{"id":"https://openalex.org/W2000774716","doi":"https://doi.org/10.1016/s0002-9270(00)02163-8","title":"Progressive Familial Intrahepatic Cholestasis: Partial Biliary Diversion Normalizes Serum Lipids and Improves Growth in Noncirrhotic Patients","display_name":"Progressive Familial Intrahepatic Cholestasis: Partial Biliary Diversion Normalizes Serum Lipids and Improves Growth in Noncirrhotic Patients","publication_year":2000,"publication_date":"2000-12-01","ids":{"openalex":"https://openalex.org/W2000774716","doi":"https://doi.org/10.1016/s0002-9270(00)02163-8","mag":"2000774716","pmid":"https://pubmed.ncbi.nlm.nih.gov/11151888"},"language":"en","primary_location":{"id":"doi:10.1016/s0002-9270(00)02163-8","doi":"https://doi.org/10.1016/s0002-9270(00)02163-8","is_oa":false,"landing_page_url":"https://doi.org/10.1016/s0002-9270(00)02163-8","pdf_url":null,"source":{"id":"https://openalex.org/S66441642","display_name":"The American Journal of Gastroenterology","issn_l":"0002-9270","issn":["0002-9270","1572-0241"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The American Journal of Gastroenterology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5038274554","display_name":"Michael Melter","orcid":"https://orcid.org/0000-0002-4194-0758","observed_orcids":["https://orcid.org/0000-0002-4194-0758"]},"institutions":[{"id":"https://openalex.org/I34809795","display_name":"Medizinische Hochschule Hannover","ror":"https://ror.org/00f2yqf98","country_code":"DE","type":"education","lineage":["https://openalex.org/I34809795"]}],"countries":["DE"],"is_corresponding":true,"raw_author_name":"Michael Melter","raw_affiliation_strings":["Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Germany","institution_ids":["https://openalex.org/I34809795"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5065953619","display_name":"Burkhard Rodeck","orcid":"https://orcid.org/0000-0003-3422-5104","observed_orcids":["https://orcid.org/0000-0003-3422-5104"]},"institutions":[{"id":"https://openalex.org/I34809795","display_name":"Medizinische Hochschule Hannover","ror":"https://ror.org/00f2yqf98","country_code":"DE","type":"education","lineage":["https://openalex.org/I34809795"]}],"countries":["DE"],"is_corresponding":false,"raw_author_name":"Burkhard Rodeck","raw_affiliation_strings":["Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany","institution_ids":["https://openalex.org/I34809795"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5109685209","display_name":"R\u00fcdiger Kardorff","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I34809795","display_name":"Medizinische Hochschule Hannover","ror":"https://ror.org/00f2yqf98","country_code":"DE","type":"education","lineage":["https://openalex.org/I34809795"]}],"countries":["DE"],"is_corresponding":false,"raw_author_name":"R\u00fcdiger Kardorff","raw_affiliation_strings":["Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany","institution_ids":["https://openalex.org/I34809795"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5006521153","display_name":"Peter F. Hoyer","orcid":"https://orcid.org/0000-0002-9132-0282","observed_orcids":["https://orcid.org/0000-0002-9132-0282"]},"institutions":[{"id":"https://openalex.org/I34809795","display_name":"Medizinische Hochschule Hannover","ror":"https://ror.org/00f2yqf98","country_code":"DE","type":"education","lineage":["https://openalex.org/I34809795"]}],"countries":["DE"],"is_corresponding":false,"raw_author_name":"Peter F Hoyer","raw_affiliation_strings":["Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany","institution_ids":["https://openalex.org/I34809795"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5022595895","display_name":"Claus Petersen","orcid":"https://orcid.org/0000-0002-1789-7163","observed_orcids":["https://orcid.org/0000-0002-1789-7163"]},"institutions":[{"id":"https://openalex.org/I34809795","display_name":"Medizinische Hochschule Hannover","ror":"https://ror.org/00f2yqf98","country_code":"DE","type":"education","lineage":["https://openalex.org/I34809795"]}],"countries":["DE"],"is_corresponding":false,"raw_author_name":"Claus Petersen","raw_affiliation_strings":["Department of Pediatric Surgery, Children's Hospital, Hannover Medical School, Hannover, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Surgery, Children's Hospital, Hannover Medical School, Hannover, Germany","institution_ids":["https://openalex.org/I34809795"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5008779270","display_name":"Antje Ballauff","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210119759","display_name":"Essen University Hospital","ror":"https://ror.org/02na8dn90","country_code":"DE","type":"funder","lineage":["https://openalex.org/I4210119759"]}],"countries":["DE"],"is_corresponding":false,"raw_author_name":"Antje Ballauff","raw_affiliation_strings":["Children's Hospital, University of Essen, Essen, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Children's Hospital, University of Essen, Essen, Germany","institution_ids":["https://openalex.org/I4210119759"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5108517612","display_name":"Johannes Brodehl","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I34809795","display_name":"Medizinische Hochschule Hannover","ror":"https://ror.org/00f2yqf98","country_code":"DE","type":"education","lineage":["https://openalex.org/I34809795"]}],"countries":["DE"],"is_corresponding":false,"raw_author_name":"Johannes Brodehl","raw_affiliation_strings":["Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pediatric Nephrology and Metabolic Disorders, Children's Hospital, Hannover Medical School, Hannover, Germany","institution_ids":["https://openalex.org/I34809795"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":["https://openalex.org/A5038274554"],"corresponding_institution_ids":["https://openalex.org/I34809795"],"apc_list":{"value":4390,"currency":"USD","value_usd":4390},"apc_paid":null,"fwci":4.6735,"has_fulltext":false,"cited_by_count":95,"citation_normalized_percentile":{"value":0.9465728,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":89,"max":99},"biblio":{"volume":"95","issue":"12","first_page":"3522","last_page":"3528"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12460","display_name":"Pediatric Hepatobiliary Diseases and Treatments","score":0.9887999892234802,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12460","display_name":"Pediatric Hepatobiliary Diseases and Treatments","score":0.9887999892234802,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10570","display_name":"Drug Transport and Resistance Mechanisms","score":0.004999999888241291,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11834","display_name":"Liver Diseases and Immunity","score":0.0008999999845400453,"subfield":{"id":"https://openalex.org/subfields/2721","display_name":"Hepatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/progressive-familial-intrahepatic-cholestasis","display_name":"progressive familial intrahepatic cholestasis","score":1.0},{"id":"https://openalex.org/keywords/cholestasis","display_name":"cholestasis","score":0.5709999799728394},{"id":"https://openalex.org/keywords/pruritus","display_name":"pruritus","score":0.8460000157356262},{"id":"https://openalex.org/keywords/serum-bile-acids","display_name":"serum bile acids","score":0.7260000109672546},{"id":"https://openalex.org/keywords/serum-lipids","display_name":"serum lipids","score":0.7919999957084656},{"id":"https://openalex.org/keywords/high-density-lipoprotein","display_name":"high-density lipoprotein","score":0.8169999718666077},{"id":"https://openalex.org/keywords/apolipoprotein-a-i","display_name":"apolipoprotein A-I","score":0.9769999980926514},{"id":"https://openalex.org/keywords/growth-failure","display_name":"growth failure","score":0.6179999709129333},{"id":"https://openalex.org/keywords/catch-up-growth","display_name":"catch-up growth","score":0.968999981880188},{"id":"https://openalex.org/keywords/cholinesterase-activity","display_name":"cholinesterase activity","score":0.7310000061988831},{"id":"https://openalex.org/keywords/non-cirrhotic-patients","display_name":"non-cirrhotic patients","score":0.7609999775886536},{"id":"https://openalex.org/keywords/pediatric-patients","display_name":"pediatric patients","score":0.5339999794960022}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8774770498275757},{"id":"https://openalex.org/C2778593092","wikidata":"https://www.wikidata.org/wiki/Q1075923","display_name":"Cholestasis","level":2,"score":0.7981402277946472},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.7650476694107056},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.6854695081710815},{"id":"https://openalex.org/C512861765","wikidata":"https://www.wikidata.org/wiki/Q1359801","display_name":"Liver function tests","level":2,"score":0.5944749116897583},{"id":"https://openalex.org/C2780890998","wikidata":"https://www.wikidata.org/wiki/Q6993476","display_name":"Neonatal cholestasis","level":5,"score":0.5192701816558838},{"id":"https://openalex.org/C2992208098","wikidata":"https://www.wikidata.org/wiki/Q1359801","display_name":"Liver function","level":2,"score":0.5169681906700134},{"id":"https://openalex.org/C134018914","wikidata":"https://www.wikidata.org/wiki/Q162606","display_name":"Endocrinology","level":1,"score":0.4432346820831299},{"id":"https://openalex.org/C2778456037","wikidata":"https://www.wikidata.org/wiki/Q133244","display_name":"Jaundice","level":2,"score":0.43512922525405884},{"id":"https://openalex.org/C2777513400","wikidata":"https://www.wikidata.org/wiki/Q104219","display_name":"Bilirubin","level":2,"score":0.4274529814720154},{"id":"https://openalex.org/C2779243279","wikidata":"https://www.wikidata.org/wiki/Q659033","display_name":"Biliary atresia","level":4,"score":0.20126581192016602},{"id":"https://openalex.org/C2779609443","wikidata":"https://www.wikidata.org/wiki/Q1368191","display_name":"Liver transplantation","level":3,"score":0.14796829223632812},{"id":"https://openalex.org/C2911091166","wikidata":"https://www.wikidata.org/wiki/Q106419912","display_name":"Transplantation","level":2,"score":0.05692574381828308}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001662","descriptor_name":"Biliary Tract Surgical Procedures","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002780","descriptor_name":"Cholestasis, Intrahepatic","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":true},{"descriptor_ui":"D002780","descriptor_name":"Cholestasis, Intrahepatic","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":true},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005500","descriptor_name":"Follow-Up Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005704","descriptor_name":"Gallbladder","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":false},{"descriptor_ui":"D006128","descriptor_name":"Growth","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D006130","descriptor_name":"Growth Disorders","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007583","descriptor_name":"Jejunum","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":false},{"descriptor_ui":"D008055","descriptor_name":"Lipids","qualifier_ui":"Q000097","qualifier_name":"blood","is_major_topic":true},{"descriptor_ui":"D008103","descriptor_name":"Liver Cirrhosis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008111","descriptor_name":"Liver Function Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013997","descriptor_name":"Time Factors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1016/s0002-9270(00)02163-8","doi":"https://doi.org/10.1016/s0002-9270(00)02163-8","is_oa":false,"landing_page_url":"https://doi.org/10.1016/s0002-9270(00)02163-8","pdf_url":null,"source":{"id":"https://openalex.org/S66441642","display_name":"The American Journal of Gastroenterology","issn_l":"0002-9270","issn":["0002-9270","1572-0241"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The American Journal of Gastroenterology","raw_type":"journal-article"},{"id":"doi:10.1111/j.1572-0241.2000.03370.x","doi":"https://doi.org/10.1111/j.1572-0241.2000.03370.x","is_oa":false,"landing_page_url":"https://doi.org/10.1111/j.1572-0241.2000.03370.x","pdf_url":null,"source":{"id":"https://openalex.org/S66441642","display_name":"The American Journal of Gastroenterology","issn_l":"0002-9270","issn":["0002-9270","1572-0241"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-2","ki-jl-2","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310315671","host_organization_name":"Lippincott Williams & Wilkins","host_organization_lineage":["https://openalex.org/P4310315671","https://openalex.org/P4310318547"],"host_organization_lineage_names":["Lippincott Williams & Wilkins","Wolters Kluwer"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"American Journal of Gastroenterology","raw_type":"journal-article"},{"id":"pmid:11151888","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/11151888","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The American journal of gastroenterology","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3","score":1.0}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":55,"referenced_works":["https://openalex.org/W66417364","https://openalex.org/W1553854484","https://openalex.org/W1571954921","https://openalex.org/W1612407641","https://openalex.org/W1751757376","https://openalex.org/W1904363208","https://openalex.org/W1974599572","https://openalex.org/W1976450060","https://openalex.org/W1993595151","https://openalex.org/W2000859228","https://openalex.org/W2004833297","https://openalex.org/W2006590877","https://openalex.org/W2007085863","https://openalex.org/W2007136995","https://openalex.org/W2009261731","https://openalex.org/W2011090208","https://openalex.org/W2011849415","https://openalex.org/W2012678885","https://openalex.org/W2013306641","https://openalex.org/W2015293456","https://openalex.org/W2020451356","https://openalex.org/W2024039041","https://openalex.org/W2030988632","https://openalex.org/W2036204884","https://openalex.org/W2040312759","https://openalex.org/W2055630306","https://openalex.org/W2058379737","https://openalex.org/W2058675862","https://openalex.org/W2065565173","https://openalex.org/W2065999061","https://openalex.org/W2070337491","https://openalex.org/W2074238421","https://openalex.org/W2074769363","https://openalex.org/W2075423334","https://openalex.org/W2085302633","https://openalex.org/W2089597861","https://openalex.org/W2093737352","https://openalex.org/W2095409521","https://openalex.org/W2115161881","https://openalex.org/W2121739950","https://openalex.org/W2128427613","https://openalex.org/W2133359496","https://openalex.org/W2134120897","https://openalex.org/W2135222142","https://openalex.org/W2157291177","https://openalex.org/W2162075432","https://openalex.org/W2185291318","https://openalex.org/W2189572630","https://openalex.org/W2208148114","https://openalex.org/W2305634217","https://openalex.org/W2328987984","https://openalex.org/W2338530640","https://openalex.org/W2605536858","https://openalex.org/W4294443831","https://openalex.org/W4300072036"],"related_works":["https://openalex.org/W2050538572","https://openalex.org/W1973759180","https://openalex.org/W2225405165","https://openalex.org/W2157291177","https://openalex.org/W3012685160","https://openalex.org/W4312509500","https://openalex.org/W1968698689","https://openalex.org/W2550619956","https://openalex.org/W7223124157","https://openalex.org/W1997436888"],"abstract_inverted_index":{"OBJECTIVES:":[0],"Progressive":[1],"familial":[2],"intrahepatic":[3],"cholestasis":[4],"(PFIC)":[5],"usually":[6],"presents":[7],"with":[8,54,84,235,265],"pruritus,":[9,174],"jaundice,":[10],"hepatomegaly,":[11],"and":[12,33,39,73,91,131,141,149,175,188,232,249],"growth":[13,206,268],"failure.":[14],"A":[15],"group":[16],"of":[17,24,64,173,178,226,245],"PFIC":[18,230],"is":[19],"recognized":[20],"by":[21],"marked":[22,204],"elevation":[23],"total":[25],"serum":[26,30,195],"bile":[27,117],"acids,":[28],"decreased":[29,124],"apolipoprotein":[31,132],"A-1,":[32],"high-density":[34,125],"lipoprotein,":[35],"but":[36,138,162],"normal":[37,139],"gamma-glutamyltranspeptidase":[38,140],"cholesterol.":[40,142],"Although":[41],"medical":[42,95],"therapy":[43],"generally":[44],"fails,":[45],"partial":[46],"external":[47],"biliary":[48],"diversion":[49],"(DIV)":[50],"has":[51,61],"been":[52,62],"used":[53],"promising":[55],"results":[56],"for":[57,107],"cholestasis.":[58],"However,":[59],"little":[60],"reported":[63],"its":[65],"effect":[66],"on":[67,80],"linear":[68],"growth,":[69],"synthetic":[70,156,246],"liver":[71,157,180,247],"function,":[72],"lipid":[74,196,250],"metabolism.":[75,251],"METHODS:":[76],"DIV":[77,227,260],"was":[78,98,211],"performed":[79],"six":[81],"noncirrhotic":[82,229],"children":[83,161],"PFIC,":[85],"all":[86,110,160,168,179,217],"suffering":[87],"from":[88],"severe":[89],"pruritus":[90],"cholestasis,":[92],"refractory":[93],"to":[94],"treatment.":[96],"Stature":[97],"below":[99],"-1":[100],"(median,":[101,207],"-2.3)":[102],"standard":[103],"deviation":[104],"score":[105],"(SDS)":[106],"height":[108],"in":[109,159,216,228,269],"cases.":[111,218],"All":[112,238],"patients":[113,169,231,239],"had":[114],"markedly":[115,123],"enhanced":[116],"acids":[118],"(307":[119],"+/-":[120,128,135,208],"72":[121],"microl/L),":[122],"lipoprotein":[126],"(20":[127],"7":[129],"mg/dl),":[130,137],"A-1":[133],"(58":[134],"37":[136],"In":[143,201],"addition,":[144,202],"cholinesterase":[145,184],"activity,":[146,185],"monoethylglycinexylidide":[147,186],"test,":[148,187],"Fischer's":[150,189],"ratio":[151],"indicated":[152],"a":[153,203],"significantly":[154],"reduced":[155],"function":[158,181,248],"the":[163,194,253],"youngest.":[164],"RESULTS:":[165],"After":[166],"DIV,":[167],"were":[170],"consistently":[171],"relieved":[172],"experienced":[176,240],"normalization":[177,244],"tests,":[182],"including":[183,243],"ratio,":[190],"as":[191,193],"well":[192],"profile":[197],"within":[198],"1":[199,214],"yr.":[200],"catch-up":[205],"1.3":[209],"SDS)":[210],"evident":[212],"after":[213],"yr":[215],"CONCLUSIONS:":[219],"This":[220],"report":[221],"shows":[222],"an":[223,266],"excellent":[224],"result":[225],"compares":[233],"favorably":[234],"other":[236],"reports.":[237],"complete":[241],"remission,":[242],"For":[252],"first":[254],"time":[255],"we":[256],"have":[257],"shown":[258],"that":[259],"can":[261],"also":[262],"be":[263],"associated":[264],"accelerated":[267],"these":[270],"patients.":[271]},"counts_by_year":[{"year":2023,"cited_by_count":3},{"year":2022,"cited_by_count":2},{"year":2021,"cited_by_count":3},{"year":2020,"cited_by_count":5},{"year":2018,"cited_by_count":4},{"year":2017,"cited_by_count":1},{"year":2016,"cited_by_count":6},{"year":2015,"cited_by_count":2},{"year":2014,"cited_by_count":5},{"year":2013,"cited_by_count":1},{"year":2012,"cited_by_count":5}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
