{"id":"https://openalex.org/W2015577087","doi":"https://doi.org/10.1074/jbc.m110.211912","title":"Substrate Specificity Overlap and Interaction between Adrenoleukodystrophy Protein (ALDP/ABCD1) and Adrenoleukodystrophy-related Protein (ALDRP/ABCD2)","display_name":"Substrate Specificity Overlap and Interaction between Adrenoleukodystrophy Protein (ALDP/ABCD1) and Adrenoleukodystrophy-related Protein (ALDRP/ABCD2)","publication_year":2011,"publication_date":"2011-01-06","ids":{"openalex":"https://openalex.org/W2015577087","doi":"https://doi.org/10.1074/jbc.m110.211912","mag":"2015577087","pmid":"https://pubmed.ncbi.nlm.nih.gov/21209459","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/3048694"},"language":"en","primary_location":{"id":"doi:10.1074/jbc.m110.211912","doi":"https://doi.org/10.1074/jbc.m110.211912","is_oa":true,"landing_page_url":"https://doi.org/10.1074/jbc.m110.211912","pdf_url":"http://www.jbc.org/article/S0021925820539525/pdf","source":{"id":"https://openalex.org/S140251998","display_name":"Journal of Biological Chemistry","issn_l":"0021-9258","issn":["0021-9258","1067-8816","1083-351X"],"is_oa":false,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-100","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Biological Chemistry","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","doaj","pubmed"],"open_access":{"is_oa":true,"oa_status":"hybrid","oa_url":"http://www.jbc.org/article/S0021925820539525/pdf","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5101475379","display_name":"Emmanuelle C. Genin","orcid":"https://orcid.org/0000-0003-3039-7101","observed_orcids":["https://orcid.org/0000-0003-3039-7101"]},"institutions":[{"id":"https://openalex.org/I1294671590","display_name":"Centre National de la Recherche Scientifique","ror":"https://ror.org/02feahw73","country_code":"FR","type":"government","lineage":["https://openalex.org/I1294671590"]},{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I177064439","display_name":"Universit\u00e9 de Bourgogne","ror":"https://ror.org/03k1bsr36","country_code":"FR","type":"education","lineage":["https://openalex.org/I177064439","https://openalex.org/I4405253280"]},{"id":"https://openalex.org/I4210139033","display_name":"Centre de recherche Translationnelle en M\u00e9decine mol\u00e9culaire","ror":"https://ror.org/04d70nb60","country_code":"FR","type":"facility","lineage":["https://openalex.org/I154526488","https://openalex.org/I159885104","https://openalex.org/I2746051580","https://openalex.org/I4210117091","https://openalex.org/I4210135996","https://openalex.org/I4210139033","https://openalex.org/I4399657933","https://openalex.org/I4405253280"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Emmanuelle C. Genin","raw_affiliation_strings":["From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I1294671590","https://openalex.org/I154526488","https://openalex.org/I177064439","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I177064439"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5052167957","display_name":"Flore Geillon","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1294671590","display_name":"Centre National de la Recherche Scientifique","ror":"https://ror.org/02feahw73","country_code":"FR","type":"government","lineage":["https://openalex.org/I1294671590"]},{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I177064439","display_name":"Universit\u00e9 de Bourgogne","ror":"https://ror.org/03k1bsr36","country_code":"FR","type":"education","lineage":["https://openalex.org/I177064439","https://openalex.org/I4405253280"]},{"id":"https://openalex.org/I4210139033","display_name":"Centre de recherche Translationnelle en M\u00e9decine mol\u00e9culaire","ror":"https://ror.org/04d70nb60","country_code":"FR","type":"facility","lineage":["https://openalex.org/I154526488","https://openalex.org/I159885104","https://openalex.org/I2746051580","https://openalex.org/I4210117091","https://openalex.org/I4210135996","https://openalex.org/I4210139033","https://openalex.org/I4399657933","https://openalex.org/I4405253280"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Flore Geillon","raw_affiliation_strings":["From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I1294671590","https://openalex.org/I154526488","https://openalex.org/I177064439","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I177064439"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5007715743","display_name":"Catherine Gondcaille","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I1294671590","display_name":"Centre National de la Recherche Scientifique","ror":"https://ror.org/02feahw73","country_code":"FR","type":"government","lineage":["https://openalex.org/I1294671590"]},{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I177064439","display_name":"Universit\u00e9 de Bourgogne","ror":"https://ror.org/03k1bsr36","country_code":"FR","type":"education","lineage":["https://openalex.org/I177064439","https://openalex.org/I4405253280"]},{"id":"https://openalex.org/I4210139033","display_name":"Centre de recherche Translationnelle en M\u00e9decine mol\u00e9culaire","ror":"https://ror.org/04d70nb60","country_code":"FR","type":"facility","lineage":["https://openalex.org/I154526488","https://openalex.org/I159885104","https://openalex.org/I2746051580","https://openalex.org/I4210117091","https://openalex.org/I4210135996","https://openalex.org/I4210139033","https://openalex.org/I4399657933","https://openalex.org/I4405253280"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Catherine Gondcaille","raw_affiliation_strings":["From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I1294671590","https://openalex.org/I154526488","https://openalex.org/I177064439","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I177064439"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5053654765","display_name":"Anne Athias","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Anne Athias","raw_affiliation_strings":["Plateforme de Lipidomique-IFR100, H\u00f4pital du Bocage, Dijon F-21000, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Plateforme de Lipidomique-IFR100, H\u00f4pital du Bocage, Dijon F-21000, France","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5002032049","display_name":"Philippe Gambert","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Philippe Gambert","raw_affiliation_strings":["Plateforme de Lipidomique-IFR100, H\u00f4pital du Bocage, Dijon F-21000, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Plateforme de Lipidomique-IFR100, H\u00f4pital du Bocage, Dijon F-21000, France","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5066111301","display_name":"Doriane Trompier","orcid":"https://orcid.org/0000-0002-0746-1753","observed_orcids":["https://orcid.org/0000-0002-0746-1753"]},"institutions":[{"id":"https://openalex.org/I1294671590","display_name":"Centre National de la Recherche Scientifique","ror":"https://ror.org/02feahw73","country_code":"FR","type":"government","lineage":["https://openalex.org/I1294671590"]},{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I177064439","display_name":"Universit\u00e9 de Bourgogne","ror":"https://ror.org/03k1bsr36","country_code":"FR","type":"education","lineage":["https://openalex.org/I177064439","https://openalex.org/I4405253280"]},{"id":"https://openalex.org/I4210139033","display_name":"Centre de recherche Translationnelle en M\u00e9decine mol\u00e9culaire","ror":"https://ror.org/04d70nb60","country_code":"FR","type":"facility","lineage":["https://openalex.org/I154526488","https://openalex.org/I159885104","https://openalex.org/I2746051580","https://openalex.org/I4210117091","https://openalex.org/I4210135996","https://openalex.org/I4210139033","https://openalex.org/I4399657933","https://openalex.org/I4405253280"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"Doriane Trompier","raw_affiliation_strings":["From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I1294671590","https://openalex.org/I154526488","https://openalex.org/I177064439","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I177064439"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5043662104","display_name":"St\u00e9phane Savary","orcid":"https://orcid.org/0000-0002-9237-1727","observed_orcids":["https://orcid.org/0000-0002-9237-1727"]},"institutions":[{"id":"https://openalex.org/I154526488","display_name":"Inserm","ror":"https://ror.org/02vjkv261","country_code":"FR","type":"government","lineage":["https://openalex.org/I154526488"]},{"id":"https://openalex.org/I177064439","display_name":"Universit\u00e9 de Bourgogne","ror":"https://ror.org/03k1bsr36","country_code":"FR","type":"education","lineage":["https://openalex.org/I177064439","https://openalex.org/I4405253280"]},{"id":"https://openalex.org/I4210139033","display_name":"Centre de recherche Translationnelle en M\u00e9decine mol\u00e9culaire","ror":"https://ror.org/04d70nb60","country_code":"FR","type":"facility","lineage":["https://openalex.org/I154526488","https://openalex.org/I159885104","https://openalex.org/I2746051580","https://openalex.org/I4210117091","https://openalex.org/I4210135996","https://openalex.org/I4210139033","https://openalex.org/I4399657933","https://openalex.org/I4405253280"]}],"countries":["FR"],"is_corresponding":true,"raw_author_name":"St\u00e9phane Savary","raw_affiliation_strings":["From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and. Electronic address: stsavary@u-bourgogne.fr","From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,; the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and. Electronic address: stsavary@u-bourgogne.fr","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I177064439","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"From the INSERM, UMR866, Centre de Recherche Lipides, Nutrition, Cancer, Dijon F-21000,","institution_ids":["https://openalex.org/I154526488","https://openalex.org/I4210139033"]},{"raw_affiliation_string":"the Universit\u00e9 de Bourgogne, Laboratoire de Biochimie M\u00e9tabolique et Nutritionnelle (LBMN), GDRCNRS 2583, 6 Bd Gabriel, Dijon F-21000, and","institution_ids":["https://openalex.org/I177064439"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":4,"corresponding_author_ids":["https://openalex.org/A5043662104"],"corresponding_institution_ids":["https://openalex.org/I154526488","https://openalex.org/I177064439","https://openalex.org/I4210139033"],"apc_list":{"value":3430,"currency":"USD","value_usd":3430},"apc_paid":{"value":3430,"currency":"USD","value_usd":3430},"fwci":4.7917,"has_fulltext":true,"cited_by_count":56,"citation_normalized_percentile":{"value":0.96404399,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":88,"max":99},"biblio":{"volume":"286","issue":"10","first_page":"8075","last_page":"8084"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11027","display_name":"Metabolism and Genetic Disorders","score":0.9901999831199646,"subfield":{"id":"https://openalex.org/subfields/1308","display_name":"Clinical Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11027","display_name":"Metabolism and Genetic Disorders","score":0.9901999831199646,"subfield":{"id":"https://openalex.org/subfields/1308","display_name":"Clinical Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T10945","display_name":"Lysosomal Storage Disorders Research","score":0.0034000000450760126,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T13481","display_name":"Neurological diseases and metabolism","score":0.0012000000569969416,"subfield":{"id":"https://openalex.org/subfields/2808","display_name":"Neurology"},"field":{"id":"https://openalex.org/fields/28","display_name":"Neuroscience"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/x-linked-adrenoleukodystrophy","display_name":"X-linked adrenoleukodystrophy","score":0.8970000147819519},{"id":"https://openalex.org/keywords/abcd1","display_name":"ABCD1","score":0.8389999866485596},{"id":"https://openalex.org/keywords/abcd2","display_name":"ABCD2","score":0.9290000200271606},{"id":"https://openalex.org/keywords/aldp","display_name":"ALDP","score":0.9100000262260437},{"id":"https://openalex.org/keywords/very-long-chain-fatty-acids","display_name":"very long chain fatty acids","score":0.871999979019165},{"id":"https://openalex.org/keywords/peroxisomal-beta-oxidation","display_name":"peroxisomal beta-oxidation","score":0.8180000185966492},{"id":"https://openalex.org/keywords/docosahexaenoic-acid","display_name":"docosahexaenoic acid","score":0.8700000047683716},{"id":"https://openalex.org/keywords/substrate-specificity","display_name":"substrate specificity","score":0.6370000243186951},{"id":"https://openalex.org/keywords/protein-protein-interaction","display_name":"protein-protein interaction","score":0.8809999823570251},{"id":"https://openalex.org/keywords/phospholipid-fatty-acid-composition","display_name":"phospholipid fatty acid composition","score":0.871999979019165}],"concepts":[{"id":"https://openalex.org/C2777150068","wikidata":"https://www.wikidata.org/wiki/Q366964","display_name":"Adrenoleukodystrophy","level":4,"score":0.9339375495910645},{"id":"https://openalex.org/C44312359","wikidata":"https://www.wikidata.org/wiki/Q286958","display_name":"ATP-binding cassette transporter","level":4,"score":0.8119626045227051},{"id":"https://openalex.org/C127078168","wikidata":"https://www.wikidata.org/wiki/Q138639","display_name":"Peroxisome","level":3,"score":0.7160446643829346},{"id":"https://openalex.org/C55493867","wikidata":"https://www.wikidata.org/wiki/Q7094","display_name":"Biochemistry","level":1,"score":0.5636261105537415},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.47755298018455505},{"id":"https://openalex.org/C104317684","wikidata":"https://www.wikidata.org/wiki/Q7187","display_name":"Gene","level":2,"score":0.3392504155635834},{"id":"https://openalex.org/C185592680","wikidata":"https://www.wikidata.org/wiki/Q2329","display_name":"Chemistry","level":0,"score":0.3206467628479004},{"id":"https://openalex.org/C149011108","wikidata":"https://www.wikidata.org/wiki/Q652985","display_name":"Transporter","level":3,"score":0.3052174150943756}],"mesh":[{"descriptor_ui":"D000074061","descriptor_name":"ATP Binding Cassette Transporter, Subfamily D","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000326","descriptor_name":"Adrenoleukodystrophy","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D000326","descriptor_name":"Adrenoleukodystrophy","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":false},{"descriptor_ui":"D000818","descriptor_name":"Animals","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005227","descriptor_name":"Fatty Acids","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D005227","descriptor_name":"Fatty Acids","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":true},{"descriptor_ui":"D010084","descriptor_name":"Oxidation-Reduction","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018528","descriptor_name":"ATP-Binding Cassette Transporters","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D018528","descriptor_name":"ATP-Binding Cassette Transporters","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":true},{"descriptor_ui":"D020675","descriptor_name":"Peroxisomes","qualifier_ui":"Q000201","qualifier_name":"enzymology","is_major_topic":true},{"descriptor_ui":"D020675","descriptor_name":"Peroxisomes","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D045744","descriptor_name":"Cell Line, Tumor","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D051381","descriptor_name":"Rats","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":6,"locations":[{"id":"doi:10.1074/jbc.m110.211912","doi":"https://doi.org/10.1074/jbc.m110.211912","is_oa":true,"landing_page_url":"https://doi.org/10.1074/jbc.m110.211912","pdf_url":"http://www.jbc.org/article/S0021925820539525/pdf","source":{"id":"https://openalex.org/S140251998","display_name":"Journal of Biological Chemistry","issn_l":"0021-9258","issn":["0021-9258","1067-8816","1083-351X"],"is_oa":false,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-100","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Biological Chemistry","raw_type":"journal-article"},{"id":"pmh:oai:europepmc.org:2307583","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/3048694","pdf_url":null,"source":{"id":"https://openalex.org/S4306400806","display_name":"Europe PMC (PubMed Central)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1303153112","host_organization_name":"European Bioinformatics Institute","host_organization_lineage":["https://openalex.org/I1303153112"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":null,"raw_type":"Text"},{"id":"pmh:oai:pubmedcentral.nih.gov:3048694","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/3048694","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"J Biol Chem","raw_type":"Text"},{"id":"pmid:21209459","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/21209459","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Journal of biological chemistry","raw_type":"Journal Article"},{"id":"pmh:oai:HAL:hal-01221369v1","doi":null,"is_oa":true,"landing_page_url":"https://hal.science/hal-01221369","pdf_url":"https://hal.science/hal-01221369v1/document","source":{"id":"https://openalex.org/S4306402512","display_name":"HAL","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I4405252976","host_organization_name":"Centre pour la Communication Scientifique Directe","host_organization_lineage":["https://openalex.org/I4405252976"],"host_organization_lineage_names":[],"type":"repository"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Journal of Biological Chemistry, 2011, 286 (10), pp.8075-8084. &#x27E8;10.1074/jbc.M110.211912&#x27E9;","raw_type":"info:eu-repo/semantics/article"},{"id":"pmh:oai:orbi.ulg.ac.be:2268/115342","doi":null,"is_oa":true,"landing_page_url":"https://orbi.uliege.be/handle/2268/115342","pdf_url":null,"source":{"id":"https://openalex.org/S4306401300","display_name":"ORBi (University of Li\u00e8ge)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I157674565","host_organization_name":"University of Li\u00e8ge","host_organization_lineage":["https://openalex.org/I157674565"],"host_organization_lineage_names":[],"type":"repository"},"license":"other-oa","license_id":"https://openalex.org/licenses/other-oa","version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Journal of Biological Chemistry, 286 (10), 8075-84 (2011-03-11)","raw_type":"http://purl.org/coar/resource_type/c_6501"}],"best_oa_location":{"id":"doi:10.1074/jbc.m110.211912","doi":"https://doi.org/10.1074/jbc.m110.211912","is_oa":true,"landing_page_url":"https://doi.org/10.1074/jbc.m110.211912","pdf_url":"http://www.jbc.org/article/S0021925820539525/pdf","source":{"id":"https://openalex.org/S140251998","display_name":"Journal of Biological Chemistry","issn_l":"0021-9258","issn":["0021-9258","1067-8816","1083-351X"],"is_oa":false,"is_in_doaj":true,"is_core":true,"listed_in":["anvur-scientific","cwts-core","doaj","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-100","vabb-shw"],"host_organization":"https://openalex.org/P4310320990","host_organization_name":"Elsevier BV","host_organization_lineage":["https://openalex.org/P4310320990"],"host_organization_lineage_names":["Elsevier BV"],"type":"journal"},"license":"cc-by","license_id":"https://openalex.org/licenses/cc-by","version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Biological Chemistry","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":0.8048999905586243,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[],"awards":[],"funders":[{"id":"https://openalex.org/F4320327269","display_name":"Conseil r\u00e9gional de Bourgogne-Franche-Comt\u00e9","ror":"https://ror.org/04t9bwz39"}],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2015577087.pdf","grobid_xml":"https://content.openalex.org/works/W2015577087.grobid-xml"},"referenced_works_count":35,"referenced_works":["https://openalex.org/W1523946871","https://openalex.org/W1606277396","https://openalex.org/W1913087900","https://openalex.org/W1970958008","https://openalex.org/W1971007745","https://openalex.org/W1974449499","https://openalex.org/W2002285852","https://openalex.org/W2005093647","https://openalex.org/W2010056900","https://openalex.org/W2032106401","https://openalex.org/W2035007022","https://openalex.org/W2037167329","https://openalex.org/W2040079641","https://openalex.org/W2044929463","https://openalex.org/W2051446956","https://openalex.org/W2057729851","https://openalex.org/W2059824676","https://openalex.org/W2066656769","https://openalex.org/W2071626794","https://openalex.org/W2074571932","https://openalex.org/W2074995622","https://openalex.org/W2079075112","https://openalex.org/W2081939141","https://openalex.org/W2099862428","https://openalex.org/W2104564418","https://openalex.org/W2119068792","https://openalex.org/W2120211298","https://openalex.org/W2124230153","https://openalex.org/W2124546457","https://openalex.org/W2135684554","https://openalex.org/W2138312139","https://openalex.org/W2138878645","https://openalex.org/W2141570423","https://openalex.org/W2158601400","https://openalex.org/W2168526937"],"related_works":["https://openalex.org/W2124546457","https://openalex.org/W2104564418","https://openalex.org/W2116753947","https://openalex.org/W1967549048","https://openalex.org/W2371812736","https://openalex.org/W2011304265","https://openalex.org/W2057729851","https://openalex.org/W1956831573","https://openalex.org/W2040022730","https://openalex.org/W1986966017"],"abstract_inverted_index":{"X-linked":[0],"adrenoleukodystrophy":[1],"(X-ALD)":[2],"is":[3,30,198],"a":[4,16,35,103,107,111,186,201,222,239],"neurodegenerative":[5],"disorder":[6],"caused":[7],"by":[8,62,77,211],"mutations":[9],"in":[10,102,139,226,244],"the":[11,20,38,49,51,70,74,91,100,119,122,129,145,164,178,190,218,227,245],"ABCD1":[12],"gene,":[13],"which":[14],"encodes":[15],"peroxisomal":[17],"member":[18],"of":[19,40,42,54,64,73,93,106,121,124,147,149,168,181,189,224,229,235,242,247],"ATP-binding":[21],"cassette":[22],"(ABC)":[23],"transporter":[24],"subfamily":[25],"D":[26],"called":[27],"ALDP.":[28],"ALDP":[29,57,83,194,207],"supposed":[31],"to":[32,200],"function":[33,92],"as":[34,141,143],"homodimer":[36],"allowing":[37,99],"entry":[39],"CoA-esters":[41],"very-long":[43],"chain":[44],"fatty":[45,130,137,165],"acids":[46],"(VLCFA)":[47],"into":[48,90],"peroxisome,":[50],"unique":[52],"site":[53],"their":[55],"\u03b2-oxidation.":[56],"deficiency":[58],"can":[59],"be":[60],"corrected":[61],"overexpression":[63],"ALDRP,":[65,94],"its":[66,80],"closest":[67],"homolog.":[68],"However,":[69],"exact":[71],"nature":[72],"substrates":[75],"transported":[76],"ALDRP":[78,125,205,225,243],"and":[79,135,155,172,177,206,215],"relationships":[81],"with":[82,233],"still":[84],"remain":[85],"unclear.":[86],"To":[87],"gain":[88],"insight":[89],"we":[95,184,209],"used":[96],"cell":[97],"models":[98],"induction":[101],"dose-dependent":[104],"manner":[105],"wild":[108],"type":[109],"or":[110],"mutated":[112],"non-functional":[113],"ALDRP-EGFP":[114,192],"fusion":[115],"protein.":[116],"We":[117,158],"explored":[118],"consequences":[120],"changes":[123],"expression":[126,179],"levels":[127,146],"on":[128,144,193],"acid":[131,166],"content":[132,167],"(saturated,":[133],"monounsaturated,":[134],"polyunsaturated":[136],"acids)":[138],"phospholipids":[140],"well":[142],"\u03b2-oxidation":[148,219],"3":[150],"suspected":[151],"substrates:":[152],"C26:0,":[153],"C24:0,":[154],"C22:6n-3":[156],"(DHA).":[157],"found":[159],"an":[160],"inverse":[161],"correlation":[162],"between":[163,204],"saturated":[169,230],"(C26:0,":[170],"C24:0)":[171],"monounsaturated":[173],"(C26:1,":[174],"C24:1)":[175],"VLCFA":[176,231],"level":[180],"ALDRP.":[182],"Interestingly,":[183],"obtained":[185],"transdominant-negative":[187],"effect":[188,197],"inactive":[191],"function.":[195],"This":[196],"due":[199],"physical":[202],"interaction":[203],"that":[208,234],"evidenced":[210],"proximity":[212],"ligation":[213],"assays":[214,220],"coimmunoprecipitation.":[216],"Finally,":[217],"demonstrate":[221],"role":[223],"metabolism":[228,246],"(redundant":[232],"ALDP)":[236],"but":[237],"also":[238],"specific":[240],"involvement":[241],"DHA.":[248]},"counts_by_year":[{"year":2024,"cited_by_count":2},{"year":2023,"cited_by_count":4},{"year":2022,"cited_by_count":3},{"year":2021,"cited_by_count":2},{"year":2020,"cited_by_count":2},{"year":2019,"cited_by_count":3},{"year":2018,"cited_by_count":1},{"year":2017,"cited_by_count":5},{"year":2016,"cited_by_count":3},{"year":2015,"cited_by_count":5},{"year":2014,"cited_by_count":6},{"year":2013,"cited_by_count":8},{"year":2012,"cited_by_count":8}],"updated_date":"2026-11-07T11:25:07.637180","created_date":"2016-06-24T00:00:00"}
