{"id":"https://openalex.org/W1997232609","doi":"https://doi.org/10.1046/j.1365-2133.1997.5771549.x","title":"Treatment of refractory epidermolysis bullosa acquisita with extracorporeal photochemotherapy","display_name":"Treatment of refractory epidermolysis bullosa acquisita with extracorporeal photochemotherapy","publication_year":1997,"publication_date":"1997-03-01","ids":{"openalex":"https://openalex.org/W1997232609","doi":"https://doi.org/10.1046/j.1365-2133.1997.5771549.x","mag":"1997232609","pmid":"https://pubmed.ncbi.nlm.nih.gov/9115929"},"language":"en","primary_location":{"id":"doi:10.1046/j.1365-2133.1997.5771549.x","doi":"https://doi.org/10.1046/j.1365-2133.1997.5771549.x","is_oa":false,"landing_page_url":"https://doi.org/10.1046/j.1365-2133.1997.5771549.x","pdf_url":null,"source":{"id":"https://openalex.org/S45720283","display_name":"British Journal of Dermatology","issn_l":"0007-0963","issn":["0007-0963","1365-2133"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"British Journal of Dermatology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5080574863","display_name":"Konstantin B. Gordon","orcid":"https://orcid.org/0000-0002-3146-5615","observed_orcids":["https://orcid.org/0000-0002-3146-5615"]},"institutions":[{"id":"https://openalex.org/I111979921","display_name":"Northwestern University","ror":"https://ror.org/000e0be47","country_code":"US","type":"education","lineage":["https://openalex.org/I111979921"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"K.B. GORDON","raw_affiliation_strings":["Department of Dermatology, Northwestern University Medical School, 303 East Chicago Avenue, Chicago, II, 60611, U.S.A","Department of Dermatology, Northwestern University Medical School, Chicago, IL 60611, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, Northwestern University Medical School, 303 East Chicago Avenue, Chicago, II, 60611, U.S.A","institution_ids":["https://openalex.org/I111979921"]},{"raw_affiliation_string":"Department of Dermatology, Northwestern University Medical School, Chicago, IL 60611, USA","institution_ids":["https://openalex.org/I111979921"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5030763743","display_name":"Lawrence S. Chan","orcid":"https://orcid.org/0009-0007-0640-980X","observed_orcids":["https://orcid.org/0009-0007-0640-980X"]},"institutions":[{"id":"https://openalex.org/I111979921","display_name":"Northwestern University","ror":"https://ror.org/000e0be47","country_code":"US","type":"education","lineage":["https://openalex.org/I111979921"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"L.S. CHAN","raw_affiliation_strings":["Department of Dermatology, Northwestern University Medical School, 303 East Chicago Avenue, Chicago, II, 60611, U.S.A"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, Northwestern University Medical School, 303 East Chicago Avenue, Chicago, II, 60611, U.S.A","institution_ids":["https://openalex.org/I111979921"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5007855326","display_name":"David T. Woodley","orcid":"https://orcid.org/0000-0001-6103-7120","observed_orcids":["https://orcid.org/0000-0001-6103-7120"]},"institutions":[{"id":"https://openalex.org/I111979921","display_name":"Northwestern University","ror":"https://ror.org/000e0be47","country_code":"US","type":"education","lineage":["https://openalex.org/I111979921"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"D.T. WOODLEY","raw_affiliation_strings":["Department of Dermatology, Northwestern University Medical School, 303 East Chicago Avenue, Chicago, II, 60611, U.S.A"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Dermatology, Northwestern University Medical School, 303 East Chicago Avenue, Chicago, II, 60611, U.S.A","institution_ids":["https://openalex.org/I111979921"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5007855326"],"corresponding_institution_ids":["https://openalex.org/I111979921"],"apc_list":{"value":3731,"currency":"GBP","value_usd":4920},"apc_paid":null,"fwci":2.4279,"has_fulltext":false,"cited_by_count":69,"citation_normalized_percentile":{"value":0.88403309,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":97},"biblio":{"volume":"136","issue":"3","first_page":"415","last_page":"420"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11730","display_name":"Autoimmune Bullous Skin Diseases","score":0.9262999892234802,"subfield":{"id":"https://openalex.org/subfields/2734","display_name":"Pathology and Forensic Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11730","display_name":"Autoimmune Bullous Skin Diseases","score":0.9262999892234802,"subfield":{"id":"https://openalex.org/subfields/2734","display_name":"Pathology and Forensic Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11650","display_name":"Skin and Cellular Biology Research","score":0.06289999932050705,"subfield":{"id":"https://openalex.org/subfields/1307","display_name":"Cell Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T10308","display_name":"Systemic Lupus Erythematosus Research","score":0.000699999975040555,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/epidermolysis-bullosa-acquisita","display_name":"epidermolysis bullosa acquisita","score":0.9950000047683716},{"id":"https://openalex.org/keywords/extracorporeal-photopheresis","display_name":"extracorporeal photopheresis","score":0.9269999861717224},{"id":"https://openalex.org/keywords/refractory-disease","display_name":"refractory disease","score":0.9380000233650208},{"id":"https://openalex.org/keywords/autoimmune-disease","display_name":"autoimmune disease","score":0.7549999952316284},{"id":"https://openalex.org/keywords/immunomodulation","display_name":"immunomodulation","score":0.9919999837875366},{"id":"https://openalex.org/keywords/skin-fragility","display_name":"skin fragility","score":0.953000009059906},{"id":"https://openalex.org/keywords/disease-severity","display_name":"disease severity","score":0.6859999895095825}],"concepts":[{"id":"https://openalex.org/C2779305546","wikidata":"https://www.wikidata.org/wiki/Q3726860","display_name":"Epidermolysis bullosa acquisita","level":4,"score":0.970257580280304},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.905800998210907},{"id":"https://openalex.org/C142424586","wikidata":"https://www.wikidata.org/wiki/Q7307572","display_name":"Refractory (planetary science)","level":2,"score":0.8507301807403564},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.5954300761222839},{"id":"https://openalex.org/C2781207856","wikidata":"https://www.wikidata.org/wiki/Q923020","display_name":"Epidermolysis bullosa","level":2,"score":0.5504121780395508},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.43981102108955383},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.32274773716926575},{"id":"https://openalex.org/C2779252107","wikidata":"https://www.wikidata.org/wiki/Q1004647","display_name":"Bullous pemphigoid","level":3,"score":0.166640967130661},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.1426478624343872},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.09621399641036987},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.0},{"id":"https://openalex.org/C121332964","wikidata":"https://www.wikidata.org/wiki/Q413","display_name":"Physics","level":0,"score":0.0},{"id":"https://openalex.org/C87355193","wikidata":"https://www.wikidata.org/wiki/Q411","display_name":"Astrobiology","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001323","descriptor_name":"Autoantibodies","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D001327","descriptor_name":"Autoimmune Diseases","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D001327","descriptor_name":"Autoimmune Diseases","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D001327","descriptor_name":"Autoimmune Diseases","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true},{"descriptor_ui":"D001485","descriptor_name":"Basement Membrane","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D011446","descriptor_name":"Prospective Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012867","descriptor_name":"Skin","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D012867","descriptor_name":"Skin","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D016107","descriptor_name":"Epidermolysis Bullosa Acquisita","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D016107","descriptor_name":"Epidermolysis Bullosa Acquisita","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D016107","descriptor_name":"Epidermolysis Bullosa Acquisita","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true},{"descriptor_ui":"D017893","descriptor_name":"Photopheresis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":true},{"descriptor_ui":"D019084","descriptor_name":"Fluorescent Antibody Technique, Indirect","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1046/j.1365-2133.1997.5771549.x","doi":"https://doi.org/10.1046/j.1365-2133.1997.5771549.x","is_oa":false,"landing_page_url":"https://doi.org/10.1046/j.1365-2133.1997.5771549.x","pdf_url":null,"source":{"id":"https://openalex.org/S45720283","display_name":"British Journal of Dermatology","issn_l":"0007-0963","issn":["0007-0963","1365-2133"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"British Journal of Dermatology","raw_type":"journal-article"},{"id":"doi:10.1111/j.1365-2133.1997.tb14957.x","doi":"https://doi.org/10.1111/j.1365-2133.1997.tb14957.x","is_oa":false,"landing_page_url":"https://doi.org/10.1111/j.1365-2133.1997.tb14957.x","pdf_url":null,"source":{"id":"https://openalex.org/S45720283","display_name":"British Journal of Dermatology","issn_l":"0007-0963","issn":["0007-0963","1365-2133"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-b","doyens","jufo-3","ki-jl-3","medline","norway-2","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310311648","host_organization_name":"Oxford University Press","host_organization_lineage":["https://openalex.org/P4310311648","https://openalex.org/P4310311647"],"host_organization_lineage_names":["Oxford University Press","University of Oxford"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"British Journal of Dermatology","raw_type":"journal-article"},{"id":"pmid:9115929","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/9115929","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"The British journal of dermatology","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3","score":0.9940000176429749}],"study_designs":[],"awards":[{"id":"https://openalex.org/G1583782658","display_name":null,"funder_award_id":"IT32AB07593-01","funder_id":"https://openalex.org/F4320332505","funder_display_name":"U.S. Public Health Service"},{"id":"https://openalex.org/G2381941243","display_name":null,"funder_award_id":"RR00048","funder_id":"https://openalex.org/F4320337375","funder_display_name":"National Center for Research Resources"},{"id":"https://openalex.org/G5024593974","display_name":null,"funder_award_id":"R01AR33635-09","funder_id":"https://openalex.org/F4320337362","funder_display_name":"National Institute of Arthritis and Musculoskeletal and Skin Diseases"}],"funders":[{"id":"https://openalex.org/F4320306866","display_name":"American Academy of Dermatology","ror":"https://ror.org/00bbqy387"},{"id":"https://openalex.org/F4320309475","display_name":"Northwestern University","ror":"https://ror.org/000e0be47"},{"id":"https://openalex.org/F4320314508","display_name":"Chicago Dermatological Society","ror":"https://ror.org/02ft72j58"},{"id":"https://openalex.org/F4320332161","display_name":"National Institutes of Health","ror":"https://ror.org/01cwqze88"},{"id":"https://openalex.org/F4320332505","display_name":"U.S. Public Health Service","ror":"https://ror.org/05xf94514"},{"id":"https://openalex.org/F4320337362","display_name":"National Institute of Arthritis and Musculoskeletal and Skin Diseases","ror":"https://ror.org/006zn3t30"},{"id":"https://openalex.org/F4320337375","display_name":"National Center for Research Resources","ror":"https://ror.org/04pw6fb54"}],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":26,"referenced_works":["https://openalex.org/W52469116","https://openalex.org/W1512513473","https://openalex.org/W1966688563","https://openalex.org/W1994646633","https://openalex.org/W2008947034","https://openalex.org/W2010594881","https://openalex.org/W2011096466","https://openalex.org/W2018648554","https://openalex.org/W2024462818","https://openalex.org/W2029117355","https://openalex.org/W2044603809","https://openalex.org/W2044914944","https://openalex.org/W2049176688","https://openalex.org/W2050767039","https://openalex.org/W2055946340","https://openalex.org/W2055975319","https://openalex.org/W2069834122","https://openalex.org/W2074365868","https://openalex.org/W2086077250","https://openalex.org/W2088303434","https://openalex.org/W2337557724","https://openalex.org/W4232795384","https://openalex.org/W4240166237","https://openalex.org/W4245136776","https://openalex.org/W4246968662","https://openalex.org/W4256583545"],"related_works":["https://openalex.org/W2018648554","https://openalex.org/W2246932776","https://openalex.org/W2088312051","https://openalex.org/W2412818583","https://openalex.org/W2004474855","https://openalex.org/W2038730262","https://openalex.org/W2894867502","https://openalex.org/W2990295233","https://openalex.org/W2049176688","https://openalex.org/W4415985452"],"abstract_inverted_index":{"Treatment":[0],"of":[1,26,31,55,61,76,85,95,106],"epidermolysis":[2],"bullosa":[3],"acquisita":[4],"(EBA)":[5],"with":[6,39,45,108],"conventional":[7,114],"therapy":[8],"frequently":[9],"does":[10],"not":[11],"result":[12],"in":[13,28,52,68,103],"improvement.":[14],"Extracorporeal":[15],"photochemotherapy":[16],"(ECP)":[17],"is":[18],"a":[19],"novel":[20],"immunomodulating":[21],"technique":[22],"which":[23],"might":[24],"be":[25,100],"benefit":[27],"the":[29,62,73,80,86,96,104],"treatment":[30,105],"autoimmune":[32],"disease.":[33,78],"We":[34],"prospectively":[35],"studied":[36],"three":[37,48,63],"patients":[38,49,107],"refractory":[40,112],"EBA":[41,109],"who":[42,110],"were":[43],"treated":[44],"ECP.":[46],"All":[47],"had":[50,64],"improvement":[51,67],"objective":[53,81],"measurement":[54],"their":[56,69,77],"disease":[57,87],"severity":[58],"while":[59],"two":[60],"significant":[65],"subjective":[66,83],"skin":[70],"fragility":[71],"and":[72,82],"clinical":[74],"activity":[75],"Both":[79],"manifestations":[84],"continued":[88],"to":[89,113],"improve":[90],"6":[91],"months":[92],"after":[93],"completion":[94],"protocol.":[97],"ECP":[98],"may":[99],"therapeutic":[101],"option":[102],"are":[111],"therapy.":[115]},"counts_by_year":[{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":2},{"year":2023,"cited_by_count":1},{"year":2022,"cited_by_count":1},{"year":2020,"cited_by_count":2},{"year":2019,"cited_by_count":2},{"year":2017,"cited_by_count":1},{"year":2016,"cited_by_count":2},{"year":2015,"cited_by_count":2},{"year":2014,"cited_by_count":1},{"year":2013,"cited_by_count":3},{"year":2012,"cited_by_count":1}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
