{"id":"https://openalex.org/W2134910282","doi":"https://doi.org/10.1016/j.jemermed.2010.02.028","title":"A Case Report of Porphyria Variegata Management in the Emergency Department","display_name":"A Case Report of Porphyria Variegata Management in the Emergency Department","publication_year":2010,"publication_date":"2010-04-23","ids":{"openalex":"https://openalex.org/W2134910282","doi":"https://doi.org/10.1016/j.jemermed.2010.02.028","mag":"2134910282","pmid":"https://pubmed.ncbi.nlm.nih.gov/20417053"},"language":"en","primary_location":{"id":"doi:10.1016/j.jemermed.2010.02.028","doi":"https://doi.org/10.1016/j.jemermed.2010.02.028","is_oa":false,"landing_page_url":"https://doi.org/10.1016/j.jemermed.2010.02.028","pdf_url":null,"source":{"id":"https://openalex.org/S4210219855","display_name":"Journal of Emergency Medicine","issn_l":"0736-4679","issn":["0736-4679","1090-1280","2352-5029"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of Emergency Medicine","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5030788565","display_name":"Betty C. Chen","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I204465549","display_name":"Washington University in St. Louis","ror":"https://ror.org/01yc7t268","country_code":"US","type":"education","lineage":["https://openalex.org/I204465549"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Betty C. Chen","raw_affiliation_strings":["Division of Emergency Medicine, Washington University School of Medicine, St. Louis, Missouri 63110, USA","Division of Emergency Medicine Washington University School of Medicine  St Louis Missouri"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Emergency Medicine, Washington University School of Medicine, St. Louis, Missouri 63110, USA","institution_ids":["https://openalex.org/I204465549"]},{"raw_affiliation_string":"Division of Emergency Medicine Washington University School of Medicine  St Louis Missouri","institution_ids":["https://openalex.org/I204465549"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5043018613","display_name":"Richard Thomas Griffey","orcid":"https://orcid.org/0000-0002-6279-7380","observed_orcids":["https://orcid.org/0000-0002-6279-7380"]},"institutions":[{"id":"https://openalex.org/I204465549","display_name":"Washington University in St. Louis","ror":"https://ror.org/01yc7t268","country_code":"US","type":"education","lineage":["https://openalex.org/I204465549"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Richard T. Griffey","raw_affiliation_strings":["Division of Emergency Medicine, Washington University School of Medicine, St. Louis, Missouri"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Emergency Medicine, Washington University School of Medicine, St. Louis, Missouri","institution_ids":["https://openalex.org/I204465549"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5030788565"],"corresponding_institution_ids":["https://openalex.org/I204465549"],"apc_list":{"value":3390,"currency":"USD","value_usd":3390},"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":2,"citation_normalized_percentile":{"value":0.15026255,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":94},"biblio":{"volume":"43","issue":"4","first_page":"e235","last_page":"e238"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12441","display_name":"Porphyrin Metabolism and Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T12441","display_name":"Porphyrin Metabolism and Disorders","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11027","display_name":"Metabolism and Genetic Disorders","score":0.0,"subfield":{"id":"https://openalex.org/subfields/1308","display_name":"Clinical Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12068","display_name":"Neonatal Health and Biochemistry","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2735","display_name":"Pediatrics, Perinatology and Child Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/variegate-porphyria","display_name":"variegate porphyria","score":0.9909999966621399},{"id":"https://openalex.org/keywords/hepatic-porphyria","display_name":"hepatic porphyria","score":0.9580000042915344},{"id":"https://openalex.org/keywords/acute-porphyria-attacks","display_name":"acute porphyria attacks","score":0.699999988079071},{"id":"https://openalex.org/keywords/abdominal-pain","display_name":"abdominal pain","score":0.9229999780654907},{"id":"https://openalex.org/keywords/intravenous-dextrose","display_name":"intravenous dextrose","score":0.9169999957084656},{"id":"https://openalex.org/keywords/emergency-department-management","display_name":"emergency department management","score":0.9470000267028809}],"concepts":[{"id":"https://openalex.org/C2777940757","wikidata":"https://www.wikidata.org/wiki/Q271759","display_name":"Porphyria","level":2,"score":0.9684562683105469},{"id":"https://openalex.org/C2780724011","wikidata":"https://www.wikidata.org/wiki/Q1295316","display_name":"Emergency department","level":2,"score":0.8252017498016357},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8087471127510071},{"id":"https://openalex.org/C2780955771","wikidata":"https://www.wikidata.org/wiki/Q183425","display_name":"Abdominal pain","level":2,"score":0.7684106826782227},{"id":"https://openalex.org/C2779028619","wikidata":"https://www.wikidata.org/wiki/Q424247","display_name":"Acute intermittent porphyria","level":3,"score":0.4611971378326416},{"id":"https://openalex.org/C2776217839","wikidata":"https://www.wikidata.org/wiki/Q189621","display_name":"Heme","level":3,"score":0.4377519190311432},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.34211933612823486},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.2901766300201416},{"id":"https://openalex.org/C181199279","wikidata":"https://www.wikidata.org/wiki/Q8047","display_name":"Enzyme","level":2,"score":0.12493759393692017},{"id":"https://openalex.org/C118552586","wikidata":"https://www.wikidata.org/wiki/Q7867","display_name":"Psychiatry","level":1,"score":0.06711128354072571},{"id":"https://openalex.org/C185592680","wikidata":"https://www.wikidata.org/wiki/Q2329","display_name":"Chemistry","level":0,"score":0.0},{"id":"https://openalex.org/C55493867","wikidata":"https://www.wikidata.org/wiki/Q7094","display_name":"Biochemistry","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000701","descriptor_name":"Analgesics, Opioid","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D004091","descriptor_name":"Hydromorphone","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005440","descriptor_name":"Fluid Therapy","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005947","descriptor_name":"Glucose","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015746","descriptor_name":"Abdominal Pain","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D015746","descriptor_name":"Abdominal Pain","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true},{"descriptor_ui":"D046350","descriptor_name":"Porphyria, Variegate","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D046350","descriptor_name":"Porphyria, Variegate","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true}],"locations_count":2,"locations":[{"id":"doi:10.1016/j.jemermed.2010.02.028","doi":"https://doi.org/10.1016/j.jemermed.2010.02.028","is_oa":false,"landing_page_url":"https://doi.org/10.1016/j.jemermed.2010.02.028","pdf_url":null,"source":{"id":"https://openalex.org/S4210219855","display_name":"Journal of Emergency Medicine","issn_l":"0736-4679","issn":["0736-4679","1090-1280","2352-5029"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of Emergency Medicine","raw_type":"journal-article"},{"id":"pmid:20417053","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/20417053","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of emergency medicine","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3","score":0.9940000176429749}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":14,"referenced_works":["https://openalex.org/W1997494859","https://openalex.org/W2014876665","https://openalex.org/W2024005016","https://openalex.org/W2030334942","https://openalex.org/W2031067362","https://openalex.org/W2050445717","https://openalex.org/W2053004141","https://openalex.org/W2056313634","https://openalex.org/W2087291747","https://openalex.org/W2096589216","https://openalex.org/W2142162687","https://openalex.org/W2332494913","https://openalex.org/W4241367285","https://openalex.org/W4253239096"],"related_works":["https://openalex.org/W1980794742","https://openalex.org/W2065771144","https://openalex.org/W3206226491","https://openalex.org/W2547072450","https://openalex.org/W7126265570","https://openalex.org/W2143786427","https://openalex.org/W4313489157","https://openalex.org/W2330862199","https://openalex.org/W2419582044","https://openalex.org/W7095302642"],"abstract_inverted_index":null,"counts_by_year":[{"year":2021,"cited_by_count":1},{"year":2016,"cited_by_count":1}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
