{"id":"https://openalex.org/W2092555019","doi":"https://doi.org/10.1016/0098-2997(87)90007-0","title":"Genetic deficiency of bilirubin glucuronidation in rats and humans","display_name":"Genetic deficiency of bilirubin glucuronidation in rats and humans","publication_year":1987,"publication_date":"1987-01-01","ids":{"openalex":"https://openalex.org/W2092555019","doi":"https://doi.org/10.1016/0098-2997(87)90007-0","mag":"2092555019","pmid":"https://pubmed.ncbi.nlm.nih.gov/3306240"},"language":"en","primary_location":{"id":"doi:10.1016/0098-2997(87)90007-0","doi":"https://doi.org/10.1016/0098-2997(87)90007-0","is_oa":false,"landing_page_url":"https://doi.org/10.1016/0098-2997(87)90007-0","pdf_url":null,"source":{"id":"https://openalex.org/S61794117","display_name":"Molecular Aspects of Medicine","issn_l":"0098-2997","issn":["0098-2997","1872-9452"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","jufo-3","ki-jl-1","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Molecular Aspects of Medicine","raw_type":"journal-article"},"volume":null,"type":"review","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5067829318","display_name":"Brian Burchell","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I177639307","display_name":"University of Dundee","ror":"https://ror.org/03h2bxq36","country_code":"GB","type":"education","lineage":["https://openalex.org/I177639307"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Brian Burchell","raw_affiliation_strings":["Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland","institution_ids":["https://openalex.org/I177639307"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5028415096","display_name":"Michael W.H. Coughtrie","orcid":"https://orcid.org/0000-0003-1989-1416","observed_orcids":["https://orcid.org/0000-0003-1989-1416"]},"institutions":[{"id":"https://openalex.org/I177639307","display_name":"University of Dundee","ror":"https://ror.org/03h2bxq36","country_code":"GB","type":"education","lineage":["https://openalex.org/I177639307"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Michael W.H. Coughtrie","raw_affiliation_strings":["Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland","institution_ids":["https://openalex.org/I177639307"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5102730050","display_name":"Michael R. Jackson","orcid":"https://orcid.org/0000-0002-3377-0138","observed_orcids":["https://orcid.org/0000-0002-3377-0138"]},"institutions":[{"id":"https://openalex.org/I177639307","display_name":"University of Dundee","ror":"https://ror.org/03h2bxq36","country_code":"GB","type":"education","lineage":["https://openalex.org/I177639307"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Michael R. Jackson","raw_affiliation_strings":["Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland","institution_ids":["https://openalex.org/I177639307"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5073267583","display_name":"Steven R. P. SHEPHERD","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I177639307","display_name":"University of Dundee","ror":"https://ror.org/03h2bxq36","country_code":"GB","type":"education","lineage":["https://openalex.org/I177639307"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Steven R.P. Shepherd","raw_affiliation_strings":["Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland","institution_ids":["https://openalex.org/I177639307"]}]},{"author_position":"middle","author":{"id":null,"display_name":"David Harding","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I177639307","display_name":"University of Dundee","ror":"https://ror.org/03h2bxq36","country_code":"GB","type":"education","lineage":["https://openalex.org/I177639307"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"David Harding","raw_affiliation_strings":["Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Biochemistry, Medical Sciences Institute, The University, Dundee DD1 4HN, Scotland","institution_ids":["https://openalex.org/I177639307"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5075595875","display_name":"Robert Hume","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I98677209","display_name":"University of Edinburgh","ror":"https://ror.org/01nrxwf90","country_code":"GB","type":"education","lineage":["https://openalex.org/I98677209"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Robert Hume","raw_affiliation_strings":["Department of Paediatrics, Medical School, University of Edinburgh, Scotland"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Paediatrics, Medical School, University of Edinburgh, Scotland","institution_ids":["https://openalex.org/I98677209"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":5220,"currency":"USD","value_usd":5220},"apc_paid":null,"fwci":2.072,"has_fulltext":false,"cited_by_count":36,"citation_normalized_percentile":{"value":0.88571429,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":94},"biblio":{"volume":"9","issue":"5","first_page":"429","last_page":"455"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12068","display_name":"Neonatal Health and Biochemistry","score":0.9907000064849854,"subfield":{"id":"https://openalex.org/subfields/2735","display_name":"Pediatrics, Perinatology and Child Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12068","display_name":"Neonatal Health and Biochemistry","score":0.9907000064849854,"subfield":{"id":"https://openalex.org/subfields/2735","display_name":"Pediatrics, Perinatology and Child Health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10570","display_name":"Drug Transport and Resistance Mechanisms","score":0.003800000064074993,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12460","display_name":"Pediatric Hepatobiliary Diseases and Treatments","score":0.00139999995008111,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/bilirubin-glucuronidation","display_name":"bilirubin glucuronidation","score":0.9850000143051147},{"id":"https://openalex.org/keywords/genetic-deficiency","display_name":"genetic deficiency","score":0.8450000286102295},{"id":"https://openalex.org/keywords/bilirubin-metabolism","display_name":"bilirubin metabolism","score":0.675000011920929},{"id":"https://openalex.org/keywords/udp-glucuronosyltransferase","display_name":"UDP-glucuronosyltransferase","score":0.7850000262260437},{"id":"https://openalex.org/keywords/conjugated-bilirubin","display_name":"direct bilirubin","score":0.7070000171661377},{"id":"https://openalex.org/keywords/hyperbilirubinemia","display_name":"hyperbilirubinemia","score":0.6899999976158142},{"id":"https://openalex.org/keywords/rats","display_name":"rats","score":0.49900001287460327},{"id":"https://openalex.org/keywords/human","display_name":"human","score":0.968999981880188}],"concepts":[{"id":"https://openalex.org/C2779907587","wikidata":"https://www.wikidata.org/wiki/Q14901439","display_name":"Glucuronidation","level":4,"score":0.8611152172088623},{"id":"https://openalex.org/C2777513400","wikidata":"https://www.wikidata.org/wiki/Q104219","display_name":"Bilirubin","level":2,"score":0.6336086392402649},{"id":"https://openalex.org/C2781278898","wikidata":"https://www.wikidata.org/wiki/Q419543","display_name":"Glucuronosyltransferase","level":4,"score":0.48698148131370544},{"id":"https://openalex.org/C54355233","wikidata":"https://www.wikidata.org/wiki/Q7162","display_name":"Genetics","level":1,"score":0.4320458471775055},{"id":"https://openalex.org/C134018914","wikidata":"https://www.wikidata.org/wiki/Q162606","display_name":"Endocrinology","level":1,"score":0.4050949811935425},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.38626301288604736},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.38396698236465454},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.32348281145095825},{"id":"https://openalex.org/C202751555","wikidata":"https://www.wikidata.org/wiki/Q221681","display_name":"In vitro","level":2,"score":0.0},{"id":"https://openalex.org/C87644729","wikidata":"https://www.wikidata.org/wiki/Q547502","display_name":"Microsome","level":3,"score":0.0}],"mesh":[{"descriptor_ui":"D000818","descriptor_name":"Animals","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001663","descriptor_name":"Bilirubin","qualifier_ui":"Q000172","qualifier_name":"deficiency","is_major_topic":true},{"descriptor_ui":"D005965","descriptor_name":"Glucuronates","qualifier_ui":"Q000172","qualifier_name":"deficiency","is_major_topic":true},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007565","descriptor_name":"Jaundice","qualifier_ui":"Q000151","qualifier_name":"congenital","is_major_topic":true},{"descriptor_ui":"D013045","descriptor_name":"Species Specificity","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D051381","descriptor_name":"Rats","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1016/0098-2997(87)90007-0","doi":"https://doi.org/10.1016/0098-2997(87)90007-0","is_oa":false,"landing_page_url":"https://doi.org/10.1016/0098-2997(87)90007-0","pdf_url":null,"source":{"id":"https://openalex.org/S61794117","display_name":"Molecular Aspects of Medicine","issn_l":"0098-2997","issn":["0098-2997","1872-9452"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","jufo-3","ki-jl-1","medline","norway-1","poland-140","russia-white-list-1"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Molecular Aspects of Medicine","raw_type":"journal-article"},{"id":"pmid:3306240","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/3306240","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Molecular aspects of medicine","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.8048999905586243}],"study_designs":[],"awards":[],"funders":[{"id":"https://openalex.org/F4320311904","display_name":"Wellcome Trust","ror":"https://ror.org/029chgv08"}],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":56,"referenced_works":["https://openalex.org/W3953146","https://openalex.org/W49145843","https://openalex.org/W60358548","https://openalex.org/W66551181","https://openalex.org/W87158133","https://openalex.org/W239141007","https://openalex.org/W587932429","https://openalex.org/W627029004","https://openalex.org/W1429527117","https://openalex.org/W1483148476","https://openalex.org/W1497837463","https://openalex.org/W1502207890","https://openalex.org/W1513717105","https://openalex.org/W1538625706","https://openalex.org/W1561943091","https://openalex.org/W1569367290","https://openalex.org/W1581567205","https://openalex.org/W1822059636","https://openalex.org/W1861725651","https://openalex.org/W1950804083","https://openalex.org/W1963928473","https://openalex.org/W1969276900","https://openalex.org/W1971486995","https://openalex.org/W1975959445","https://openalex.org/W1979143756","https://openalex.org/W1991374252","https://openalex.org/W1996699684","https://openalex.org/W2009946751","https://openalex.org/W2017529889","https://openalex.org/W2030616232","https://openalex.org/W2031119708","https://openalex.org/W2036323751","https://openalex.org/W2059698989","https://openalex.org/W2060333964","https://openalex.org/W2060925223","https://openalex.org/W2063244690","https://openalex.org/W2065355061","https://openalex.org/W2066123125","https://openalex.org/W2068775214","https://openalex.org/W2076352568","https://openalex.org/W2084595268","https://openalex.org/W2084779432","https://openalex.org/W2090768768","https://openalex.org/W2092528393","https://openalex.org/W2101108802","https://openalex.org/W2126603148","https://openalex.org/W2144634347","https://openalex.org/W2177038219","https://openalex.org/W2284290711","https://openalex.org/W2288747165","https://openalex.org/W2340083957","https://openalex.org/W2407184983","https://openalex.org/W2408208913","https://openalex.org/W4235545045","https://openalex.org/W4300056090","https://openalex.org/W6713792636"],"related_works":["https://openalex.org/W2472568315","https://openalex.org/W1845772111","https://openalex.org/W2070872379","https://openalex.org/W3021399193","https://openalex.org/W2415369685","https://openalex.org/W1868530020","https://openalex.org/W1971032555","https://openalex.org/W3182763549","https://openalex.org/W2314410397","https://openalex.org/W1982956722"],"abstract_inverted_index":null,"counts_by_year":[{"year":2017,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
