{"id":"https://openalex.org/W1998291301","doi":"https://doi.org/10.7326/0003-4819-75-3-369","title":"Survival with Systemic Sclerosis (Scleroderma): A Life-Table Analysis of Clinical and Demographic Factors in 309 Patients","display_name":"Survival with Systemic Sclerosis (Scleroderma): A Life-Table Analysis of Clinical and Demographic Factors in 309 Patients","publication_year":1971,"publication_date":"1971-09-01","ids":{"openalex":"https://openalex.org/W1998291301","doi":"https://doi.org/10.7326/0003-4819-75-3-369","mag":"1998291301","pmid":"https://pubmed.ncbi.nlm.nih.gov/4105464"},"language":"en","primary_location":{"id":"doi:10.7326/0003-4819-75-3-369","doi":"https://doi.org/10.7326/0003-4819-75-3-369","is_oa":false,"landing_page_url":"https://doi.org/10.7326/0003-4819-75-3-369","pdf_url":null,"source":{"id":"https://openalex.org/S119722071","display_name":"Annals of Internal Medicine","issn_l":"0003-4819","issn":["0003-4819","1539-3704"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310316812","host_organization_name":"American College of Physicians","host_organization_lineage":["https://openalex.org/P4310316812"],"host_organization_lineage_names":["American College of Physicians"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annals of Internal Medicine","raw_type":"journal-article"},"parent_works":[],"lineage":["https://openalex.org/W1998291301"],"child_works_count":0,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5112247165","display_name":"Thomas A. Medsger","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"THOMAS A. MEDSGER","raw_affiliation_strings":["Memphis, Tennessee; and Pittsburgh, Pennsylvania"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Memphis, Tennessee; and Pittsburgh, Pennsylvania","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5031226177","display_name":"Alfonse T. Masi","orcid":"https://orcid.org/0000-0002-9695-6634","observed_orcids":["https://orcid.org/0000-0002-9695-6634"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"ALFONSE T. MASI","raw_affiliation_strings":["Memphis, Tennessee; and Pittsburgh, Pennsylvania","Epidemiology and Biostatistics"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Memphis, Tennessee; and Pittsburgh, Pennsylvania","institution_ids":[]},{"raw_affiliation_string":"Epidemiology and Biostatistics","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5017461374","display_name":"Gerald P. Rodnan","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"GERALD P. RODNAN","raw_affiliation_strings":["Memphis, Tennessee; and Pittsburgh, Pennsylvania"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Memphis, Tennessee; and Pittsburgh, Pennsylvania","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5067490363","display_name":"Thomas G. Benedek","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"THOMAS G. BENEDEK","raw_affiliation_strings":["Memphis, Tennessee; and Pittsburgh, Pennsylvania"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Memphis, Tennessee; and Pittsburgh, Pennsylvania","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5021610694","display_name":"Harry Robinson","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"HARRY ROBINSON","raw_affiliation_strings":["Memphis, Tennessee; and Pittsburgh, Pennsylvania"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Memphis, Tennessee; and Pittsburgh, Pennsylvania","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":4.8045,"has_fulltext":false,"cited_by_count":327,"citation_normalized_percentile":{"value":0.93784206,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":87,"max":99},"biblio":{"volume":"75","issue":"3","first_page":"369","last_page":"376"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11330","display_name":"Systemic Sclerosis and Related Diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11330","display_name":"Systemic Sclerosis and Related Diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10728","display_name":"Pulmonary Hypertension Research and Treatments","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11310","display_name":"Connective tissue disorders research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/systemic-sclerosis","display_name":"systemic sclerosis","score":0.9990000128746033},{"id":"https://openalex.org/keywords/survival","display_name":"survival","score":0.9620000123977661},{"id":"https://openalex.org/keywords/mortality","display_name":"mortality","score":0.8230000138282776},{"id":"https://openalex.org/keywords/life-table-analysis","display_name":"life table analysis","score":0.8050000071525574},{"id":"https://openalex.org/keywords/racial-differences","display_name":"racial differences","score":0.492000013589859},{"id":"https://openalex.org/keywords/sex-differences","display_name":"sex differences","score":0.8130000233650208},{"id":"https://openalex.org/keywords/internal-organ-involvement","display_name":"internal organ involvement","score":0.7929999828338623},{"id":"https://openalex.org/keywords/renal-involvement","display_name":"renal involvement","score":0.953000009059906},{"id":"https://openalex.org/keywords/cardiac-involvement","display_name":"cardiac involvement","score":0.9890000224113464},{"id":"https://openalex.org/keywords/pulmonary-involvement","display_name":"pulmonary involvement","score":0.9480000138282776},{"id":"https://openalex.org/keywords/prognosis","display_name":"prognosis","score":0.8270000219345093}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9595640897750854},{"id":"https://openalex.org/C172400760","wikidata":"https://www.wikidata.org/wiki/Q332796","display_name":"Survivorship curve","level":3,"score":0.730004608631134},{"id":"https://openalex.org/C2779967694","wikidata":"https://www.wikidata.org/wiki/Q1383511","display_name":"Scleroderma (fungus)","level":3,"score":0.6560155153274536},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.5338726043701172},{"id":"https://openalex.org/C10515644","wikidata":"https://www.wikidata.org/wiki/Q543310","display_name":"Survival analysis","level":2,"score":0.4692623019218445},{"id":"https://openalex.org/C2776283816","wikidata":"https://www.wikidata.org/wiki/Q332823","display_name":"Survival rate","level":2,"score":0.4573982357978821},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.33745402097702026},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.09550413489341736},{"id":"https://openalex.org/C180032290","wikidata":"https://www.wikidata.org/wiki/Q1664296","display_name":"Inoculation","level":2,"score":0.0},{"id":"https://openalex.org/C121608353","wikidata":"https://www.wikidata.org/wiki/Q12078","display_name":"Cancer","level":2,"score":0.0}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000367","descriptor_name":"Age Factors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000974","descriptor_name":"Antibodies, Antinuclear","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D001741","descriptor_name":"Black or African American","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001799","descriptor_name":"Blood Sedimentation","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005500","descriptor_name":"Follow-Up Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005719","descriptor_name":"gamma-Globulins","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D005767","descriptor_name":"Gastrointestinal Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007674","descriptor_name":"Kidney Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D007841","descriptor_name":"Latex Fixation Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008171","descriptor_name":"Lung Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010414","descriptor_name":"Pennsylvania","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D011928","descriptor_name":"Raynaud Disease","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D012595","descriptor_name":"Scleroderma, Systemic","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D012595","descriptor_name":"Scleroderma, Systemic","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D012595","descriptor_name":"Scleroderma, Systemic","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":true},{"descriptor_ui":"D012737","descriptor_name":"Sex Factors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012871","descriptor_name":"Skin Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D013714","descriptor_name":"Tennessee","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013997","descriptor_name":"Time Factors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.7326/0003-4819-75-3-369","doi":"https://doi.org/10.7326/0003-4819-75-3-369","is_oa":false,"landing_page_url":"https://doi.org/10.7326/0003-4819-75-3-369","pdf_url":null,"source":{"id":"https://openalex.org/S119722071","display_name":"Annals of Internal Medicine","issn_l":"0003-4819","issn":["0003-4819","1539-3704"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310316812","host_organization_name":"American College of Physicians","host_organization_lineage":["https://openalex.org/P4310316812"],"host_organization_lineage_names":["American College of Physicians"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annals of Internal Medicine","raw_type":"journal-article"},{"id":"pmid:4105464","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/4105464","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annals of internal medicine","raw_type":"Journal Article"},{"id":"mag:3028534635","doi":null,"is_oa":false,"landing_page_url":"https://www.acpjournals.org/doi/abs/10.7326/0003-4819-75-3-369","pdf_url":null,"source":{"id":"https://openalex.org/S119722071","display_name":"Annals of Internal Medicine","issn_l":"0003-4819","issn":["0003-4819","1539-3704"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-a","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-200","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310316812","host_organization_name":"American College of Physicians","host_organization_lineage":["https://openalex.org/P4310316812"],"host_organization_lineage_names":["American College of Physicians"],"type":"journal"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"Annals of Internal Medicine","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":17,"referenced_works":["https://openalex.org/W87105600","https://openalex.org/W1915469550","https://openalex.org/W1984249199","https://openalex.org/W1986714479","https://openalex.org/W1987319762","https://openalex.org/W2036610337","https://openalex.org/W2049770223","https://openalex.org/W2054604454","https://openalex.org/W2060885164","https://openalex.org/W2065830768","https://openalex.org/W2066293475","https://openalex.org/W2089992644","https://openalex.org/W2139984188","https://openalex.org/W2405985974","https://openalex.org/W2412475789","https://openalex.org/W2419369966","https://openalex.org/W7116915201"],"related_works":["https://openalex.org/W4238719656","https://openalex.org/W2023190197","https://openalex.org/W4298280462","https://openalex.org/W2132986338","https://openalex.org/W2114857739","https://openalex.org/W258082647","https://openalex.org/W3165785428","https://openalex.org/W2109242477","https://openalex.org/W1896799110"],"abstract_inverted_index":{"A":[0,49],"life-table":[1],"analysis":[2,43],"of":[3,27,38,44,57,86,97,119,121],"survivorship":[4,75],"with":[5,99,155],"scleroderma":[6],"was":[7,53,64,81,91,129,138],"done,":[8],"using":[9],"223":[10],"patients":[11,18,85],"diagnosed":[12],"in":[13,19,55,62,83],"Pittsburgh,":[14],"Pennsylvania,":[15],"and":[16,24,42,148],"86":[17],"Memphis,":[20],"Tennessee.":[21],"The":[22],"demographic":[23],"clinical":[25],"characteristics":[26],"the":[28,39,45,67,71,94,116,135],"two":[29,40,68],"series":[30,88],"were":[31,151],"similar,":[32],"thus":[33],"allowing":[34],"for":[35,93],"both":[36,87],"comparison":[37],"groups":[41],"total":[46],"309":[47],"patients.":[48,59,123],"follow-up":[50,120,144],"during":[51,115],"1970":[52],"successful":[54],"94%":[56],"all":[58,122],"No":[60],"difference":[61],"survival":[63,80,105,112],"found":[65,82],"between":[66],"patient":[69],"groups,":[70],"combined":[72],"7-year":[73,143],"cumulative":[74],"being":[76],"35%.":[77],"Significantly":[78],"decreased":[79,156],"older":[84],"after":[89],"allowance":[90],"made":[92],"natural":[95],"increase":[96],"mortality":[98],"age.":[100],"Males":[101],"had":[102,109],"significantly":[103,110,139],"worse":[104,111,140],"than":[106,113],"females.":[107],"Negroes":[108],"whites":[114],"first":[117],"year":[118],"When":[124],"no":[125],"internal":[126],"organ":[127],"involvement":[128,150],"detected":[130],"at":[131],"entry":[132],"to":[133],"study,":[134],"negro":[136],"prognosis":[137],"throughout":[141],"a":[142],"period.":[145],"Renal,":[146],"cardiac,":[147],"pulmonary":[149],"each":[152],"independently":[153],"correlated":[154],"survival.":[157]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":1},{"year":2022,"cited_by_count":1},{"year":2021,"cited_by_count":1},{"year":2020,"cited_by_count":4},{"year":2019,"cited_by_count":4},{"year":2018,"cited_by_count":4},{"year":2017,"cited_by_count":2},{"year":2016,"cited_by_count":8},{"year":2015,"cited_by_count":4},{"year":2014,"cited_by_count":6},{"year":2013,"cited_by_count":6},{"year":2012,"cited_by_count":6}],"updated_date":"2026-11-14T11:04:58.165337","created_date":"2016-06-24T00:00:00"}
