{"id":"https://openalex.org/W2016356907","doi":"https://doi.org/10.1136/jnnp.60.4.403","title":"Progressive supranuclear palsy presenting with dynamic aphasia.","display_name":"Progressive supranuclear palsy presenting with dynamic aphasia.","publication_year":1996,"publication_date":"1996-04-01","ids":{"openalex":"https://openalex.org/W2016356907","doi":"https://doi.org/10.1136/jnnp.60.4.403","mag":"2016356907","pmid":"https://pubmed.ncbi.nlm.nih.gov/8774405","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/1073893"},"language":"en","primary_location":{"id":"doi:10.1136/jnnp.60.4.403","doi":"https://doi.org/10.1136/jnnp.60.4.403","is_oa":true,"landing_page_url":"https://doi.org/10.1136/jnnp.60.4.403","pdf_url":"https://jnnp.bmj.com/content/jnnp/60/4/403.full.pdf","source":{"id":"https://openalex.org/S134773490","display_name":"Journal of Neurology Neurosurgery & Psychiatry","issn_l":"0022-3050","issn":["0022-3050","1468-330X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Neurology, Neurosurgery &amp; Psychiatry","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://jnnp.bmj.com/content/jnnp/60/4/403.full.pdf","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5111854247","display_name":"Thomas Esmonde","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210130048","display_name":"Royal Victoria Hospital","ror":"https://ror.org/03rq50d77","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1289110261","https://openalex.org/I4210130048"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"T Esmonde","raw_affiliation_strings":["Department of Neurology, Royal Victoria Hospital, Belfast, UK"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Royal Victoria Hospital, Belfast, UK","institution_ids":["https://openalex.org/I4210130048"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5077066289","display_name":"Elaine Giles","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210130048","display_name":"Royal Victoria Hospital","ror":"https://ror.org/03rq50d77","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1289110261","https://openalex.org/I4210130048"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"E Giles","raw_affiliation_strings":["Department of Neurology, Royal Victoria Hospital, Belfast, UK"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Royal Victoria Hospital, Belfast, UK","institution_ids":["https://openalex.org/I4210130048"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5048546011","display_name":"John H. Xuereb","orcid":"https://orcid.org/0000-0002-1378-1163","observed_orcids":["https://orcid.org/0000-0002-1378-1163"]},"institutions":[{"id":"https://openalex.org/I4210130048","display_name":"Royal Victoria Hospital","ror":"https://ror.org/03rq50d77","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1289110261","https://openalex.org/I4210130048"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"J Xuereb","raw_affiliation_strings":["Department of Neurology, Royal Victoria Hospital, Belfast, UK"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Royal Victoria Hospital, Belfast, UK","institution_ids":["https://openalex.org/I4210130048"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5107843438","display_name":"J. R. Hodges","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210130048","display_name":"Royal Victoria Hospital","ror":"https://ror.org/03rq50d77","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I1289110261","https://openalex.org/I4210130048"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"J Hodges","raw_affiliation_strings":["Department of Neurology, Royal Victoria Hospital, Belfast, UK"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, Royal Victoria Hospital, Belfast, UK","institution_ids":["https://openalex.org/I4210130048"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I4210130048"],"apc_list":null,"apc_paid":null,"fwci":1.672,"has_fulltext":true,"cited_by_count":87,"citation_normalized_percentile":{"value":0.83273247,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":99},"biblio":{"volume":"60","issue":"4","first_page":"403","last_page":"410"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10085","display_name":"Parkinson's Disease Mechanisms and Treatments","score":0.5404999852180481,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10085","display_name":"Parkinson's Disease Mechanisms and Treatments","score":0.5404999852180481,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10009","display_name":"Dementia and Cognitive Impairment Research","score":0.2712000012397766,"subfield":{"id":"https://openalex.org/subfields/2738","display_name":"Psychiatry and Mental health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10465","display_name":"Neurobiology of Language and Bilingualism","score":0.13760000467300415,"subfield":{"id":"https://openalex.org/subfields/2805","display_name":"Cognitive Neuroscience"},"field":{"id":"https://openalex.org/fields/28","display_name":"Neuroscience"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/progressive-supranuclear-palsy","display_name":"progressive supranuclear palsy","score":1.0},{"id":"https://openalex.org/keywords/akinetic-rigid-syndrome","display_name":"akinetic-rigid syndrome","score":0.7590000033378601},{"id":"https://openalex.org/keywords/fluency-disorders","display_name":"fluency disorders","score":0.5389999747276306},{"id":"https://openalex.org/keywords/semantic-memory","display_name":"semantic memory","score":0.8169999718666077},{"id":"https://openalex.org/keywords/neuropsychological-impairment","display_name":"neuropsychological deficits","score":0.5830000042915344}],"concepts":[{"id":"https://openalex.org/C2776477761","wikidata":"https://www.wikidata.org/wiki/Q945930","display_name":"Progressive supranuclear palsy","level":3,"score":0.9215496778488159},{"id":"https://openalex.org/C2779422653","wikidata":"https://www.wikidata.org/wiki/Q2836","display_name":"Aphasia","level":2,"score":0.6543338894844055},{"id":"https://openalex.org/C99508421","wikidata":"https://www.wikidata.org/wiki/Q2678675","display_name":"Physical medicine and rehabilitation","level":1,"score":0.5009438991546631},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.48636844754219055},{"id":"https://openalex.org/C15744967","wikidata":"https://www.wikidata.org/wiki/Q9418","display_name":"Psychology","level":0,"score":0.4198189079761505},{"id":"https://openalex.org/C169760540","wikidata":"https://www.wikidata.org/wiki/Q207011","display_name":"Neuroscience","level":1,"score":0.31380409002304077},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.12497234344482422},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.109458327293396}],"mesh":[{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001037","descriptor_name":"Aphasia","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009483","descriptor_name":"Neuropsychological Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013068","descriptor_name":"Speech Production Measurement","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013494","descriptor_name":"Supranuclear Palsy, Progressive","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D013494","descriptor_name":"Supranuclear Palsy, Progressive","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D016022","descriptor_name":"Case-Control Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D017809","descriptor_name":"Fatal Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1136/jnnp.60.4.403","doi":"https://doi.org/10.1136/jnnp.60.4.403","is_oa":true,"landing_page_url":"https://doi.org/10.1136/jnnp.60.4.403","pdf_url":"https://jnnp.bmj.com/content/jnnp/60/4/403.full.pdf","source":{"id":"https://openalex.org/S134773490","display_name":"Journal of Neurology Neurosurgery & Psychiatry","issn_l":"0022-3050","issn":["0022-3050","1468-330X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Neurology, Neurosurgery &amp; Psychiatry","raw_type":"journal-article"},{"id":"pmh:oai:pubmedcentral.nih.gov:1073893","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/1073893","pdf_url":"https://pmc.ncbi.nlm.nih.gov/articles/PMC1073893/pdf/jnnpsyc00016-0045.pdf","source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"J Neurol Neurosurg Psychiatry","raw_type":"Text"},{"id":"pmid:8774405","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/8774405","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of neurology, neurosurgery, and psychiatry","raw_type":"Case Reports"}],"best_oa_location":{"id":"doi:10.1136/jnnp.60.4.403","doi":"https://doi.org/10.1136/jnnp.60.4.403","is_oa":true,"landing_page_url":"https://doi.org/10.1136/jnnp.60.4.403","pdf_url":"https://jnnp.bmj.com/content/jnnp/60/4/403.full.pdf","source":{"id":"https://openalex.org/S134773490","display_name":"Journal of Neurology Neurosurgery & Psychiatry","issn_l":"0022-3050","issn":["0022-3050","1468-330X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-2","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319945","host_organization_name":"BMJ","host_organization_lineage":["https://openalex.org/P4310319945"],"host_organization_lineage_names":["BMJ"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Neurology, Neurosurgery &amp; Psychiatry","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9391000270843506,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2016356907.pdf","grobid_xml":"https://content.openalex.org/works/W2016356907.grobid-xml"},"referenced_works_count":43,"referenced_works":["https://openalex.org/W16641107","https://openalex.org/W38490725","https://openalex.org/W99777439","https://openalex.org/W103341460","https://openalex.org/W117129675","https://openalex.org/W192045032","https://openalex.org/W599451930","https://openalex.org/W1522435878","https://openalex.org/W1573496596","https://openalex.org/W1847168837","https://openalex.org/W1931777916","https://openalex.org/W1972806157","https://openalex.org/W1978063188","https://openalex.org/W1978580877","https://openalex.org/W1989474631","https://openalex.org/W2008854521","https://openalex.org/W2008984484","https://openalex.org/W2010883767","https://openalex.org/W2027407178","https://openalex.org/W2033638327","https://openalex.org/W2039754195","https://openalex.org/W2049823907","https://openalex.org/W2056287225","https://openalex.org/W2067202045","https://openalex.org/W2072543924","https://openalex.org/W2082423614","https://openalex.org/W2086288358","https://openalex.org/W2090057077","https://openalex.org/W2097835289","https://openalex.org/W2121229721","https://openalex.org/W2127645597","https://openalex.org/W2144438579","https://openalex.org/W2148080316","https://openalex.org/W2161571501","https://openalex.org/W2167311298","https://openalex.org/W2333192282","https://openalex.org/W2409624134","https://openalex.org/W2561502167","https://openalex.org/W2772874006","https://openalex.org/W2954411470","https://openalex.org/W4238974234","https://openalex.org/W6632697518","https://openalex.org/W6765880599"],"related_works":["https://openalex.org/W2131386474","https://openalex.org/W1101423082","https://openalex.org/W2772111173","https://openalex.org/W3162091997","https://openalex.org/W2916572400","https://openalex.org/W4300336642","https://openalex.org/W1652153503","https://openalex.org/W4414945147","https://openalex.org/W4389366067","https://openalex.org/W2018735312"],"abstract_inverted_index":{"BACKGROUND:":[0],"Progressive":[1],"supranuclear":[2],"palsy":[3],"(PSP)":[4],"is":[5,167],"an":[6],"akinetic-rigid":[7],"syndrome":[8],"of":[9,18,54,68,88,111,122,144,180],"unknown":[10],"aetiology":[11],"which":[12,48,72],"usually":[13],"presents":[14],"with":[15,39,56,137,153],"a":[16,66],"combination":[17],"unsteadiness,":[19],"bradykinesia,":[20],"and":[21,76,80,85,97,101,103,128],"disordered":[22],"eye":[23],"movement.":[24],"Speech":[25],"often":[26],"becomes":[27],"dysarthric":[28],"but":[29],"language":[30,57,90,130],"disorders":[31],"are":[32,45],"not":[33],"well":[34],"recognised.":[35],"METHODS:":[36],"Three":[37],"patients":[38,136,152],"PSP":[40],"(pathologically":[41],"confirmed":[42],"in":[43,47,134,151],"two)":[44],"reported":[46],"the":[49,142,170],"presenting":[50],"symptoms":[51],"were":[52,106,161],"those":[53],"difficulty":[55],"output.":[58],"RESULTS:":[59],"Neuropsychological":[60],"testing":[61],"showed":[62],"considerable":[63],"impairment":[64,114],"on":[65,86],"range":[67],"single":[69],"word":[70,102],"tasks":[71],"require":[73],"active":[74],"initiation":[75],"search":[77],"strategies":[78],"(letter":[79],"category":[81],"fluency,":[82],"sentence":[83,104],"completion),":[84],"tests":[87],"narrative":[89],"production.":[91],"By":[92],"contrast,":[93],"naming":[94],"from":[95,98],"pictures":[96],"verbal":[99],"descriptions,":[100],"comprehension":[105],"largely":[107],"intact.":[108],"The":[109],"degree":[110],"semantic":[112],"memory":[113],"was":[115],"also":[116],"slight.":[117],"CONCLUSIONS:":[118],"Relatively":[119],"selective":[120],"involvement":[121],"cognitive":[123],"processes":[124],"critical":[125],"for":[126],"planning":[127],"initiating":[129],"output":[131],"may":[132],"occur":[133],"some":[135],"PSP.":[138],"This":[139],"presentation":[140],"resembles":[141],"phenomenon":[143],"\"verbal":[145],"adynamia\"":[146],"or":[147],"\"dynamic":[148],"aphasia\"":[149],"seen":[150],"frontal":[154,175],"lobe":[155],"damage.":[156],"Although":[157],"definite":[158],"cortical":[159],"changes":[160],"present":[162],"at":[163],"postmortem":[164],"examination,":[165],"it":[166],"likely":[168],"that":[169],"neuropsychological":[171],"deficits":[172],"reflect":[173],"functional":[174],"deafferentation":[176],"secondary":[177],"to":[178],"interruption":[179],"frontostriatal":[181],"feedback":[182],"loops.":[183]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":4},{"year":2024,"cited_by_count":4},{"year":2022,"cited_by_count":1},{"year":2021,"cited_by_count":8},{"year":2020,"cited_by_count":2},{"year":2019,"cited_by_count":7},{"year":2018,"cited_by_count":4},{"year":2017,"cited_by_count":3},{"year":2016,"cited_by_count":1},{"year":2015,"cited_by_count":3},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":3},{"year":2012,"cited_by_count":3}],"updated_date":"2026-11-07T11:25:07.637180","created_date":"2016-06-24T00:00:00"}
