{"id":"https://openalex.org/W2106434649","doi":"https://doi.org/10.1136/jnnp.2009.190462","title":"The profile of motor unit number estimation (MUNE) in spinal and bulbar muscular atrophy","display_name":"The profile of motor unit number estimation (MUNE) in spinal and bulbar muscular atrophy","publication_year":2009,"publication_date":"2009-12-03","ids":{"openalex":"https://openalex.org/W2106434649","doi":"https://doi.org/10.1136/jnnp.2009.190462","mag":"2106434649","pmid":"https://pubmed.ncbi.nlm.nih.gov/19965845"},"language":"en","primary_location":{"id":"doi:10.1136/jnnp.2009.190462","doi":"https://doi.org/10.1136/jnnp.2009.190462","is_oa":false,"landing_page_url":"https://doi.org/10.1136/jnnp.2009.190462","pdf_url":null,"source":{"id":"https://openalex.org/S134773490","display_name":"Journal of Neurology Neurosurgery & Psychiatry","issn_l":"0022-3050","issn":["0022-3050","1468-330X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Neurology, Neurosurgery &amp; Psychiatry","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5010703590","display_name":"Keisuke Suzuki","orcid":"https://orcid.org/0000-0001-5790-1289","observed_orcids":["https://orcid.org/0000-0001-5790-1289"]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"K. Suzuki","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, 65 Tsurumai-cho, Showa-ku, Nagoya 466-8550, Japan","Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, 65 Tsurumai-cho, Showa-ku, Nagoya 466-8550, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5036681718","display_name":"Masahisa Katsuno","orcid":"https://orcid.org/0000-0001-9453-9311","observed_orcids":["https://orcid.org/0000-0001-9453-9311"]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"M. Katsuno","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","Institute for Advanced Research, Nagoya University, Nagoya, Japan","Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan; Institute for Advanced Research, Nagoya University, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Institute for Advanced Research, Nagoya University, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan; Institute for Advanced Research, Nagoya University, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5030581235","display_name":"Haruhiko Banno","orcid":"https://orcid.org/0000-0002-0404-3839","observed_orcids":["https://orcid.org/0000-0002-0404-3839"]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"H. Banno","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5088316632","display_name":"Yu Takeuchi","orcid":"https://orcid.org/0000-0002-2953-3965","observed_orcids":["https://orcid.org/0000-0002-2953-3965"]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Y. Takeuchi","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":null,"display_name":"M. Kawashima","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"M. Kawashima","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":null,"display_name":"N. Suga","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"N. Suga","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5060933834","display_name":"Atsushi Hashizume","orcid":"https://orcid.org/0000-0002-3098-7390","observed_orcids":["https://orcid.org/0000-0002-3098-7390"]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"A. Hashizume","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":null,"display_name":"T. Hama","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210090647","display_name":"Nagoya University Hospital","ror":"https://ror.org/008zz8m46","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210090647"]},{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"T. Hama","raw_affiliation_strings":["Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647"]},{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647","https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5055822025","display_name":"K\u00f4ji Uchida","orcid":"https://orcid.org/0000-0003-3894-5299","observed_orcids":["https://orcid.org/0000-0003-3894-5299","https://orcid.org/0000-0003-2029-1768"]},"institutions":[{"id":"https://openalex.org/I4210090647","display_name":"Nagoya University Hospital","ror":"https://ror.org/008zz8m46","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210090647"]},{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"K. Uchida","raw_affiliation_strings":["Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647"]},{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647","https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":null,"display_name":"F. Yamashita","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4405257914","display_name":"Nakatsugawa Municipal General Hospital","ror":"https://ror.org/05t9myw53","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4405257914"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"F. Yamashita","raw_affiliation_strings":["Nakatsugawa Municipal General Hospital, Nakatsugawa, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Nakatsugawa Municipal General Hospital, Nakatsugawa, Japan","institution_ids":["https://openalex.org/I4405257914"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037448497","display_name":"Tomohiko Nakamura","orcid":"https://orcid.org/0000-0001-7622-4527","observed_orcids":["https://orcid.org/0000-0001-7622-4527"]},"institutions":[{"id":"https://openalex.org/I4210090647","display_name":"Nagoya University Hospital","ror":"https://ror.org/008zz8m46","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210090647"]},{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"T. Nakamura","raw_affiliation_strings":["Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647"]},{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647","https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5054366611","display_name":"Masaaki Hirayama","orcid":"https://orcid.org/0000-0003-0092-7837","observed_orcids":["https://orcid.org/0000-0003-0092-7837"]},"institutions":[{"id":"https://openalex.org/I4210090647","display_name":"Nagoya University Hospital","ror":"https://ror.org/008zz8m46","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210090647"]},{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"M. Hirayama","raw_affiliation_strings":["Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647"]},{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]},{"raw_affiliation_string":"Central Neurophysiological Laboratories, Nagoya University Hospital, Nagoya, Japan; Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I4210090647","https://openalex.org/I60134161"]}]},{"author_position":"middle","author":{"id":null,"display_name":"F. Tanaka","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"F. Tanaka","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5112176593","display_name":"Gen Sobue","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I60134161","display_name":"Nagoya University","ror":"https://ror.org/04chrp450","country_code":"JP","type":"education","lineage":["https://openalex.org/I60134161"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"G. Sobue","raw_affiliation_strings":["Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Nagoya University Graduate School of Medicine, Nagoya, Japan","institution_ids":["https://openalex.org/I60134161"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":3,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.8797,"has_fulltext":false,"cited_by_count":25,"citation_normalized_percentile":{"value":0.69616464,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":98},"biblio":{"volume":"81","issue":"5","first_page":"567","last_page":"571"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10949","display_name":"Genetic Neurodegenerative Diseases","score":0.9692000150680542,"subfield":{"id":"https://openalex.org/subfields/2804","display_name":"Cellular and Molecular Neuroscience"},"field":{"id":"https://openalex.org/fields/28","display_name":"Neuroscience"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T10949","display_name":"Genetic Neurodegenerative Diseases","score":0.9692000150680542,"subfield":{"id":"https://openalex.org/subfields/2804","display_name":"Cellular and Molecular Neuroscience"},"field":{"id":"https://openalex.org/fields/28","display_name":"Neuroscience"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T10855","display_name":"Amyotrophic Lateral Sclerosis Research","score":0.01360000018030405,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12331","display_name":"Hereditary Neurological Disorders","score":0.005799999926239252,"subfield":{"id":"https://openalex.org/subfields/2804","display_name":"Cellular and Molecular Neuroscience"},"field":{"id":"https://openalex.org/fields/28","display_name":"Neuroscience"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/spinal-and-bulbar-muscular-atrophy","display_name":"spinal and bulbar muscular atrophy","score":0.9980000257492065},{"id":"https://openalex.org/keywords/motor-unit-number-estimation","display_name":"motor unit number estimation","score":0.9869999885559082},{"id":"https://openalex.org/keywords/lower-motor-neuron-disease","display_name":"lower motor neuron disease","score":0.8579999804496765},{"id":"https://openalex.org/keywords/motor-neuron-degeneration","display_name":"motor neuron degeneration","score":0.8679999709129333},{"id":"https://openalex.org/keywords/biomarkers","display_name":"biomarkers","score":0.7870000004768372},{"id":"https://openalex.org/keywords/handgrip-strength","display_name":"grip strength","score":0.6470000147819519},{"id":"https://openalex.org/keywords/disease-progression","display_name":"disease progression","score":0.9259999990463257},{"id":"https://openalex.org/keywords/longitudinal-change","display_name":"longitudinal change","score":0.3149999976158142}],"concepts":[{"id":"https://openalex.org/C2780434838","wikidata":"https://www.wikidata.org/wiki/Q1995327","display_name":"Spinal and bulbar muscular atrophy","level":5,"score":0.8942776918411255},{"id":"https://openalex.org/C2776752467","wikidata":"https://www.wikidata.org/wiki/Q1133903","display_name":"Motor neuron","level":3,"score":0.7375046610832214},{"id":"https://openalex.org/C2781425072","wikidata":"https://www.wikidata.org/wiki/Q1889028","display_name":"Motor unit","level":2,"score":0.6348873376846313},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.5531571507453918},{"id":"https://openalex.org/C2780596555","wikidata":"https://www.wikidata.org/wiki/Q206901","display_name":"Amyotrophic lateral sclerosis","level":3,"score":0.5011870861053467},{"id":"https://openalex.org/C61367390","wikidata":"https://www.wikidata.org/wiki/Q416601","display_name":"Androgen receptor","level":4,"score":0.49216026067733765},{"id":"https://openalex.org/C551621295","wikidata":"https://www.wikidata.org/wiki/Q182228","display_name":"Brainstem","level":2,"score":0.490418404340744},{"id":"https://openalex.org/C2781172350","wikidata":"https://www.wikidata.org/wiki/Q194520","display_name":"Atrophy","level":2,"score":0.488147109746933},{"id":"https://openalex.org/C2780775167","wikidata":"https://www.wikidata.org/wiki/Q9606","display_name":"Spinal cord","level":2,"score":0.4668254256248474},{"id":"https://openalex.org/C2778558090","wikidata":"https://www.wikidata.org/wiki/Q580290","display_name":"Spinal muscular atrophy","level":3,"score":0.4262327551841736},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.37191399931907654},{"id":"https://openalex.org/C169760540","wikidata":"https://www.wikidata.org/wiki/Q207011","display_name":"Neuroscience","level":1,"score":0.35902565717697144},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.34233638644218445},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.3412647247314453},{"id":"https://openalex.org/C15744967","wikidata":"https://www.wikidata.org/wiki/Q9418","display_name":"Psychology","level":0,"score":0.2131941020488739},{"id":"https://openalex.org/C105702510","wikidata":"https://www.wikidata.org/wiki/Q514","display_name":"Anatomy","level":1,"score":0.16473427414894104},{"id":"https://openalex.org/C121608353","wikidata":"https://www.wikidata.org/wiki/Q12078","display_name":"Cancer","level":2,"score":0.0},{"id":"https://openalex.org/C2780192828","wikidata":"https://www.wikidata.org/wiki/Q181257","display_name":"Prostate cancer","level":3,"score":0.0}],"mesh":[{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002452","descriptor_name":"Cell Count","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002452","descriptor_name":"Cell Count","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002452","descriptor_name":"Cell Count","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D004247","descriptor_name":"DNA","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D004247","descriptor_name":"DNA","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D004247","descriptor_name":"DNA","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007839","descriptor_name":"Functional Laterality","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D007839","descriptor_name":"Functional Laterality","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D007839","descriptor_name":"Functional Laterality","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D008137","descriptor_name":"Longitudinal Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008137","descriptor_name":"Longitudinal Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008137","descriptor_name":"Longitudinal Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009046","descriptor_name":"Motor Neurons","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D009046","descriptor_name":"Motor Neurons","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D009046","descriptor_name":"Motor Neurons","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D009460","descriptor_name":"Neurologic Examination","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009460","descriptor_name":"Neurologic Examination","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009460","descriptor_name":"Neurologic Examination","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015415","descriptor_name":"Biomarkers","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015415","descriptor_name":"Biomarkers","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015415","descriptor_name":"Biomarkers","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D017668","descriptor_name":"Age of Onset","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D017668","descriptor_name":"Age of Onset","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D017668","descriptor_name":"Age of Onset","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018450","descriptor_name":"Disease Progression","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018450","descriptor_name":"Disease Progression","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018450","descriptor_name":"Disease Progression","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018485","descriptor_name":"Muscle Fibers, Skeletal","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D018485","descriptor_name":"Muscle Fibers, Skeletal","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D018485","descriptor_name":"Muscle Fibers, Skeletal","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D018737","descriptor_name":"Hand Strength","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D018737","descriptor_name":"Hand Strength","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D018737","descriptor_name":"Hand Strength","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D020966","descriptor_name":"Muscular Disorders, Atrophic","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D020966","descriptor_name":"Muscular Disorders, Atrophic","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D020966","descriptor_name":"Muscular Disorders, Atrophic","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D020966","descriptor_name":"Muscular Disorders, Atrophic","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D020966","descriptor_name":"Muscular Disorders, Atrophic","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D020966","descriptor_name":"Muscular Disorders, Atrophic","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D053580","descriptor_name":"Muscle Strength","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D053580","descriptor_name":"Muscle Strength","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false},{"descriptor_ui":"D053580","descriptor_name":"Muscle Strength","qualifier_ui":"Q000502","qualifier_name":"physiology","is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1136/jnnp.2009.190462","doi":"https://doi.org/10.1136/jnnp.2009.190462","is_oa":false,"landing_page_url":"https://doi.org/10.1136/jnnp.2009.190462","pdf_url":null,"source":{"id":"https://openalex.org/S134773490","display_name":"Journal of Neurology Neurosurgery & Psychiatry","issn_l":"0022-3050","issn":["0022-3050","1468-330X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Neurology, Neurosurgery &amp; Psychiatry","raw_type":"journal-article"},{"id":"pmid:19965845","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/19965845","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of neurology, neurosurgery, and psychiatry","raw_type":"Journal Article"},{"id":"pmh:oai:open-archive.highwire.org:jnnp:jnnp.2009.190462v1","doi":null,"is_oa":false,"landing_page_url":"http://jnnp.bmj.com/cgi/content/short/jnnp.2009.190462v1","pdf_url":null,"source":{"id":"https://openalex.org/S4406923041","display_name":"HighWire Press Open Archive","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":null,"host_organization_name":null,"host_organization_lineage":[],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"","raw_type":"TEXT"}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.9763000011444092,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"sustainable_development_goals_aurora":[{"score":0.8500000238418579,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":43,"referenced_works":["https://openalex.org/W91108901","https://openalex.org/W1969719416","https://openalex.org/W1984355984","https://openalex.org/W1985318432","https://openalex.org/W1985902870","https://openalex.org/W1989876807","https://openalex.org/W1996158859","https://openalex.org/W2006101507","https://openalex.org/W2024818041","https://openalex.org/W2025049761","https://openalex.org/W2030491608","https://openalex.org/W2033687324","https://openalex.org/W2041637430","https://openalex.org/W2043607357","https://openalex.org/W2048937882","https://openalex.org/W2067261805","https://openalex.org/W2069153889","https://openalex.org/W2074342599","https://openalex.org/W2074830646","https://openalex.org/W2081914453","https://openalex.org/W2089038365","https://openalex.org/W2090941837","https://openalex.org/W2093319899","https://openalex.org/W2095568662","https://openalex.org/W2098590651","https://openalex.org/W2099562440","https://openalex.org/W2106032723","https://openalex.org/W2108834942","https://openalex.org/W2111714299","https://openalex.org/W2113333419","https://openalex.org/W2114038592","https://openalex.org/W2117527164","https://openalex.org/W2125953041","https://openalex.org/W2133502584","https://openalex.org/W2140530485","https://openalex.org/W2143395795","https://openalex.org/W2152930788","https://openalex.org/W2155478811","https://openalex.org/W2156922160","https://openalex.org/W2157731839","https://openalex.org/W2159317313","https://openalex.org/W2166668030","https://openalex.org/W2249338989"],"related_works":["https://openalex.org/W2007234093","https://openalex.org/W2416259612","https://openalex.org/W1994142333","https://openalex.org/W2040265875","https://openalex.org/W1964854351","https://openalex.org/W1970491283","https://openalex.org/W2123231783","https://openalex.org/W152616065","https://openalex.org/W1970819184","https://openalex.org/W2029835834"],"abstract_inverted_index":{"OBJECTIVE:":[0],"Spinal":[1],"and":[2,47,100,129,137,167],"bulbar":[3],"muscular":[4],"atrophy":[5],"(SBMA)":[6],"is":[7,35,159],"a":[8,18,95,107,144],"lower":[9,40],"motor":[10,41,59,78,117,148,170],"neuron":[11,60,171],"disease":[12,34,138],"caused":[13],"by":[14],"the":[15,23,44,56,64,70,110,165],"expansion":[16],"of":[17,32,39,58,98,109,115,169],"trinucleotide":[19],"CAG":[20],"repeat":[21],"in":[22,43,83,106,122,147,173],"androgen":[24],"receptor":[25],"(AR)":[26],"gene.":[27],"The":[28,75,113,154],"fundamental":[29],"histopathological":[30],"finding":[31],"this":[33,91],"an":[36,160],"extensive":[37],"loss":[38],"neurons":[42],"spinal":[45],"cord":[46],"brainstem.":[48],"It":[49],"is,":[50],"however,":[51],"difficult":[52],"to":[53,68,88],"evaluate":[54],"clinically":[55],"degree":[57],"degeneration,":[61],"which":[62],"stresses":[63],"need":[65],"for":[66],"biomarkers":[67],"detect":[69],"remaining":[71],"neuronal":[72],"function.":[73],"METHODS:":[74],"authors":[76],"performed":[77],"unit":[79],"number":[80,114],"estimation":[81],"(MUNE)":[82],"52":[84],"patients":[85,123,174],"with":[86,124,127,132,175],"SBMA,":[87,99],"investigate":[89],"whether":[90],"method":[92],"could":[93],"be":[94],"potential":[96],"biomarker":[97],"re-evaluated":[101],"MUNE":[102,158],"1":[103,151],"year":[104],"later":[105],"subgroup":[108],"patients.":[111],"RESULTS:":[112],"functioning":[116],"units":[118,149],"was":[119,130],"remarkably":[120],"reduced":[121],"SBMA":[125],"compared":[126],"controls,":[128],"correlated":[131],"both":[133],"ipsilateral":[134],"grip":[135],"power":[136],"duration.":[139],"A":[140],"longitudinal":[141],"analysis":[142],"demonstrated":[143],"further":[145],"reduction":[146],"within":[150],"year.":[152],"CONCLUSIONS:":[153],"results":[155],"suggest":[156],"that":[157,163],"electrophysiological":[161],"parameter":[162],"reflects":[164],"severity":[166],"progression":[168],"degeneration":[172],"SBMA.":[176]},"counts_by_year":[{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":1},{"year":2022,"cited_by_count":4},{"year":2020,"cited_by_count":3},{"year":2019,"cited_by_count":1},{"year":2018,"cited_by_count":1},{"year":2017,"cited_by_count":2},{"year":2016,"cited_by_count":2},{"year":2015,"cited_by_count":2},{"year":2013,"cited_by_count":1},{"year":2012,"cited_by_count":6}],"updated_date":"2026-10-08T09:06:37.294493","created_date":"2025-10-10T00:00:00"}
