{"id":"https://openalex.org/W2007265073","doi":"https://doi.org/10.1111/j.1399-6576.2005.00727.x","title":"Anaesthetic management of Osler\u2013Weber\u2013Rendu syndrome with coexisting congenital methaemoglobinaemia","display_name":"Anaesthetic management of Osler\u2013Weber\u2013Rendu syndrome with coexisting congenital methaemoglobinaemia","publication_year":2005,"publication_date":"2005-04-29","ids":{"openalex":"https://openalex.org/W2007265073","doi":"https://doi.org/10.1111/j.1399-6576.2005.00727.x","mag":"2007265073","pmid":"https://pubmed.ncbi.nlm.nih.gov/16146483"},"language":"en","primary_location":{"id":"doi:10.1111/j.1399-6576.2005.00727.x","doi":"https://doi.org/10.1111/j.1399-6576.2005.00727.x","is_oa":false,"landing_page_url":"https://doi.org/10.1111/j.1399-6576.2005.00727.x","pdf_url":null,"source":{"id":"https://openalex.org/S177321322","display_name":"Acta Anaesthesiologica Scandinavica","issn_l":"0001-5172","issn":["0001-5172","1399-6576"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Acta Anaesthesiologica Scandinavica","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"D. Sharma","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I63739035","display_name":"All India Institute of Medical Sciences","ror":"https://ror.org/02dwcqs71","country_code":"IN","type":"education","lineage":["https://openalex.org/I2799351866","https://openalex.org/I4210148677","https://openalex.org/I63739035"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"D. Sharma","raw_affiliation_strings":["Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India","institution_ids":["https://openalex.org/I63739035"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111975594","display_name":"M. P. Pandia","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I63739035","display_name":"All India Institute of Medical Sciences","ror":"https://ror.org/02dwcqs71","country_code":"IN","type":"education","lineage":["https://openalex.org/I2799351866","https://openalex.org/I4210148677","https://openalex.org/I63739035"]}],"countries":["IN"],"is_corresponding":true,"raw_author_name":"M. P. Pandia","raw_affiliation_strings":["Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India","institution_ids":["https://openalex.org/I63739035"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5086448672","display_name":"Parmod Kumar Bithal","orcid":"https://orcid.org/0000-0001-5348-2814","observed_orcids":["https://orcid.org/0000-0001-5348-2814"]},"institutions":[{"id":"https://openalex.org/I63739035","display_name":"All India Institute of Medical Sciences","ror":"https://ror.org/02dwcqs71","country_code":"IN","type":"education","lineage":["https://openalex.org/I2799351866","https://openalex.org/I4210148677","https://openalex.org/I63739035"]}],"countries":["IN"],"is_corresponding":false,"raw_author_name":"P. K. Bithal","raw_affiliation_strings":["Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neuroanaesthesiology, Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India","institution_ids":["https://openalex.org/I63739035"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5111975594"],"corresponding_institution_ids":["https://openalex.org/I63739035"],"apc_list":{"value":4430,"currency":"USD","value_usd":4430},"apc_paid":null,"fwci":0.6703,"has_fulltext":false,"cited_by_count":20,"citation_normalized_percentile":{"value":0.66284257,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":95},"biblio":{"volume":"49","issue":"9","first_page":"1391","last_page":"1394"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12199","display_name":"Vascular Anomalies and Treatments","score":0.6615999937057495,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12199","display_name":"Vascular Anomalies and Treatments","score":0.6615999937057495,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics (clinical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T12845","display_name":"Methemoglobinemia and Tumor Lysis Syndrome","score":0.16210000216960907,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10436","display_name":"Anesthesia and Sedative Agents","score":0.04360000044107437,"subfield":{"id":"https://openalex.org/subfields/2703","display_name":"Anesthesiology and Pain Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hereditary-hemorrhagic-telangiectasia","display_name":"hereditary hemorrhagic telangiectasia","score":0.9739999771118164},{"id":"https://openalex.org/keywords/pulmonary-arteriovenous-malformation","display_name":"pulmonary arteriovenous malformation","score":0.9380000233650208},{"id":"https://openalex.org/keywords/cyanosis","display_name":"cyanosis","score":0.8970000147819519},{"id":"https://openalex.org/keywords/cerebral-angiography","display_name":"cerebral angiography","score":0.7979999780654907},{"id":"https://openalex.org/keywords/general-anesthesia","display_name":"general anesthesia","score":0.8690000176429749},{"id":"https://openalex.org/keywords/positive-pressure-ventilation","display_name":"positive pressure ventilation","score":0.9330000281333923},{"id":"https://openalex.org/keywords/arterial-oxygenation","display_name":"arterial oxygenation","score":0.7319999933242798},{"id":"https://openalex.org/keywords/pediatric-anesthesia","display_name":"pediatric anesthesia","score":0.8389999866485596}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9782334566116333},{"id":"https://openalex.org/C42219234","wikidata":"https://www.wikidata.org/wiki/Q131130","display_name":"Anesthesia","level":1,"score":0.5559833645820618},{"id":"https://openalex.org/C2776983577","wikidata":"https://www.wikidata.org/wiki/Q166543","display_name":"General anaesthesia","level":2,"score":0.514498233795166},{"id":"https://openalex.org/C70289976","wikidata":"https://www.wikidata.org/wiki/Q17143603","display_name":"Oxygenation","level":2,"score":0.4116032123565674},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.39373579621315},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.32027876377105713}],"mesh":[{"descriptor_ui":"D000758","descriptor_name":"Anesthesia","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D000768","descriptor_name":"Anesthesia, General","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001784","descriptor_name":"Blood Gas Analysis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002533","descriptor_name":"Cerebral Angiography","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003241","descriptor_name":"Consanguinity","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003490","descriptor_name":"Cyanosis","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D006439","descriptor_name":"Hemodynamics","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008168","descriptor_name":"Lung","qualifier_ui":"Q000000981","qualifier_name":"diagnostic imaging","is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008708","descriptor_name":"Methemoglobinemia","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D008708","descriptor_name":"Methemoglobinemia","qualifier_ui":"Q000151","qualifier_name":"congenital","is_major_topic":true},{"descriptor_ui":"D013683","descriptor_name":"Telangiectasia, Hereditary Hemorrhagic","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true}],"locations_count":2,"locations":[{"id":"doi:10.1111/j.1399-6576.2005.00727.x","doi":"https://doi.org/10.1111/j.1399-6576.2005.00727.x","is_oa":false,"landing_page_url":"https://doi.org/10.1111/j.1399-6576.2005.00727.x","pdf_url":null,"source":{"id":"https://openalex.org/S177321322","display_name":"Acta Anaesthesiologica Scandinavica","issn_l":"0001-5172","issn":["0001-5172","1399-6576"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Acta Anaesthesiologica Scandinavica","raw_type":"journal-article"},{"id":"pmid:16146483","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/16146483","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Acta anaesthesiologica Scandinavica","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.98580002784729,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":9,"referenced_works":["https://openalex.org/W1511967074","https://openalex.org/W1586707763","https://openalex.org/W1972165192","https://openalex.org/W1991135405","https://openalex.org/W2024832550","https://openalex.org/W2051714564","https://openalex.org/W2053933759","https://openalex.org/W2110158978","https://openalex.org/W3152278779"],"related_works":["https://openalex.org/W4319460644","https://openalex.org/W2795785044","https://openalex.org/W2076939717","https://openalex.org/W2410027888","https://openalex.org/W2415962408","https://openalex.org/W4400479135","https://openalex.org/W2032737647","https://openalex.org/W4406411277","https://openalex.org/W4391382870","https://openalex.org/W2063188731"],"abstract_inverted_index":{"A":[0],"9-year-old":[1],"cyanosed":[2],"child":[3],"suffering":[4],"from":[5],"Osler-Weber-Rendu":[6,39],"syndrome":[7,40],"with":[8,42,80],"bilateral":[9],"pulmonary":[10],"arteriovenous":[11],"malformations":[12],"(PAVMs)":[13],"was":[14,78],"posted":[15],"for":[16,61],"cerebral":[17],"angiography":[18],"under":[19],"general":[20],"anaesthesia.":[21],"Careful":[22],"preanaesthetic":[23,94],"evaluation":[24],"led":[25],"to":[26,93],"the":[27,63],"diagnosis":[28],"of":[29,38,53,101],"coexisting":[30,41],"congenital":[31,43],"methaemoglobinaemia.":[32,44],"There":[33],"is":[34],"no":[35],"previous":[36],"report":[37,46],"This":[45],"emphasizes":[47],"that":[48],"a":[49,66,72],"second":[50],"contributory":[51],"cause":[52],"cyanosis":[54],"must":[55],"be":[56,69],"suspected":[57],"and":[58,99],"meticulously":[59],"looked":[60],"if":[62],"symptomatology":[64],"in":[65,82],"patient":[67],"cannot":[68],"explained":[70],"by":[71],"single":[73],"established":[74],"diagnosis.":[75],"Positive-pressure":[76],"ventilation":[77],"associated":[79],"reduction":[81],"arterial":[83],"oxygenation":[84],"despite":[85],"an":[86],"increasing":[87],"inspired":[88],"oxygen":[89],"concentration,":[90],"which":[91],"returned":[92],"levels":[95],"only":[96],"after":[97],"extubation":[98],"resumption":[100],"spontaneous":[102],"respiration.":[103]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2024,"cited_by_count":1},{"year":2021,"cited_by_count":2},{"year":2020,"cited_by_count":1},{"year":2018,"cited_by_count":1},{"year":2016,"cited_by_count":1},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":2}],"updated_date":"2026-11-05T12:25:35.769452","created_date":"2016-06-24T00:00:00"}
