{"id":"https://openalex.org/W1985451835","doi":"https://doi.org/10.1001/archneur.56.8.1010","title":"\"Neuro-Sweet Disease\": Benign Recurrent Encephalitis With Neutrophilic Dermatosis","display_name":"\"Neuro-Sweet Disease\": Benign Recurrent Encephalitis With Neutrophilic Dermatosis","publication_year":1999,"publication_date":"1999-08-01","ids":{"openalex":"https://openalex.org/W1985451835","doi":"https://doi.org/10.1001/archneur.56.8.1010","mag":"1985451835","pmid":"https://pubmed.ncbi.nlm.nih.gov/10448808"},"language":"en","primary_location":{"id":"doi:10.1001/archneur.56.8.1010","doi":"https://doi.org/10.1001/archneur.56.8.1010","is_oa":false,"landing_page_url":"https://doi.org/10.1001/archneur.56.8.1010","pdf_url":null,"source":{"id":"https://openalex.org/S4210230857","display_name":"Archives of Neurology","issn_l":"0003-9942","issn":["0003-9942","1538-3687"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core"],"host_organization":"https://openalex.org/P4310320259","host_organization_name":"American Medical Association","host_organization_lineage":["https://openalex.org/P4310320259"],"host_organization_lineage_names":["American Medical Association"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of Neurology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5029368734","display_name":"Kinya Hisanaga","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4405255506","display_name":"Miyagi National Hospital","ror":"https://ror.org/03344ty51","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4405255506"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Kinya Hisanaga","raw_affiliation_strings":["Department of Neurology and Clinical Research Center, Miyagi National Hospital, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Neurology and Clinical Research Center, Miyagi National Hospital, Japan","institution_ids":["https://openalex.org/I4405255506"]}]},{"author_position":"middle","author":{"id":null,"display_name":"Michiko Hosokawa","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Michiko Hosokawa","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5112638335","display_name":"Nobuyuki Sato","orcid":"https://orcid.org/0009-0000-2403-1643","observed_orcids":["https://orcid.org/0009-0000-2403-1643"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nobuyuki Sato","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5082836616","display_name":"Hiroshi Mochizuki","orcid":"https://orcid.org/0009-0001-6744-0559","observed_orcids":["https://orcid.org/0009-0001-6744-0559"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Hiroshi Mochizuki","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111380662","display_name":"Yasuto Itoyama","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Yasuto Itoyama","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5103453992","display_name":"Yuzo Iwasaki","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Yuzo Iwasaki","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":2.1652,"has_fulltext":false,"cited_by_count":82,"citation_normalized_percentile":{"value":0.86495836,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":98},"biblio":{"volume":"56","issue":"8","first_page":"1010","last_page":"1010"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12328","display_name":"Autoimmune and Inflammatory Disorders","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2708","display_name":"Dermatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11194","display_name":"Ocular Diseases and Beh\u00e7et\u2019s Syndrome","score":0.0003000000142492354,"subfield":{"id":"https://openalex.org/subfields/2731","display_name":"Ophthalmology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10697","display_name":"Vasculitis and related conditions","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2745","display_name":"Rheumatology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/sweet-syndrome","display_name":"Sweet syndrome","score":0.8569999933242798},{"id":"https://openalex.org/keywords/behcet-s-disease","display_name":"Beh\u00e7et's disease","score":0.9210000038146973},{"id":"https://openalex.org/keywords/hla-b54","display_name":"HLA-B54","score":0.9599999785423279},{"id":"https://openalex.org/keywords/corticosteroid-therapy","display_name":"corticosteroid therapy","score":0.8510000109672546},{"id":"https://openalex.org/keywords/prednisolone","display_name":"prednisolone","score":0.9580000042915344},{"id":"https://openalex.org/keywords/neutrophilic-dermatitis","display_name":"neutrophilic dermatitis","score":0.8009999990463257},{"id":"https://openalex.org/keywords/central-nervous-system-involvement","display_name":"central nervous system involvement","score":0.7450000047683716},{"id":"https://openalex.org/keywords/mucocutaneous-manifestations","display_name":"mucocutaneous manifestations","score":0.7699999809265137}],"concepts":[{"id":"https://openalex.org/C156662089","wikidata":"https://www.wikidata.org/wiki/Q6931223","display_name":"Mucocutaneous zone","level":3,"score":0.7914078235626221},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.7065929174423218},{"id":"https://openalex.org/C2776715498","wikidata":"https://www.wikidata.org/wiki/Q11426176","display_name":"Prednisolone","level":2,"score":0.6570632457733154},{"id":"https://openalex.org/C83455156","wikidata":"https://www.wikidata.org/wiki/Q199615","display_name":"Encephalitis","level":3,"score":0.5316890478134155},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5247000455856323},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.4979403018951416},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.4911961257457733},{"id":"https://openalex.org/C2781428731","wikidata":"https://www.wikidata.org/wiki/Q911427","display_name":"Behcet's disease","level":3,"score":0.4169631004333496},{"id":"https://openalex.org/C2908805171","wikidata":"https://www.wikidata.org/wiki/Q1514476","display_name":"Sweet Syndrome","level":2,"score":0.41383105516433716},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.18753644824028015},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.16293972730636597},{"id":"https://openalex.org/C2522874641","wikidata":"https://www.wikidata.org/wiki/Q808","display_name":"Virus","level":2,"score":0.08583709597587585}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000893","descriptor_name":"Anti-Inflammatory Agents","qualifier_ui":"Q000627","qualifier_name":"therapeutic use","is_major_topic":false},{"descriptor_ui":"D001528","descriptor_name":"Behcet Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D001921","descriptor_name":"Brain","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D003937","descriptor_name":"Diagnosis, Differential","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D004660","descriptor_name":"Encephalitis","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D004660","descriptor_name":"Encephalitis","qualifier_ui":"Q000188","qualifier_name":"drug therapy","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008279","descriptor_name":"Magnetic Resonance Imaging","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009504","descriptor_name":"Neutrophils","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012008","descriptor_name":"Recurrence","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013256","descriptor_name":"Steroids","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015235","descriptor_name":"HLA-B Antigens","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D016463","descriptor_name":"Sweet Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D016463","descriptor_name":"Sweet Syndrome","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1001/archneur.56.8.1010","doi":"https://doi.org/10.1001/archneur.56.8.1010","is_oa":false,"landing_page_url":"https://doi.org/10.1001/archneur.56.8.1010","pdf_url":null,"source":{"id":"https://openalex.org/S4210230857","display_name":"Archives of Neurology","issn_l":"0003-9942","issn":["0003-9942","1538-3687"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core"],"host_organization":"https://openalex.org/P4310320259","host_organization_name":"American Medical Association","host_organization_lineage":["https://openalex.org/P4310320259"],"host_organization_lineage_names":["American Medical Association"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of Neurology","raw_type":"journal-article"},{"id":"pmid:10448808","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/10448808","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Archives of neurology","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3","score":0.9922999739646912}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":18,"referenced_works":["https://openalex.org/W1979862347","https://openalex.org/W1984766495","https://openalex.org/W2009347072","https://openalex.org/W2014826952","https://openalex.org/W2047503807","https://openalex.org/W2057524608","https://openalex.org/W2069585539","https://openalex.org/W2083760792","https://openalex.org/W2085691139","https://openalex.org/W2110359844","https://openalex.org/W2110861137","https://openalex.org/W2111991423","https://openalex.org/W2146115523","https://openalex.org/W2158199056","https://openalex.org/W2460800676","https://openalex.org/W2463465627","https://openalex.org/W2473433727","https://openalex.org/W4214522682"],"related_works":["https://openalex.org/W135216395","https://openalex.org/W2335003364","https://openalex.org/W2014826952","https://openalex.org/W2189287858","https://openalex.org/W2134142302","https://openalex.org/W2907780895","https://openalex.org/W2315438183","https://openalex.org/W3015276448","https://openalex.org/W2158170783","https://openalex.org/W2110359844"],"abstract_inverted_index":{"OBJECTIVE:":[0],"To":[1],"describe":[2],"benign":[3],"recurrent":[4,125],"encephalitis":[5,30,102,126],"in":[6,50,84,89],"a":[7,55,134],"case":[8],"of":[9,17,45,57,64,157],"Sweet":[10,75,85,121],"syndrome":[11,86],"that":[12,113,118,147],"also":[13],"showed":[14,40,79],"clinical":[15],"features":[16],"Beh\u00e7et":[18,35,90,158],"disease.":[19,36,91,159],"CASE":[20],"REPORT:":[21],"A":[22,60],"37-year-old":[23],"Japanese":[24],"man":[25],"developed":[26],"relapsing":[27],"and":[28,31,133],"remitting":[29],"mucocutaneous":[32,108],"symptoms":[33],"mimicking":[34],"Magnetic":[37],"resonance":[38],"images":[39],"at":[41],"least":[42],"5":[43,58],"episodes":[44],"transient":[46],"abnormal":[47],"signal":[48],"intensity":[49],"various":[51],"cerebral":[52],"regions":[53],"over":[54],"period":[56],"years.":[59],"skin":[61],"biopsy":[62],"specimen":[63],"the":[65,101,107,151],"cutaneous":[66],"edematous":[67],"erythematous":[68],"plaques":[69],"revealed":[70],"neutrophilic":[71],"dermatitis":[72],"compatible":[73],"with":[74,124,131],"syndrome.":[76],"HLA":[77],"typing":[78],"B54,":[80],"which":[81,140],"is":[82,115,119,148],"frequent":[83],"but":[87,123],"rare":[88],"Oral":[92],"prednisolone":[93],"therapy":[94],"(10-60":[95],"mg/d)":[96],"was":[97],"remarkably":[98],"effective":[99],"for":[100,106],"as":[103,105],"well":[104],"symptoms.":[109],"CONCLUSION:":[110],"We":[111],"propose":[112],"there":[114],"an":[116,129],"entity":[117],"like":[120],"disease,":[122,146],"characterized":[127],"by":[128],"association":[130],"HLA-B54":[132],"high":[135],"responsiveness":[136],"to":[137],"corticosteroid":[138],"therapy,":[139],"we":[141],"have":[142],"tentatively":[143],"named":[144],"neuro-Sweet":[145],"distinct":[149],"from":[150],"classic":[152],"central":[153],"nervous":[154],"system":[155],"involvement":[156]},"counts_by_year":[{"year":2026,"cited_by_count":1},{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":3},{"year":2023,"cited_by_count":4},{"year":2022,"cited_by_count":2},{"year":2021,"cited_by_count":2},{"year":2020,"cited_by_count":3},{"year":2019,"cited_by_count":5},{"year":2018,"cited_by_count":4},{"year":2017,"cited_by_count":1},{"year":2016,"cited_by_count":5},{"year":2015,"cited_by_count":2},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":1},{"year":2012,"cited_by_count":3}],"updated_date":"2026-11-12T12:28:57.059296","created_date":"2016-06-24T00:00:00"}