{"id":"https://openalex.org/W1994759834","doi":"https://doi.org/10.1001/archneurol.2008.517","title":"Alzheimer Abnormalities of the Amygdala With Kl\u00fcver-Bucy Syndrome Symptoms","display_name":"Alzheimer Abnormalities of the Amygdala With Kl\u00fcver-Bucy Syndrome Symptoms","publication_year":2009,"publication_date":"2009-01-01","ids":{"openalex":"https://openalex.org/W1994759834","doi":"https://doi.org/10.1001/archneurol.2008.517","mag":"1994759834","pmid":"https://pubmed.ncbi.nlm.nih.gov/19139311","pmcid":"https://www.ncbi.nlm.nih.gov/pmc/articles/2868923"},"language":"en","primary_location":{"id":"doi:10.1001/archneurol.2008.517","doi":"https://doi.org/10.1001/archneurol.2008.517","is_oa":true,"landing_page_url":"https://doi.org/10.1001/archneurol.2008.517","pdf_url":"https://jamanetwork.com/journals/jamaneurology/articlepdf/796361/nob80009_125_129.pdf","source":{"id":"https://openalex.org/S4210230857","display_name":"Archives of Neurology","issn_l":"0003-9942","issn":["0003-9942","1538-3687"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core"],"host_organization":"https://openalex.org/P4310320259","host_organization_name":"American Medical Association","host_organization_lineage":["https://openalex.org/P4310320259"],"host_organization_lineage_names":["American Medical Association"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of Neurology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://jamanetwork.com/journals/jamaneurology/articlepdf/796361/nob80009_125_129.pdf","any_repository_has_fulltext":true},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5025728942","display_name":"Shawn J. Kile","orcid":"https://orcid.org/0000-0001-7906-4186","observed_orcids":["https://orcid.org/0000-0001-7906-4186"]},"institutions":[{"id":"https://openalex.org/I84218800","display_name":"University of California, Davis","ror":"https://ror.org/05rrcem69","country_code":"US","type":"education","lineage":["https://openalex.org/I84218800"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Shawn J. Kile","raw_affiliation_strings":["Department of Neurology, University of California at Davis, 4860 Y St, Ste 3700, Sacramento, CA 95817, USA"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, University of California at Davis, 4860 Y St, Ste 3700, Sacramento, CA 95817, USA","institution_ids":["https://openalex.org/I84218800"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5110686168","display_name":"William G. Ellis","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I84218800","display_name":"University of California, Davis","ror":"https://ror.org/05rrcem69","country_code":"US","type":"education","lineage":["https://openalex.org/I84218800"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"William G. Ellis","raw_affiliation_strings":["Department of Neurology , University of California at Davis , Sacramento","University of California at Davis"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology , University of California at Davis , Sacramento","institution_ids":["https://openalex.org/I84218800"]},{"raw_affiliation_string":"University of California at Davis","institution_ids":["https://openalex.org/I84218800"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5007748241","display_name":"John Olichney","orcid":"https://orcid.org/0009-0008-6640-7563","observed_orcids":["https://orcid.org/0009-0008-6640-7563"]},"institutions":[{"id":"https://openalex.org/I84218800","display_name":"University of California, Davis","ror":"https://ror.org/05rrcem69","country_code":"US","type":"education","lineage":["https://openalex.org/I84218800"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"John M. Olichney","raw_affiliation_strings":["Department of Neurology, University of California at Davis, Sacramento"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, University of California at Davis, Sacramento","institution_ids":["https://openalex.org/I84218800"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112904024","display_name":"Sarah Tomaszewski Farias","orcid":"https://orcid.org/0009-0009-8969-3387","observed_orcids":["https://orcid.org/0009-0009-8969-3387"]},"institutions":[{"id":"https://openalex.org/I84218800","display_name":"University of California, Davis","ror":"https://ror.org/05rrcem69","country_code":"US","type":"education","lineage":["https://openalex.org/I84218800"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Sarah Farias","raw_affiliation_strings":["Department of Neurology, University of California at Davis, Sacramento"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, University of California at Davis, Sacramento","institution_ids":["https://openalex.org/I84218800"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5071825455","display_name":"Charles S DeCarli","orcid":"https://orcid.org/0000-0003-1914-2693","observed_orcids":["https://orcid.org/0000-0003-1914-2693"]},"institutions":[{"id":"https://openalex.org/I84218800","display_name":"University of California, Davis","ror":"https://ror.org/05rrcem69","country_code":"US","type":"education","lineage":["https://openalex.org/I84218800"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Charles DeCarli","raw_affiliation_strings":["Department of Neurology, University of California at Davis, Sacramento"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology, University of California at Davis, Sacramento","institution_ids":["https://openalex.org/I84218800"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I84218800"],"apc_list":null,"apc_paid":null,"fwci":1.9643,"has_fulltext":true,"cited_by_count":32,"citation_normalized_percentile":{"value":0.84505387,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":89,"max":98},"biblio":{"volume":"66","issue":"1","first_page":"125","last_page":"9"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10009","display_name":"Dementia and Cognitive Impairment Research","score":0.9688000082969666,"subfield":{"id":"https://openalex.org/subfields/2738","display_name":"Psychiatry and Mental health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10009","display_name":"Dementia and Cognitive Impairment Research","score":0.9688000082969666,"subfield":{"id":"https://openalex.org/subfields/2738","display_name":"Psychiatry and Mental health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10086","display_name":"Alzheimer's disease research and treatments","score":0.02930000051856041,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology (medical)"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10855","display_name":"Amyotrophic Lateral Sclerosis Research","score":9.999999747378752e-05,"subfield":{"id":"https://openalex.org/subfields/2728","display_name":"Clinical Neurology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/alzheimer-s-disease","display_name":"Alzheimer's disease","score":0.9610000252723694},{"id":"https://openalex.org/keywords/kluver-bucy-syndrome","display_name":"Kl\u00fcver-Bucy syndrome","score":0.9729999899864197},{"id":"https://openalex.org/keywords/amygdala","display_name":"amygdala","score":0.9290000200271606},{"id":"https://openalex.org/keywords/neurofibrillary-tangles","display_name":"neurofibrillary tangles","score":0.9490000009536743},{"id":"https://openalex.org/keywords/amyloid-plaques","display_name":"amyloid plaques","score":0.9940000176429749},{"id":"https://openalex.org/keywords/hyperorality","display_name":"hyperorality","score":0.7429999709129333},{"id":"https://openalex.org/keywords/hypersexuality","display_name":"hypersexuality","score":0.9660000205039978},{"id":"https://openalex.org/keywords/hypermetamorphosis","display_name":"hypermetamorphosis","score":0.9459999799728394},{"id":"https://openalex.org/keywords/visual-agnosia","display_name":"visual agnosia","score":0.7990000247955322},{"id":"https://openalex.org/keywords/hyperphagia","display_name":"hyperphagia","score":0.9760000109672546},{"id":"https://openalex.org/keywords/apathy","display_name":"apathy","score":0.9229999780654907},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.5709999799728394},{"id":"https://openalex.org/keywords/neuropathology","display_name":"neuropathology","score":0.5920000076293945}],"concepts":[{"id":"https://openalex.org/C2780130745","wikidata":"https://www.wikidata.org/wiki/Q1650750","display_name":"Neuropathology","level":3,"score":0.6780551075935364},{"id":"https://openalex.org/C2779144063","wikidata":"https://www.wikidata.org/wiki/Q338924","display_name":"Amygdala","level":2,"score":0.6400518417358398},{"id":"https://openalex.org/C15744967","wikidata":"https://www.wikidata.org/wiki/Q9418","display_name":"Psychology","level":0,"score":0.6155831217765808},{"id":"https://openalex.org/C2779483572","wikidata":"https://www.wikidata.org/wiki/Q83030","display_name":"Dementia","level":3,"score":0.5378664135932922},{"id":"https://openalex.org/C2779088608","wikidata":"https://www.wikidata.org/wiki/Q267907","display_name":"Hypersexuality","level":3,"score":0.49386149644851685},{"id":"https://openalex.org/C502032728","wikidata":"https://www.wikidata.org/wiki/Q11081","display_name":"Alzheimer's disease","level":3,"score":0.48425814509391785},{"id":"https://openalex.org/C2776509080","wikidata":"https://www.wikidata.org/wiki/Q309406","display_name":"Apathy","level":3,"score":0.4523058235645294},{"id":"https://openalex.org/C2778641062","wikidata":"https://www.wikidata.org/wiki/Q18592","display_name":"Frontotemporal dementia","level":4,"score":0.4197181165218353},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.3899877369403839},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.3636508584022522},{"id":"https://openalex.org/C169760540","wikidata":"https://www.wikidata.org/wiki/Q207011","display_name":"Neuroscience","level":1,"score":0.36079055070877075},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.34305816888809204}],"mesh":[{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000544","descriptor_name":"Alzheimer Disease","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D000544","descriptor_name":"Alzheimer Disease","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D000544","descriptor_name":"Alzheimer Disease","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D000679","descriptor_name":"Amygdala","qualifier_ui":"Q000000981","qualifier_name":"diagnostic imaging","is_major_topic":false},{"descriptor_ui":"D000679","descriptor_name":"Amygdala","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D000679","descriptor_name":"Amygdala","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D001344","descriptor_name":"Autopsy","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003704","descriptor_name":"Dementia","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D003937","descriptor_name":"Diagnosis, Differential","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003951","descriptor_name":"Diagnostic Errors","qualifier_ui":"Q000517","qualifier_name":"prevention & control","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008279","descriptor_name":"Magnetic Resonance Imaging","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009483","descriptor_name":"Neuropsychological Tests","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012189","descriptor_name":"Retrospective Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016874","descriptor_name":"Neurofibrillary Tangles","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D017809","descriptor_name":"Fatal Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D018450","descriptor_name":"Disease Progression","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D020232","descriptor_name":"Kluver-Bucy Syndrome","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D020232","descriptor_name":"Kluver-Bucy Syndrome","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":true},{"descriptor_ui":"D020232","descriptor_name":"Kluver-Bucy Syndrome","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D049268","descriptor_name":"Positron-Emission Tomography","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D058225","descriptor_name":"Plaque, Amyloid","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1001/archneurol.2008.517","doi":"https://doi.org/10.1001/archneurol.2008.517","is_oa":true,"landing_page_url":"https://doi.org/10.1001/archneurol.2008.517","pdf_url":"https://jamanetwork.com/journals/jamaneurology/articlepdf/796361/nob80009_125_129.pdf","source":{"id":"https://openalex.org/S4210230857","display_name":"Archives of Neurology","issn_l":"0003-9942","issn":["0003-9942","1538-3687"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core"],"host_organization":"https://openalex.org/P4310320259","host_organization_name":"American Medical Association","host_organization_lineage":["https://openalex.org/P4310320259"],"host_organization_lineage_names":["American Medical Association"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of Neurology","raw_type":"journal-article"},{"id":"pmid:19139311","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/19139311","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of neurology","raw_type":"Case Reports"},{"id":"pmh:oai:pubmedcentral.nih.gov:2868923","doi":null,"is_oa":true,"landing_page_url":"https://www.ncbi.nlm.nih.gov/pmc/articles/2868923","pdf_url":null,"source":{"id":"https://openalex.org/S2764455111","display_name":"PubMed Central","issn_l":null,"issn":null,"is_oa":true,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"acceptedVersion","is_accepted":true,"is_published":false,"raw_source_name":"Arch Neurol","raw_type":"Text"}],"best_oa_location":{"id":"doi:10.1001/archneurol.2008.517","doi":"https://doi.org/10.1001/archneurol.2008.517","is_oa":true,"landing_page_url":"https://doi.org/10.1001/archneurol.2008.517","pdf_url":"https://jamanetwork.com/journals/jamaneurology/articlepdf/796361/nob80009_125_129.pdf","source":{"id":"https://openalex.org/S4210230857","display_name":"Archives of Neurology","issn_l":"0003-9942","issn":["0003-9942","1538-3687"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core"],"host_organization":"https://openalex.org/P4310320259","host_organization_name":"American Medical Association","host_organization_lineage":["https://openalex.org/P4310320259"],"host_organization_lineage_names":["American Medical Association"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of Neurology","raw_type":"journal-article"},"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.9763000011444092}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[{"id":"https://openalex.org/G1345365365","display_name":"UC Davis Alzheimer's Disease Core Center","funder_award_id":"P30AG010129","funder_id":"https://openalex.org/F4320337337","funder_display_name":"National Institute on Aging"}],"funders":[{"id":"https://openalex.org/F4320337337","display_name":"National Institute on Aging","ror":"https://ror.org/049v75w11"}],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W1994759834.pdf","grobid_xml":"https://content.openalex.org/works/W1994759834.grobid-xml"},"referenced_works_count":25,"referenced_works":["https://openalex.org/W1481839256","https://openalex.org/W1970283678","https://openalex.org/W1972444597","https://openalex.org/W1974583546","https://openalex.org/W1982734781","https://openalex.org/W1986452225","https://openalex.org/W1989451265","https://openalex.org/W2008543026","https://openalex.org/W2026553142","https://openalex.org/W2070909285","https://openalex.org/W2072361983","https://openalex.org/W2086051541","https://openalex.org/W2101891449","https://openalex.org/W2124244312","https://openalex.org/W2128330176","https://openalex.org/W2133796724","https://openalex.org/W2135479773","https://openalex.org/W2136619901","https://openalex.org/W2138878035","https://openalex.org/W2140590073","https://openalex.org/W2169771257","https://openalex.org/W4232609309","https://openalex.org/W4242067988","https://openalex.org/W4249928895","https://openalex.org/W7074185999"],"related_works":["https://openalex.org/W4388295675","https://openalex.org/W6982783774","https://openalex.org/W2135479773","https://openalex.org/W2064665931","https://openalex.org/W4210704048","https://openalex.org/W2075835057","https://openalex.org/W2136381305","https://openalex.org/W4248365675","https://openalex.org/W3213420928","https://openalex.org/W3111276950"],"abstract_inverted_index":{"BACKGROUND:":[0],"Neurofibrillary":[1],"tangles":[2,103],"and":[3,42,72,92,104,123,134],"beta-amyloid":[4],"plaques":[5,105],"have":[6],"been":[7],"observed":[8],"in":[9,12,21,106,140],"the":[10,22,45,48,107],"amygdala":[11,23,121],"Alzheimer":[13,40,99,117],"disease.":[14],"A":[15,58],"disproportionate":[16],"abundance":[17],"of":[18,39,65,79,116],"this":[19],"abnormality":[20],"may":[24,138],"cause":[25],"behavioral":[26,37,63],"symptoms":[27,64],"similar":[28],"to":[29,43],"Kl\u00fcver-Bucy":[30,125],"syndrome.":[31],"OBJECTIVES:":[32],"To":[33],"describe":[34],"an":[35],"atypical":[36],"presentation":[38],"disease":[41,100,118],"review":[44],"literature":[46],"on":[47,81],"subject.":[49],"DESIGN:":[50],"Case":[51],"study.":[52],"SETTING:":[53],"Outpatient":[54],"specialty":[55],"clinic.":[56],"PATIENT:":[57],"70-year-old":[59],"man":[60],"with":[61,101,119],"progressive":[62],"hyperorality,":[66],"hypersexuality,":[67],"hypermetamorphosis,":[68],"visual":[69],"agnosia,":[70],"hyperphagia,":[71],"apathy":[73],"who":[74],"died":[75],"at":[76],"age":[77],"77":[78],"asphyxiation":[80],"a":[82,114,124],"foreign":[83],"object.":[84],"MAIN":[85],"OUTCOME":[86],"MEASURES:":[87],"Clinical":[88,133],"symptomatology,":[89],"brain":[90],"imaging,":[91],"neuropathology.":[93],"RESULTS:":[94],"The":[95],"pathologic":[96],"diagnosis":[97,142],"was":[98,128],"abundant":[102],"lateral":[108],"amygdala.":[109],"CONCLUSIONS:":[110],"This":[111],"case":[112],"represents":[113],"variant":[115],"prominent":[120],"abnormalities":[122],"phenotype":[126],"that":[127,137],"misdiagnosed":[129],"as":[130],"frontotemporal":[131],"dementia.":[132],"imaging":[135],"findings":[136],"aid":[139],"accurate":[141],"are":[143],"reviewed.":[144]},"counts_by_year":[{"year":2026,"cited_by_count":2},{"year":2023,"cited_by_count":3},{"year":2021,"cited_by_count":3},{"year":2020,"cited_by_count":2},{"year":2019,"cited_by_count":1},{"year":2018,"cited_by_count":4},{"year":2016,"cited_by_count":4},{"year":2015,"cited_by_count":1},{"year":2014,"cited_by_count":2},{"year":2012,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
