{"id":"https://openalex.org/W2002255702","doi":"https://doi.org/10.1620/tjem.154.365","title":"A new bleeding tendency due to hereditary hyper .ALPHA.2-macroglobulinemia.","display_name":"A new bleeding tendency due to hereditary hyper .ALPHA.2-macroglobulinemia.","publication_year":1988,"publication_date":"1988-01-01","ids":{"openalex":"https://openalex.org/W2002255702","doi":"https://doi.org/10.1620/tjem.154.365","mag":"2002255702","pmid":"https://pubmed.ncbi.nlm.nih.gov/2460968"},"language":"en","primary_location":{"id":"doi:10.1620/tjem.154.365","doi":"https://doi.org/10.1620/tjem.154.365","is_oa":true,"landing_page_url":"https://doi.org/10.1620/tjem.154.365","pdf_url":"https://www.jstage.jst.go.jp/article/tjem1920/154/4/154_4_365/_pdf","source":{"id":"https://openalex.org/S189069745","display_name":"The Tohoku Journal of Experimental Medicine","issn_l":"0040-8727","issn":["0040-8727","1349-3329"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","jufo-1","ki-jl-1","medline","norway-1","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310313307","host_organization_name":"Tohoku University","host_organization_lineage":["https://openalex.org/P4310313307"],"host_organization_lineage_names":["Tohoku University"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Tohoku Journal of Experimental Medicine","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://www.jstage.jst.go.jp/article/tjem1920/154/4/154_4_365/_pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5033844318","display_name":"Yasuyuki Endo","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I203765153","display_name":"Akita University","ror":"https://ror.org/03hv1ad10","country_code":"JP","type":"education","lineage":["https://openalex.org/I203765153"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"YASUYUKI ENDO","raw_affiliation_strings":["The Third Department of Internal Medicine, Akita University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5009138532","display_name":"Keiko Iwamoto","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I203765153","display_name":"Akita University","ror":"https://ror.org/03hv1ad10","country_code":"JP","type":"education","lineage":["https://openalex.org/I203765153"]},{"id":"https://openalex.org/I4210132405","display_name":"Akita University Hospital","ror":"https://ror.org/02szmmq82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210132405"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"KEIKO IWAMOTO","raw_affiliation_strings":["The Third Department of Internal Medicine, Akita University School of Medicine","the Third Department of Internal Medicine, Akita University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153"]},{"raw_affiliation_string":"the Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153","https://openalex.org/I4210132405"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5108699593","display_name":"Shigeo Mamiya","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I203765153","display_name":"Akita University","ror":"https://ror.org/03hv1ad10","country_code":"JP","type":"education","lineage":["https://openalex.org/I203765153"]},{"id":"https://openalex.org/I4210132405","display_name":"Akita University Hospital","ror":"https://ror.org/02szmmq82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210132405"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"SHIGEO MAMIYA","raw_affiliation_strings":["The Third Department of Internal Medicine, Akita University School of Medicine","the Third Department of Internal Medicine, Akita University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153"]},{"raw_affiliation_string":"the Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153","https://openalex.org/I4210132405"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5070300997","display_name":"Hidetaka Niitsu","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I203765153","display_name":"Akita University","ror":"https://ror.org/03hv1ad10","country_code":"JP","type":"education","lineage":["https://openalex.org/I203765153"]},{"id":"https://openalex.org/I4210132405","display_name":"Akita University Hospital","ror":"https://ror.org/02szmmq82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210132405"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"HIDETAKA NIITSU","raw_affiliation_strings":["The Third Department of Internal Medicine, Akita University School of Medicine","the Third Department of Internal Medicine, Akita University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153"]},{"raw_affiliation_string":"the Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153","https://openalex.org/I4210132405"]}]},{"author_position":"middle","author":{"id":null,"display_name":"TOSHIHIRO ITOH","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I203765153","display_name":"Akita University","ror":"https://ror.org/03hv1ad10","country_code":"JP","type":"education","lineage":["https://openalex.org/I203765153"]},{"id":"https://openalex.org/I4210132405","display_name":"Akita University Hospital","ror":"https://ror.org/02szmmq82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210132405"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"TOSHIHIRO ITOH","raw_affiliation_strings":["The Third Department of Internal Medicine, Akita University School of Medicine","the Third Department of Internal Medicine, Akita University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153"]},{"raw_affiliation_string":"the Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153","https://openalex.org/I4210132405"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5038408960","display_name":"AKIRA B. MIURA","orcid":"https://orcid.org/0000-0003-0388-9696","observed_orcids":["https://orcid.org/0000-0003-0388-9696"]},"institutions":[{"id":"https://openalex.org/I203765153","display_name":"Akita University","ror":"https://ror.org/03hv1ad10","country_code":"JP","type":"education","lineage":["https://openalex.org/I203765153"]},{"id":"https://openalex.org/I4210132405","display_name":"Akita University Hospital","ror":"https://ror.org/02szmmq82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210132405"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"AKIRA B. MIURA","raw_affiliation_strings":["The Third Department of Internal Medicine, Akita University School of Medicine","the Third Department of Internal Medicine, Akita University School of Medicine"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153"]},{"raw_affiliation_string":"the Third Department of Internal Medicine, Akita University School of Medicine","institution_ids":["https://openalex.org/I203765153","https://openalex.org/I4210132405"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":true,"cited_by_count":1,"citation_normalized_percentile":{"value":0.08914778,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":94},"biblio":{"volume":"154","issue":"4","first_page":"365","last_page":"373"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10881","display_name":"Blood Coagulation and Thrombosis Mechanisms","score":0.79830002784729,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10881","display_name":"Blood Coagulation and Thrombosis Mechanisms","score":0.79830002784729,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","score":0.0908999964594841,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10620","display_name":"Protease and Inhibitor Mechanisms","score":0.04619999974966049,"subfield":{"id":"https://openalex.org/subfields/1306","display_name":"Cancer Research"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hemorrhagic-diathesis","display_name":"bleeding tendency","score":0.9300000071525574},{"id":"https://openalex.org/keywords/prolonged-activated-partial-thromboplastin-time","display_name":"prolonged activated partial thromboplastin time","score":0.9039999842643738},{"id":"https://openalex.org/keywords/recalcification-time","display_name":"recalcification time","score":0.6610000133514404},{"id":"https://openalex.org/keywords/autosomal-dominant-inheritance","display_name":"autosomal dominant inheritance","score":0.8820000290870667},{"id":"https://openalex.org/keywords/plasma-protein-electrophoresis","display_name":"plasma protein electrophoresis","score":0.5929999947547913}],"concepts":[{"id":"https://openalex.org/C188997412","wikidata":"https://www.wikidata.org/wiki/Q1640386","display_name":"Proband","level":4,"score":0.7664706707000732},{"id":"https://openalex.org/C2778261982","wikidata":"https://www.wikidata.org/wiki/Q1755136","display_name":"Partial thromboplastin time","level":3,"score":0.619543194770813},{"id":"https://openalex.org/C2776391228","wikidata":"https://www.wikidata.org/wiki/Q4118092","display_name":"Macroglobulinemia","level":3,"score":0.5241939425468445},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.5061575770378113},{"id":"https://openalex.org/C91238131","wikidata":"https://www.wikidata.org/wiki/Q2440935","display_name":"Alpha globulin","level":3,"score":0.4791561961174011},{"id":"https://openalex.org/C2779390175","wikidata":"https://www.wikidata.org/wiki/Q855786","display_name":"Immunoelectrophoresis","level":3,"score":0.47322145104408264},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.43510180711746216},{"id":"https://openalex.org/C134018914","wikidata":"https://www.wikidata.org/wiki/Q162606","display_name":"Endocrinology","level":1,"score":0.3630960285663605},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.34326261281967163},{"id":"https://openalex.org/C185592680","wikidata":"https://www.wikidata.org/wiki/Q2329","display_name":"Chemistry","level":0,"score":0.26376789808273315},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.19917091727256775},{"id":"https://openalex.org/C89560881","wikidata":"https://www.wikidata.org/wiki/Q101026","display_name":"Platelet","level":2,"score":0.1333942711353302},{"id":"https://openalex.org/C2776364478","wikidata":"https://www.wikidata.org/wiki/Q467635","display_name":"Multiple myeloma","level":2,"score":0.12835711240768433},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.11072242259979248},{"id":"https://openalex.org/C55493867","wikidata":"https://www.wikidata.org/wiki/Q7094","display_name":"Biochemistry","level":1,"score":0.09323102235794067},{"id":"https://openalex.org/C501734568","wikidata":"https://www.wikidata.org/wiki/Q42918","display_name":"Mutation","level":3,"score":0.0},{"id":"https://openalex.org/C104317684","wikidata":"https://www.wikidata.org/wiki/Q7187","display_name":"Gene","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D000511","descriptor_name":"alpha-Macroglobulins","qualifier_ui":"Q000302","qualifier_name":"isolation & purification","is_major_topic":false},{"descriptor_ui":"D000511","descriptor_name":"alpha-Macroglobulins","qualifier_ui":"Q000302","qualifier_name":"isolation & purification","is_major_topic":false},{"descriptor_ui":"D000511","descriptor_name":"alpha-Macroglobulins","qualifier_ui":"Q000302","qualifier_name":"isolation & purification","is_major_topic":false},{"descriptor_ui":"D000511","descriptor_name":"alpha-Macroglobulins","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":false},{"descriptor_ui":"D000511","descriptor_name":"alpha-Macroglobulins","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":false},{"descriptor_ui":"D000511","descriptor_name":"alpha-Macroglobulins","qualifier_ui":"Q000378","qualifier_name":"metabolism","is_major_topic":false},{"descriptor_ui":"D001778","descriptor_name":"Blood Coagulation Disorders","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D001778","descriptor_name":"Blood Coagulation Disorders","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D001778","descriptor_name":"Blood Coagulation Disorders","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":false},{"descriptor_ui":"D001778","descriptor_name":"Blood Coagulation Disorders","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D001778","descriptor_name":"Blood Coagulation Disorders","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D001778","descriptor_name":"Blood Coagulation Disorders","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D001780","descriptor_name":"Blood Coagulation Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001780","descriptor_name":"Blood Coagulation Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001780","descriptor_name":"Blood Coagulation Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005342","descriptor_name":"Fibrinolysis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005342","descriptor_name":"Fibrinolysis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005342","descriptor_name":"Fibrinolysis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005799","descriptor_name":"Genes, Dominant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005799","descriptor_name":"Genes, Dominant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005799","descriptor_name":"Genes, Dominant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010314","descriptor_name":"Partial Thromboplastin Time","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010314","descriptor_name":"Partial Thromboplastin Time","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010314","descriptor_name":"Partial Thromboplastin Time","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010375","descriptor_name":"Pedigree","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010375","descriptor_name":"Pedigree","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010375","descriptor_name":"Pedigree","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010979","descriptor_name":"Platelet Function Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010979","descriptor_name":"Platelet Function Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010979","descriptor_name":"Platelet Function Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1620/tjem.154.365","doi":"https://doi.org/10.1620/tjem.154.365","is_oa":true,"landing_page_url":"https://doi.org/10.1620/tjem.154.365","pdf_url":"https://www.jstage.jst.go.jp/article/tjem1920/154/4/154_4_365/_pdf","source":{"id":"https://openalex.org/S189069745","display_name":"The Tohoku Journal of Experimental Medicine","issn_l":"0040-8727","issn":["0040-8727","1349-3329"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","jufo-1","ki-jl-1","medline","norway-1","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310313307","host_organization_name":"Tohoku University","host_organization_lineage":["https://openalex.org/P4310313307"],"host_organization_lineage_names":["Tohoku University"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Tohoku Journal of Experimental Medicine","raw_type":"journal-article"},{"id":"pmid:2460968","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/2460968","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Tohoku journal of experimental medicine","raw_type":"Case Reports"}],"best_oa_location":{"id":"doi:10.1620/tjem.154.365","doi":"https://doi.org/10.1620/tjem.154.365","is_oa":true,"landing_page_url":"https://doi.org/10.1620/tjem.154.365","pdf_url":"https://www.jstage.jst.go.jp/article/tjem1920/154/4/154_4_365/_pdf","source":{"id":"https://openalex.org/S189069745","display_name":"The Tohoku Journal of Experimental Medicine","issn_l":"0040-8727","issn":["0040-8727","1349-3329"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","jufo-1","ki-jl-1","medline","norway-1","poland-70","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310313307","host_organization_name":"Tohoku University","host_organization_lineage":["https://openalex.org/P4310313307"],"host_organization_lineage_names":["Tohoku University"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The Tohoku Journal of Experimental Medicine","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":0.9537000060081482,"display_name":"Good health and well-being"}],"sustainable_development_goals_aurora":[{"id":"https://metadata.un.org/sdg/3","score":0.5600000023841858,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W2002255702.pdf","grobid_xml":"https://content.openalex.org/works/W2002255702.grobid-xml"},"referenced_works_count":23,"referenced_works":["https://openalex.org/W1546828972","https://openalex.org/W1880892278","https://openalex.org/W1978879711","https://openalex.org/W1979849343","https://openalex.org/W1990986783","https://openalex.org/W2009158894","https://openalex.org/W2019524205","https://openalex.org/W2028627776","https://openalex.org/W2043396888","https://openalex.org/W2059197944","https://openalex.org/W2083983988","https://openalex.org/W2085445739","https://openalex.org/W2098868175","https://openalex.org/W2144446627","https://openalex.org/W2149275167","https://openalex.org/W2170358530","https://openalex.org/W2218444144","https://openalex.org/W2398890389","https://openalex.org/W4205676435","https://openalex.org/W4213120048","https://openalex.org/W4240719925","https://openalex.org/W4241369659","https://openalex.org/W4249192139"],"related_works":["https://openalex.org/W2257542139","https://openalex.org/W228982423","https://openalex.org/W2414025549","https://openalex.org/W2086447082","https://openalex.org/W2397406509","https://openalex.org/W2410535354","https://openalex.org/W2052671645","https://openalex.org/W2403648414","https://openalex.org/W2035435920","https://openalex.org/W2025775231"],"abstract_inverted_index":{"A":[0],"heritable":[1],"elevation":[2],"in":[3,10,64,198],"alpha":[4,61,126,138,150,200],"2-macroglobulin":[5],"(alpha":[6],"2M)":[7],"was":[8,98,117,132,144],"identified":[9],"a":[11,15,119,162,177],"9-year-old":[12],"girl":[13],"with":[14,161],"severe":[16],"bleeding":[17],"tendency":[18],"and":[19,77,88,128,176],"activated":[20],"partial":[21],"thromboplastin":[22],"time":[23,35],"(APTT)":[24],"prolonged":[25,36,130],"to":[26,37,48,56,100,157],"49.1":[27],"sec":[28,39],"(normal":[29],"27-38)":[30],"as":[31,33,141],"well":[32],"recalcification":[34],"438":[38],"(less":[40],"than":[41],"180).":[42],"The":[43,59,134,149],"addition":[44],"of":[45,136,169,181,188,202],"her":[46,65,71,107,124,129],"plasma":[47,50,60,160],"normal":[49,154,178],"made":[51],"APTT":[52,131],"prolong":[53],"from":[54],"26.8":[55],"38.3":[57],"sec.":[58],"2M":[62,127,151,159,201],"levels":[63,81],"relatives":[66,109],"were":[67,82],"checked,":[68],"i.e.,":[69],"proband,":[70],"sister,":[72],"mother,":[73],"maternal":[74],"grandmother,":[75],"father,":[76],"paternal":[78],"grandmother:":[79],"Their":[80],"406,":[83],"380,":[84],"352,":[85],"339,":[86],"166":[87],"236":[89],"mg/100":[90,146],"ml":[91,147],"(140-285),":[92],"respectively.":[93],"Thus":[94],"the":[95,137,167,170,199,203],"patient's":[96],"condition":[97],"thought":[99],"be":[101],"an":[102],"autosomal":[103],"dominant":[104],"disease,":[105],"though":[106],"other":[108],"displayed":[110],"no":[111,195],"apparent":[112],"clinical":[113],"symptoms.":[114],"Of":[115],"significance":[116],"that":[118],"possible":[120],"causal":[121],"association":[122],"between":[123],"elevated":[125],"indicated.":[133],"activity":[135],"2M,":[139],"determined":[140],"trypsin-protein":[142],"esterase,":[143],"351":[145],"(197%).":[148],"also":[152],"demonstrated":[153],"horizontal":[155,179],"mobility":[156,180],"anti-alpha":[158],"high":[163],"precipitin":[164],"arc":[165],"(showing":[166],"difference":[168],"protein":[171],"concentration)":[172],"by":[173,191],"crossed":[174],"immunoelectrophoresis,":[175],"immunofixation":[182],"electrophoresis.":[183],"In":[184],"addition,":[185],"after":[186],"analysis":[187],"testing":[189],"done":[190],"SDS-polyacrylamide-gel-electrophoresis,":[192],"we":[193],"found":[194],"qualitative":[196],"abnormality":[197],"patient.":[204]},"counts_by_year":[{"year":2012,"cited_by_count":1}],"updated_date":"2026-10-13T10:08:12.033832","created_date":"2025-10-10T00:00:00"}
