{"id":"https://openalex.org/W1997011093","doi":"https://doi.org/10.3810/hp.2010.02.287","title":"Treatment of Pulmonary Exacerbations in Adult Cystic Fibrosis Patients: A Review","display_name":"Treatment of Pulmonary Exacerbations in Adult Cystic Fibrosis Patients: A Review","publication_year":2010,"publication_date":"2010-02-01","ids":{"openalex":"https://openalex.org/W1997011093","doi":"https://doi.org/10.3810/hp.2010.02.287","mag":"1997011093","pmid":"https://pubmed.ncbi.nlm.nih.gov/20469621"},"language":"en","primary_location":{"id":"doi:10.3810/hp.2010.02.287","doi":"https://doi.org/10.3810/hp.2010.02.287","is_oa":false,"landing_page_url":"https://doi.org/10.3810/hp.2010.02.287","pdf_url":null,"source":{"id":"https://openalex.org/S4210173941","display_name":"Hospital Practice","issn_l":"0018-5809","issn":["0018-5809","2154-8331","2377-1003"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","ki-jl-1","medline","norway-1","poland-40","russia-white-list-2"],"host_organization":"https://openalex.org/P4310320547","host_organization_name":"Taylor & Francis","host_organization_lineage":["https://openalex.org/P4310320547","https://openalex.org/P4310320449"],"host_organization_lineage_names":["Taylor & Francis","Informa"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hospital Practice","raw_type":"journal-article"},"volume":null,"type":"review","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5055297742","display_name":"Tara Lynn Barto","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I153297377","display_name":"Medical University of South Carolina","ror":"https://ror.org/012jban78","country_code":"US","type":"education","lineage":["https://openalex.org/I153297377"]}],"countries":["US"],"is_corresponding":true,"raw_author_name":"Tara Lynn Barto","raw_affiliation_strings":["Division of Pulmonary, Critical Care, Allergy and Sleep Medicine, Medical University of South Carolina, Charleston, SC 29425, USA. barto@musc.edu","Medical University of South Carolina, Charleston, SC"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary, Critical Care, Allergy and Sleep Medicine, Medical University of South Carolina, Charleston, SC 29425, USA. barto@musc.edu","institution_ids":["https://openalex.org/I153297377"]},{"raw_affiliation_string":"Medical University of South Carolina, Charleston, SC","institution_ids":["https://openalex.org/I153297377"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5005915390","display_name":"Patrick A. Flume","orcid":"https://orcid.org/0000-0002-1560-6879","observed_orcids":["https://orcid.org/0000-0002-1560-6879"]},"institutions":[{"id":"https://openalex.org/I153297377","display_name":"Medical University of South Carolina","ror":"https://ror.org/012jban78","country_code":"US","type":"education","lineage":["https://openalex.org/I153297377"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Patrick A. Flume","raw_affiliation_strings":["Medical University of South Carolina, Charleston, SC"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Medical University of South Carolina, Charleston, SC","institution_ids":["https://openalex.org/I153297377"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":["https://openalex.org/A5055297742"],"corresponding_institution_ids":["https://openalex.org/I153297377"],"apc_list":null,"apc_paid":null,"fwci":0.2627,"has_fulltext":false,"cited_by_count":10,"citation_normalized_percentile":{"value":0.22651934,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":96},"biblio":{"volume":"38","issue":"1","first_page":"26","last_page":"34"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10665","display_name":"Cystic Fibrosis Research Advances","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10143","display_name":"Chronic Obstructive Pulmonary Disease (COPD) Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11651","display_name":"Inhalation and Respiratory Drug Delivery","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/cystic-fibrosis","display_name":"cystic fibrosis","score":1.0},{"id":"https://openalex.org/keywords/pulmonary-exacerbations","display_name":"pulmonary exacerbations","score":0.9980000257492065},{"id":"https://openalex.org/keywords/multidisciplinary-care","display_name":"multidisciplinary care","score":0.9179999828338623},{"id":"https://openalex.org/keywords/lung-function-decline","display_name":"lung function decline","score":0.8029999732971191},{"id":"https://openalex.org/keywords/cf-related-diabetes","display_name":"CF-related diabetes","score":0.9259999990463257},{"id":"https://openalex.org/keywords/pneumothorax","display_name":"pneumothorax","score":0.9980000257492065},{"id":"https://openalex.org/keywords/comorbidity","display_name":"comorbidities","score":0.6800000071525574},{"id":"https://openalex.org/keywords/treatment-goals","display_name":"treatment goals","score":0.6470000147819519}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9674890041351318},{"id":"https://openalex.org/C2776938444","wikidata":"https://www.wikidata.org/wiki/Q178194","display_name":"Cystic fibrosis","level":2,"score":0.813178539276123},{"id":"https://openalex.org/C75603125","wikidata":"https://www.wikidata.org/wiki/Q1877462","display_name":"Pulmonary function testing","level":2,"score":0.7424548864364624},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.6606473922729492},{"id":"https://openalex.org/C2778329176","wikidata":"https://www.wikidata.org/wiki/Q203601","display_name":"Pneumothorax","level":2,"score":0.6173587441444397},{"id":"https://openalex.org/C2779951463","wikidata":"https://www.wikidata.org/wiki/Q7268788","display_name":"Quality of life (healthcare)","level":2,"score":0.508854866027832},{"id":"https://openalex.org/C3020501284","wikidata":"https://www.wikidata.org/wiki/Q849359","display_name":"Multidisciplinary team","level":2,"score":0.4491878151893616},{"id":"https://openalex.org/C2992779976","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Pulmonary disease","level":2,"score":0.4435373544692993},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.433879554271698},{"id":"https://openalex.org/C2776042228","wikidata":"https://www.wikidata.org/wiki/Q35869","display_name":"Asthma","level":2,"score":0.4149463176727295},{"id":"https://openalex.org/C2781244666","wikidata":"https://www.wikidata.org/wiki/Q32446","display_name":"Pulmonary fibrosis","level":3,"score":0.4132990837097168},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.2415831983089447},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.15545156598091125},{"id":"https://openalex.org/C159110408","wikidata":"https://www.wikidata.org/wiki/Q121176","display_name":"Nursing","level":1,"score":0.10847395658493042}],"mesh":[{"descriptor_ui":"D000208","descriptor_name":"Acute Disease","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000893","descriptor_name":"Anti-Inflammatory Agents","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D000894","descriptor_name":"Anti-Inflammatory Agents, Non-Steroidal","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D000900","descriptor_name":"Anti-Bacterial Agents","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D001229","descriptor_name":"Aspergillosis, Allergic Bronchopulmonary","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D002423","descriptor_name":"Cause of Death","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003550","descriptor_name":"Cystic Fibrosis","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D004334","descriptor_name":"Drug Administration Schedule","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006469","descriptor_name":"Hemoptysis","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010348","descriptor_name":"Patient Care Team","qualifier_ui":"Q000458","qualifier_name":"organization & administration","is_major_topic":false},{"descriptor_ui":"D011030","descriptor_name":"Pneumothorax","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D012042","descriptor_name":"Registries","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012131","descriptor_name":"Respiratory Insufficiency","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D012131","descriptor_name":"Respiratory Insufficiency","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D012131","descriptor_name":"Respiratory Insufficiency","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true},{"descriptor_ui":"D012138","descriptor_name":"Respiratory Therapy","qualifier_ui":"Q000379","qualifier_name":"methods","is_major_topic":false},{"descriptor_ui":"D017410","descriptor_name":"Practice Guidelines as Topic","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018529","descriptor_name":"Nutritional Support","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.3810/hp.2010.02.287","doi":"https://doi.org/10.3810/hp.2010.02.287","is_oa":false,"landing_page_url":"https://doi.org/10.3810/hp.2010.02.287","pdf_url":null,"source":{"id":"https://openalex.org/S4210173941","display_name":"Hospital Practice","issn_l":"0018-5809","issn":["0018-5809","2154-8331","2377-1003"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","ki-jl-1","medline","norway-1","poland-40","russia-white-list-2"],"host_organization":"https://openalex.org/P4310320547","host_organization_name":"Taylor & Francis","host_organization_lineage":["https://openalex.org/P4310320547","https://openalex.org/P4310320449"],"host_organization_lineage_names":["Taylor & Francis","Informa"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hospital Practice","raw_type":"journal-article"},{"id":"pmid:20469621","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/20469621","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Hospital practice (1995)","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":44,"referenced_works":["https://openalex.org/W1904652721","https://openalex.org/W1970963921","https://openalex.org/W1972309249","https://openalex.org/W1975482215","https://openalex.org/W1979830769","https://openalex.org/W1980017808","https://openalex.org/W1982624023","https://openalex.org/W1990698756","https://openalex.org/W1993207965","https://openalex.org/W1993616165","https://openalex.org/W1998496055","https://openalex.org/W1999435300","https://openalex.org/W2004189684","https://openalex.org/W2006773867","https://openalex.org/W2035971419","https://openalex.org/W2038436322","https://openalex.org/W2042013403","https://openalex.org/W2045074682","https://openalex.org/W2050820701","https://openalex.org/W2054940816","https://openalex.org/W2056538792","https://openalex.org/W2068186502","https://openalex.org/W2094703380","https://openalex.org/W2103884572","https://openalex.org/W2105545551","https://openalex.org/W2113210963","https://openalex.org/W2115511578","https://openalex.org/W2117106765","https://openalex.org/W2121040369","https://openalex.org/W2124135806","https://openalex.org/W2125603952","https://openalex.org/W2127339866","https://openalex.org/W2132740946","https://openalex.org/W2133979383","https://openalex.org/W2142648608","https://openalex.org/W2146292644","https://openalex.org/W2146484505","https://openalex.org/W2148707202","https://openalex.org/W2166840599","https://openalex.org/W2333398204","https://openalex.org/W2913270762","https://openalex.org/W4206066785","https://openalex.org/W4210996550","https://openalex.org/W4211194064"],"related_works":["https://openalex.org/W2013055554","https://openalex.org/W2146292644","https://openalex.org/W7096932792","https://openalex.org/W2043295178","https://openalex.org/W2041489292","https://openalex.org/W2803422886","https://openalex.org/W2859669650","https://openalex.org/W2142648608","https://openalex.org/W4395697480","https://openalex.org/W4230061281"],"abstract_inverted_index":{"Cystic":[0,76],"fibrosis":[1],"(CF)":[2],"is":[3,12],"a":[4,36,55,60,65],"complex":[5],"multisystemic":[6],"disease":[7],"requiring":[8],"specialized":[9],"care.":[10],"It":[11],"characterized":[13],"by":[14,95],"progressive":[15],"pulmonary":[16,26,39,42,52,86,121],"decline,":[17],"with":[18,46,113],"intermittent":[19],"worsening":[20],"of":[21,30,38,64,85,103,120,134],"lung":[22,49],"function,":[23],"often":[24],"called":[25],"exacerbations.":[27,87],"Eighty-five":[28],"percent":[29],"all":[31],"deaths":[32],"from":[33],"CF":[34,114,124],"are":[35,44],"result":[37],"disease,":[40],"and":[41,58,72,101,109,132],"exacerbations":[43,53,115,122],"associated":[45,112],"decline":[47],"in":[48,123],"function.":[50],"Treating":[51],"requires":[54],"multifaceted":[56],"approach":[57],"includes":[59],"multidisciplinary":[61],"team":[62],"composed":[63],"physician,":[66],"nurse,":[67],"respiratory":[68],"therapist,":[69,71],"physical":[70],"nutritionist.":[73],"Recently,":[74],"the":[75,82,91,99],"Fibrosis":[77],"Foundation":[78],"published":[79],"guidelines":[80],"addressing":[81],"comprehensive":[83],"treatment":[84,92,102,119],"This":[88],"article":[89],"outlines":[90],"goals":[93],"established":[94],"these":[96],"guidelines,":[97],"including":[98],"evaluation":[100],"comorbid":[104],"conditions":[105],"(eg,":[106,116],"CF-related":[107],"diabetes)":[108],"serious":[110],"complications":[111],"pneumothorax).":[117],"Proper":[118],"patients":[125],"will":[126],"continue":[127],"to":[128],"improve":[129],"their":[130],"health":[131],"quality":[133],"life.":[135]},"counts_by_year":[{"year":2020,"cited_by_count":2},{"year":2016,"cited_by_count":1},{"year":2014,"cited_by_count":2},{"year":2012,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
