a4fb2c-ea6b-4813-9f84-75a9d4543bb0","pdf_url":null,"source":{"id":"https://openalex.org/S4306400420","display_name":"University of Groningen research database (University of Groningen / Centre for Information Technology)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I169381384","host_organization_name":"University of Groningen","host_organization_lineage":["https://openalex.org/I169381384"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"American Journal of Neuroradiology, 22(3), 541 - 552. AMER SOC NEURORADIOLOGY","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:vumc:oai:pure.atira.dk:publications/35aaa3df-4927-48f4-986b-f8bcce03f968","doi":null,"is_oa":false,"landing_page_url":"https://research.vumc.nl/en/publications/35aaa3df-4927-48f4-986b-f8bcce03f968","pdf_url":null,"source":{"id":"https://openalex.org/S4306401843","display_name":"Data Archiving and Networked Services (DANS)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1322597698","host_organization_name":"Royal Netherlands Academy of Arts and Sciences","host_organization_lineage":["https://openalex.org/I1322597698"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"American Journal of Neuroradiology, 22(3), 541 - 552. American Society of Neuroradiology","raw_type":"info:eu-repo/semantics/article"},{"id":"mag:2136990647","doi":null,"is_oa":false,"landing_page_url":"http://www.ajnr.org/content/22/3/541.full.pdf","pdf_url":null,"source":{"id":"https://openalex.org/S101278519","display_name":"American Journal of Neuroradiology","issn_l":"0195-6108","issn":["0195-6108","1936-959X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310316165","host_organization_name":"American Society of Neuroradiology","host_organization_lineage":["https://openalex.org/P4310316165"],"host_organization_lineage_names":["American Society of Neuroradiology"],"type":"journal"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"American Journal of Neuroradiology","raw_type":null}],"best_oa_location":{"id":"pmh:oai:pubmedcentral.nih.gov:7976831","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/7976831","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"AJNR Am J Neuroradiol","raw_type":"Text"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.98580002784729}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":45,"referenced_works":["https://openalex.org/W41458573","https://openalex.org/W66887054","https://openalex.org/W287231401","https://openalex.org/W1580732269","https://openalex.org/W1966516902","https://openalex.org/W1983284504","https://openalex.org/W1984409812","https://openalex.org/W1986382797","https://openalex.org/W1990722412","https://openalex.org/W1992255233","https://openalex.org/W1997625191","https://openalex.org/W2001986305","https://openalex.org/W2003289206","https://openalex.org/W2011199674","https://openalex.org/W2012648020","https://openalex.org/W2023596504","https://openalex.org/W2025462022","https://openalex.org/W2029884890","https://openalex.org/W2030482394","https://openalex.org/W2033415035","https://openalex.org/W2052694792","https://openalex.org/W2062289389","https://openalex.org/W2063680881","https://openalex.org/W2064546250","https://openalex.org/W2074849727","https://openalex.org/W2078428933","https://openalex.org/W2080186585","https://openalex.org/W2081146110","https://openalex.org/W2085936048","https://openalex.org/W2090358141","https://openalex.org/W2093430982","https://openalex.org/W2094206075","https://openalex.org/W2096456078","https://openalex.org/W2102379118","https://openalex.org/W2110085161","https://openalex.org/W2120150562","https://openalex.org/W2121678534","https://openalex.org/W2124635182","https://openalex.org/W2137270382","https://openalex.org/W2138800612","https://openalex.org/W2155622755","https://openalex.org/W2170845010","https://openalex.org/W2312976978","https://openalex.org/W2392129939","https://openalex.org/W2417542584"],"related_works":["https://openalex.org/W36187351","https://openalex.org/W638032423","https://openalex.org/W2172108073","https://openalex.org/W2138059263","https://openalex.org/W2145643979","https://openalex.org/W2005745083","https://openalex.org/W2086844604","https://openalex.org/W4396598435","https://openalex.org/W2348281100","https://openalex.org/W7139558574"],"abstract_inverted_index":{"BACKGROUND":[0],"AND":[1],"PURPOSE:":[2],"To":[3],"date,":[4],"the":[5,46,73,139,156,160,184,196,199,210,220],"demonstration":[6],"of":[7,24,32,41,48,63,85,119,130,138,155,159,183,224,240],"Rosenthal":[8],"fibers":[9],"on":[10,109,115],"brain":[11,124,249],"biopsy":[12,250],"or":[13],"autopsy":[14],"specimens":[15],"is":[16,247],"considered":[17],"a":[18,21,29,103,152,248,254],"prerequisite":[19],"for":[20,72,146,233,253],"definitive":[22,255],"diagnosis":[23,62,239],"Alexander":[25,42,64,225,241],"disease.":[26,226],"We":[27],"initiated":[28],"multiinstitutional":[30],"survey":[31],"MR":[33,53,70,90,148,157,174,211,213,237],"abnormalities":[34,118,175,214],"in":[35,56,178,198,216,235,244],"both":[36],"presumed":[37],"and":[38,112,122,127,133,202,206],"confirmed":[39],"cases":[40,246],"disease":[43,65],"to":[44,68,80,143],"assess":[45],"possibility":[47],"an":[49,60,147,234],"MR-based":[50],"diagnosis.":[51,74,150,256],"METHODS:":[52],"imaging":[54,91,238],"studies":[55,158],"three":[57],"patients":[58,200],"with":[59,83,100,106,201,209,219],"autopsy-based":[61],"were":[66,77,93,164,176,215],"analyzed":[67],"define":[69],"criteria":[71,76,92,141,230],"These":[75],"then":[78],"applied":[79],"217":[81,161],"children":[82],"leukoencephalopathy":[84],"unknown":[86],"origin.":[87],"RESULTS:":[88],"Five":[89],"defined:":[94],"extensive":[95],"cerebral":[96],"white":[97,134],"matter":[98,135],"changes":[99],"frontal":[101],"predominance,":[102],"periventricular":[104],"rim":[105],"high":[107],"signal":[108,114],"T1-weighted":[110],"images":[111],"low":[113],"T2-weighted":[116],"images,":[117],"basal":[120],"ganglia":[121],"thalami,":[123],"stem":[125],"abnormalities,":[126],"contrast":[128],"enhancement":[129],"particular":[131],"gray":[132],"structures.":[136],"Four":[137],"five":[140],"had":[142],"be":[144],"met":[145],"imaging-based":[149],"In":[151,181],"retrospective":[153],"analysis":[154],"patients,":[162,186],"19":[163,185],"found":[165,177],"who":[166],"fulfilled":[167],"these":[168,179],"criteria.":[169],"No":[170],"other":[171],"essentially":[172],"new":[173],"patients.":[180],"four":[182],"subsequent":[187],"histologic":[188,204],"confirmation":[189,205],"was":[190,195],"obtained.":[191],"The":[192,228],"clinical":[193],"symptomatology":[194],"same":[197],"without":[203],"correlated":[207],"well":[208],"abnormalities.":[212],"close":[217],"agreement":[218],"known":[221],"histopathologic":[222],"findings":[223],"CONCLUSION:":[227],"defined":[229],"are":[231],"sufficient":[232],"vivo":[236],"disease;":[242],"only":[243],"atypical":[245],"still":[251],"necessary":[252]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":12},{"year":2024,"cited_by_count":14},{"year":2023,"cited_by_count":12},{"year":2022,"cited_by_count":8},{"year":2021,"cited_by_count":12},{"year":2020,"cited_by_count":5},{"year":2019,"cited_by_count":12},{"year":2018,"cited_by_count":14},{"year":2017,"cited_by_count":21},{"year":2016,"cited_by_count":20},{"year":2015,"cited_by_count":12},{"year":2014,"cited_by_count":13},{"year":2013,"cited_by_count":14},{"year":2012,"cited_by_count":26}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
