{"id":"https://openalex.org/W1993528202","doi":"https://doi.org/10.1177/089198879400700402","title":"Clinical Characteristics of Chronic Creutzfeldt-Jakob Disease","display_name":"Clinical Characteristics of Chronic Creutzfeldt-Jakob Disease","publication_year":1994,"publication_date":"1994-10-01","ids":{"openalex":"https://openalex.org/W1993528202","doi":"https://doi.org/10.1177/089198879400700402","mag":"1993528202","pmid":"https://pubmed.ncbi.nlm.nih.gov/7826487"},"language":"en","primary_location":{"id":"doi:10.1177/089198879400700402","doi":"https://doi.org/10.1177/089198879400700402","is_oa":false,"landing_page_url":"https://doi.org/10.1177/089198879400700402","pdf_url":null,"source":{"id":"https://openalex.org/S182765863","display_name":"Journal of Geriatric Psychiatry and Neurology","issn_l":"0891-9887","issn":["0891-9887","1552-5708"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320017","host_organization_name":"SAGE Publishing","host_organization_lineage":["https://openalex.org/P4310320017"],"host_organization_lineage_names":["SAGE Publishing"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Geriatric Psychiatry and Neurology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5080419931","display_name":"Mario F. Mendez","orcid":"https://orcid.org/0000-0001-6441-7989","observed_orcids":["https://orcid.org/0000-0001-6441-7989"]},"institutions":[{"id":"https://openalex.org/I130238516","display_name":"University of Minnesota","ror":"https://ror.org/017zqws13","country_code":"US","type":"education","lineage":["https://openalex.org/I130238516"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Mario F. Mendez","raw_affiliation_strings":["Department of Neurology (Drs. Mendez and Frey, Ms. Selwood), and from The Alzheimer's Treatment and Research Center (Dr. Frey), St. Paul-Ramsey Medical Center, and The University of Minnesota, St. Paul, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology (Drs. Mendez and Frey, Ms. Selwood), and from The Alzheimer's Treatment and Research Center (Dr. Frey), St. Paul-Ramsey Medical Center, and The University of Minnesota, St. Paul, Minnesota","institution_ids":["https://openalex.org/I130238516"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5019028808","display_name":"Allison Selwood","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I130238516","display_name":"University of Minnesota","ror":"https://ror.org/017zqws13","country_code":"US","type":"education","lineage":["https://openalex.org/I130238516"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"Allison Selwood","raw_affiliation_strings":["Department of Neurology (Drs. Mendez and Frey, Ms. Selwood), and from The Alzheimer's Treatment and Research Center (Dr. Frey), St. Paul-Ramsey Medical Center, and The University of Minnesota, St. Paul, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology (Drs. Mendez and Frey, Ms. Selwood), and from The Alzheimer's Treatment and Research Center (Dr. Frey), St. Paul-Ramsey Medical Center, and The University of Minnesota, St. Paul, Minnesota","institution_ids":["https://openalex.org/I130238516"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5046805860","display_name":"William H. Frey","orcid":"https://orcid.org/0000-0002-6373-0794","observed_orcids":["https://orcid.org/0000-0002-6373-0794"]},"institutions":[{"id":"https://openalex.org/I130238516","display_name":"University of Minnesota","ror":"https://ror.org/017zqws13","country_code":"US","type":"education","lineage":["https://openalex.org/I130238516"]}],"countries":["US"],"is_corresponding":false,"raw_author_name":"William H. Frey","raw_affiliation_strings":["Department of Neurology (Drs. Mendez and Frey, Ms. Selwood), and from The Alzheimer's Treatment and Research Center (Dr. Frey), St. Paul-Ramsey Medical Center, and The University of Minnesota, St. Paul, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology (Drs. Mendez and Frey, Ms. Selwood), and from The Alzheimer's Treatment and Research Center (Dr. Frey), St. Paul-Ramsey Medical Center, and The University of Minnesota, St. Paul, Minnesota","institution_ids":["https://openalex.org/I130238516"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I130238516"],"apc_list":{"value":4150,"currency":"USD","value_usd":4150},"apc_paid":null,"fwci":0.1062,"has_fulltext":false,"cited_by_count":3,"citation_normalized_percentile":{"value":0.30392242,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"7","issue":"4","first_page":"206","last_page":"208"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11335","display_name":"Prion Diseases and Protein Misfolding","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11335","display_name":"Prion Diseases and Protein Misfolding","score":1.0,"subfield":{"id":"https://openalex.org/subfields/1312","display_name":"Molecular Biology"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T10009","display_name":"Dementia and Cognitive Impairment Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2738","display_name":"Psychiatry and Mental health"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11305","display_name":"Amyloidosis: Diagnosis, Treatment, Outcomes","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2724","display_name":"Internal Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/spongiform-encephalopathy","display_name":"spongiform encephalopathy","score":0.8579999804496765},{"id":"https://openalex.org/keywords/misdiagnosis","display_name":"misdiagnosis","score":0.6769999861717224},{"id":"https://openalex.org/keywords/dementia","display_name":"dementia","score":0.6970000267028809},{"id":"https://openalex.org/keywords/primitive-reflexes","display_name":"primitive reflexes","score":0.9909999966621399},{"id":"https://openalex.org/keywords/eeg-abnormalities","display_name":"EEG abnormalities","score":0.7850000262260437},{"id":"https://openalex.org/keywords/myoclonus","display_name":"myoclonus","score":0.9330000281333923},{"id":"https://openalex.org/keywords/prion-disease","display_name":"prion disease","score":0.531000018119812},{"id":"https://openalex.org/keywords/differential-diagnosis","display_name":"differential diagnosis","score":0.546999990940094}],"concepts":[{"id":"https://openalex.org/C2779483572","wikidata":"https://www.wikidata.org/wiki/Q83030","display_name":"Dementia","level":3,"score":0.7302453517913818},{"id":"https://openalex.org/C2776538686","wikidata":"https://www.wikidata.org/wiki/Q116275","display_name":"Myoclonus","level":2,"score":0.6774533987045288},{"id":"https://openalex.org/C2779504383","wikidata":"https://www.wikidata.org/wiki/Q41482","display_name":"Autopsy","level":2,"score":0.650807797908783},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.614555299282074},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5824369788169861},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.5032584071159363},{"id":"https://openalex.org/C2778621155","wikidata":"https://www.wikidata.org/wiki/Q576349","display_name":"Encephalopathy","level":2,"score":0.46865788102149963},{"id":"https://openalex.org/C2910731194","wikidata":"https://www.wikidata.org/wiki/Q49989","display_name":"Creutzfeldt-Jakob Syndrome","level":4,"score":0.43764206767082214},{"id":"https://openalex.org/C2777427615","wikidata":"https://www.wikidata.org/wiki/Q954257","display_name":"Degenerative disease","level":3,"score":0.4242955148220062},{"id":"https://openalex.org/C118552586","wikidata":"https://www.wikidata.org/wiki/Q7867","display_name":"Psychiatry","level":1,"score":0.2500626742839813},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.22963657975196838},{"id":"https://openalex.org/C3019804061","wikidata":"https://www.wikidata.org/wiki/Q14881255","display_name":"Prion protein","level":3,"score":0.0}],"mesh":[{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001480","descriptor_name":"Basal Ganglia Diseases","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D001480","descriptor_name":"Basal Ganglia Diseases","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D002540","descriptor_name":"Cerebral Cortex","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":true},{"descriptor_ui":"D002540","descriptor_name":"Cerebral Cortex","qualifier_ui":"Q000648","qualifier_name":"ultrastructure","is_major_topic":false},{"descriptor_ui":"D002908","descriptor_name":"Chronic Disease","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003704","descriptor_name":"Dementia","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D003937","descriptor_name":"Diagnosis, Differential","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007562","descriptor_name":"Creutzfeldt-Jakob Syndrome","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D007562","descriptor_name":"Creutzfeldt-Jakob Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D007562","descriptor_name":"Creutzfeldt-Jakob Syndrome","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010554","descriptor_name":"Personality Disorders","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D016631","descriptor_name":"Lewy Bodies","qualifier_ui":"Q000648","qualifier_name":"ultrastructure","is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1177/089198879400700402","doi":"https://doi.org/10.1177/089198879400700402","is_oa":false,"landing_page_url":"https://doi.org/10.1177/089198879400700402","pdf_url":null,"source":{"id":"https://openalex.org/S182765863","display_name":"Journal of Geriatric Psychiatry and Neurology","issn_l":"0891-9887","issn":["0891-9887","1552-5708"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-c","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-2","vabb-shw"],"host_organization":"https://openalex.org/P4310320017","host_organization_name":"SAGE Publishing","host_organization_lineage":["https://openalex.org/P4310320017"],"host_organization_lineage_names":["SAGE Publishing"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of Geriatric Psychiatry and Neurology","raw_type":"journal-article"},{"id":"pmid:7826487","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/7826487","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of geriatric psychiatry and neurology","raw_type":"Case Reports"},{"id":"pmh:oai:CiteSeerX.psu:10.1.1.910.455","doi":null,"is_oa":false,"landing_page_url":"http://citeseerx.ist.psu.edu/viewdoc/summary?doi=10.1.1.910.455","pdf_url":null,"source":null,"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"http://jgp.sagepub.com/content/7/4/206.full.pdf","raw_type":"text"}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.9763000011444092,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":14,"referenced_works":["https://openalex.org/W165833306","https://openalex.org/W1990148513","https://openalex.org/W1999664803","https://openalex.org/W1999719668","https://openalex.org/W2010891279","https://openalex.org/W2018298463","https://openalex.org/W2053187227","https://openalex.org/W2069128650","https://openalex.org/W2079646557","https://openalex.org/W2106130696","https://openalex.org/W2132767410","https://openalex.org/W2410826707","https://openalex.org/W2474046977","https://openalex.org/W2947190918"],"related_works":["https://openalex.org/W2413794970","https://openalex.org/W2071435683","https://openalex.org/W4200627634","https://openalex.org/W2274135938","https://openalex.org/W4400152054","https://openalex.org/W1486579592","https://openalex.org/W2122040748","https://openalex.org/W2395889739","https://openalex.org/W2049281822","https://openalex.org/W2948741697"],"abstract_inverted_index":{"Chronic":[0],"Creutzfeldt-Jakob":[1,81],"disease,":[2,82],"presenting":[3],"in":[4,69],"later":[5],"life,":[6],"may":[7,20],"be":[8],"difficult":[9],"to":[10],"distinguish":[11],"from":[12],"other":[13,59],"dementing":[14],"illnesses.":[15],"Patients":[16],"with":[17,32,86],"this":[18],"disease":[19],"lack":[21],"the":[22,70,84],"characteristic":[23],"myoclonus":[24],"and":[25,42,58,89],"electroencephalographic":[26,87],"complexes.":[27],"We":[28],"report":[29],"four":[30,50],"patients":[31,51],"a":[33,44,73],"slowly":[34],"progressive":[35],"dementia":[36,74],"who":[37],"were":[38],"misdiagnosed":[39],"during":[40],"life":[41],"had":[43,52],"spongiform":[45],"encephalopathy":[46],"at":[47],"autopsy.":[48],"All":[49],"early":[53,68],"extrapyramidal":[54],"rigidity,":[55],"primitive":[56],"reflexes,":[57],"neurologic":[60,66],"signs.":[61],"The":[62],"presence":[63],"of":[64,72],"these":[65],"findings":[67],"course":[71],"suggests":[75],"that":[76],"clinicians":[77],"should":[78],"consider":[79],"chronic":[80],"evaluate":[83],"patient":[85],"studies,":[88],"emphasize":[90],"universal":[91],"tissue":[92],"precautions.":[93]},"counts_by_year":[],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
