{"id":"https://openalex.org/W1983116995","doi":"https://doi.org/10.1007/s004670050281","title":"Autosomal recessive polycystic kidney disease: long-term outcome of neonatal survivors","display_name":"Autosomal recessive polycystic kidney disease: long-term outcome of neonatal survivors","publication_year":1997,"publication_date":"1997-05-26","ids":{"openalex":"https://openalex.org/W1983116995","doi":"https://doi.org/10.1007/s004670050281","mag":"1983116995","pmid":"https://pubmed.ncbi.nlm.nih.gov/9203177"},"language":"en","primary_location":{"id":"doi:10.1007/s004670050281","doi":"https://doi.org/10.1007/s004670050281","is_oa":false,"landing_page_url":"https://doi.org/10.1007/s004670050281","pdf_url":null,"source":{"id":"https://openalex.org/S25178087","display_name":"Pediatric Nephrology","issn_l":"0931-041X","issn":["0931-041X","1432-198X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319900","host_organization_name":"Springer Science+Business Media","host_organization_lineage":["https://openalex.org/P4310319900","https://openalex.org/P4310319965"],"host_organization_lineage_names":["Springer Science+Business Media","Springer Nature"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Nephrology","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"Sushmita Roy","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2800129641","display_name":"Great Ormond Street Hospital","ror":"https://ror.org/00zn2c847","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I2800129641","https://openalex.org/I2800349819"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Sushmita Roy","raw_affiliation_strings":["Renal Unit, Great Ormond Street Hospital for Children, London, UK"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Renal Unit, Great Ormond Street Hospital for Children, London, UK","institution_ids":["https://openalex.org/I2800129641"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5041706087","display_name":"Michael J. Dillon","orcid":"https://orcid.org/0000-0001-6751-7678","observed_orcids":["https://orcid.org/0000-0001-6751-7678","https://orcid.org/0009-0005-2163-9756"]},"institutions":[{"id":"https://openalex.org/I2800129641","display_name":"Great Ormond Street Hospital","ror":"https://ror.org/00zn2c847","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I2800129641","https://openalex.org/I2800349819"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Michael J. Dillon","raw_affiliation_strings":["Renal Unit, Great Ormond Street Hospital for Children, London, UK, GB"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Renal Unit, Great Ormond Street Hospital for Children, London, UK, GB","institution_ids":["https://openalex.org/I2800129641"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111597147","display_name":"Richard S. Trompeter","orcid":"https://orcid.org/0000-0003-0044-021X","observed_orcids":["https://orcid.org/0000-0003-0044-021X"]},"institutions":[{"id":"https://openalex.org/I2800129641","display_name":"Great Ormond Street Hospital","ror":"https://ror.org/00zn2c847","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I2800129641","https://openalex.org/I2800349819"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"Richard S. Trompeter","raw_affiliation_strings":["Renal Unit, Great Ormond Street Hospital for Children, London, UK, GB"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Renal Unit, Great Ormond Street Hospital for Children, London, UK, GB","institution_ids":["https://openalex.org/I2800129641"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5044717554","display_name":"T M Barratt","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I2800129641","display_name":"Great Ormond Street Hospital","ror":"https://ror.org/00zn2c847","country_code":"GB","type":"healthcare","lineage":["https://openalex.org/I2800129641","https://openalex.org/I2800349819"]}],"countries":["GB"],"is_corresponding":false,"raw_author_name":"T. Martin Barratt","raw_affiliation_strings":["Renal Unit, Great Ormond Street Hospital for Children, London, UK, GB"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Renal Unit, Great Ormond Street Hospital for Children, London, UK, GB","institution_ids":["https://openalex.org/I2800129641"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":["https://openalex.org/I2800129641"],"apc_list":{"value":4337,"currency":"USD","value_usd":4337},"apc_paid":null,"fwci":1.1202,"has_fulltext":false,"cited_by_count":209,"citation_normalized_percentile":{"value":0.74536982,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":100},"biblio":{"volume":"11","issue":"3","first_page":"302","last_page":"306"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11412","display_name":"Genetic and Kidney Cyst Diseases","score":0.9945999979972839,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11412","display_name":"Genetic and Kidney Cyst Diseases","score":0.9945999979972839,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T12460","display_name":"Pediatric Hepatobiliary Diseases and Treatments","score":0.00139999995008111,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11027","display_name":"Metabolism and Genetic Disorders","score":0.0013000000035390258,"subfield":{"id":"https://openalex.org/subfields/1308","display_name":"Clinical Biochemistry"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/autosomal-recessive-polycystic-kidney-disease","display_name":"autosomal recessive polycystic kidney disease","score":1.0},{"id":"https://openalex.org/keywords/long-term-outcomes","display_name":"long-term outcomes","score":0.7739999890327454},{"id":"https://openalex.org/keywords/newborn-survival","display_name":"neonatal survival","score":0.7950000166893005},{"id":"https://openalex.org/keywords/renal-survival","display_name":"renal survival","score":0.9269999861717224},{"id":"https://openalex.org/keywords/liver-dysfunction","display_name":"liver dysfunction","score":0.6890000104904175},{"id":"https://openalex.org/keywords/portal-hypertension","display_name":"portal hypertension","score":0.8619999885559082},{"id":"https://openalex.org/keywords/gastroesophageal-varices","display_name":"gastroesophageal varices","score":0.7979999780654907},{"id":"https://openalex.org/keywords/hypersplenism","display_name":"hypersplenism","score":0.9869999885559082},{"id":"https://openalex.org/keywords/antihypertensive-therapy","display_name":"antihypertensive therapy","score":0.875},{"id":"https://openalex.org/keywords/kidney-transplantation","display_name":"kidney transplantation","score":0.765999972820282},{"id":"https://openalex.org/keywords/dialysis","display_name":"dialysis","score":0.7699999809265137},{"id":"https://openalex.org/keywords/children","display_name":"children","score":0.3019999861717224}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9348130226135254},{"id":"https://openalex.org/C2910547607","wikidata":"https://www.wikidata.org/wiki/Q3395618","display_name":"Autosomal Recessive Polycystic Kidney Disease","level":4,"score":0.6393722295761108},{"id":"https://openalex.org/C54847362","wikidata":"https://www.wikidata.org/wiki/Q177635","display_name":"Nephrology","level":2,"score":0.6377716064453125},{"id":"https://openalex.org/C2780145431","wikidata":"https://www.wikidata.org/wiki/Q15443105","display_name":"Polycystic kidney disease","level":3,"score":0.6301807165145874},{"id":"https://openalex.org/C2778808290","wikidata":"https://www.wikidata.org/wiki/Q124604","display_name":"Portal hypertension","level":3,"score":0.5713803172111511},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.5686415433883667},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.5624602437019348},{"id":"https://openalex.org/C2778012290","wikidata":"https://www.wikidata.org/wiki/Q2624485","display_name":"Varices","level":3,"score":0.5172775387763977},{"id":"https://openalex.org/C2780091579","wikidata":"https://www.wikidata.org/wiki/Q9377","display_name":"Kidney","level":2,"score":0.45845216512680054},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.44943535327911377},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.3369433581829071},{"id":"https://openalex.org/C2777214474","wikidata":"https://www.wikidata.org/wiki/Q147778","display_name":"Cirrhosis","level":2,"score":0.1021464467048645}],"mesh":[{"descriptor_ui":"D000293","descriptor_name":"Adolescent","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002423","descriptor_name":"Cause of Death","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005500","descriptor_name":"Follow-Up Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006977","descriptor_name":"Hypertension, Renal","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D006977","descriptor_name":"Hypertension, Renal","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":false},{"descriptor_ui":"D007223","descriptor_name":"Infant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007231","descriptor_name":"Infant, Newborn","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007676","descriptor_name":"Kidney Failure, Chronic","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012140","descriptor_name":"Respiratory Tract Diseases","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D012140","descriptor_name":"Respiratory Tract Diseases","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":false},{"descriptor_ui":"D013534","descriptor_name":"Survival","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D014552","descriptor_name":"Urinary Tract Infections","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D015993","descriptor_name":"Life Tables","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016896","descriptor_name":"Treatment Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D017044","descriptor_name":"Polycystic Kidney, Autosomal Recessive","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D017044","descriptor_name":"Polycystic Kidney, Autosomal Recessive","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":true},{"descriptor_ui":"D017044","descriptor_name":"Polycystic Kidney, Autosomal Recessive","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D017741","descriptor_name":"Survivors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":3,"locations":[{"id":"doi:10.1007/s004670050281","doi":"https://doi.org/10.1007/s004670050281","is_oa":false,"landing_page_url":"https://doi.org/10.1007/s004670050281","pdf_url":null,"source":{"id":"https://openalex.org/S25178087","display_name":"Pediatric Nephrology","issn_l":"0931-041X","issn":["0931-041X","1432-198X"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-140","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310319900","host_organization_name":"Springer Science+Business Media","host_organization_lineage":["https://openalex.org/P4310319900","https://openalex.org/P4310319965"],"host_organization_lineage_names":["Springer Science+Business Media","Springer Nature"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Nephrology","raw_type":"journal-article"},{"id":"pmid:9203177","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/9203177","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric nephrology (Berlin, Germany)","raw_type":"Clinical Trial"},{"id":"pmh:oai:eprints.ucl.ac.uk.OAI2:34827","doi":null,"is_oa":false,"landing_page_url":"http://discovery.ucl.ac.uk/34827/","pdf_url":null,"source":{"id":"https://openalex.org/S4306400024","display_name":"UCL Discovery (University College London)","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I45129253","host_organization_name":"University College London","host_organization_lineage":["https://openalex.org/I45129253"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"submittedVersion","is_accepted":false,"is_published":false,"raw_source_name":"Pediatric Nephrology , 11 pp. 302-306. (1997)","raw_type":"Article"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","score":1.0,"display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":25,"referenced_works":["https://openalex.org/W18268121","https://openalex.org/W95782458","https://openalex.org/W1568706542","https://openalex.org/W1981778952","https://openalex.org/W1990512238","https://openalex.org/W2005969046","https://openalex.org/W2009137611","https://openalex.org/W2012159432","https://openalex.org/W2014900304","https://openalex.org/W2019049688","https://openalex.org/W2029871205","https://openalex.org/W2040401258","https://openalex.org/W2045518675","https://openalex.org/W2062811388","https://openalex.org/W2070891976","https://openalex.org/W2111426248","https://openalex.org/W2112810226","https://openalex.org/W2118202495","https://openalex.org/W2123332237","https://openalex.org/W2152162813","https://openalex.org/W2402374934","https://openalex.org/W2411508188","https://openalex.org/W2417797886","https://openalex.org/W2461403197","https://openalex.org/W2797597138"],"related_works":["https://openalex.org/W2029871205","https://openalex.org/W2125946047","https://openalex.org/W2144700911","https://openalex.org/W2005969046","https://openalex.org/W2009137611","https://openalex.org/W1546157928","https://openalex.org/W1966640789","https://openalex.org/W3105833869","https://openalex.org/W2400169517","https://openalex.org/W177607322"],"abstract_inverted_index":null,"counts_by_year":[{"year":2026,"cited_by_count":6},{"year":2025,"cited_by_count":2},{"year":2024,"cited_by_count":1},{"year":2023,"cited_by_count":11},{"year":2022,"cited_by_count":5},{"year":2021,"cited_by_count":4},{"year":2020,"cited_by_count":10},{"year":2019,"cited_by_count":6},{"year":2018,"cited_by_count":8},{"year":2017,"cited_by_count":10},{"year":2016,"cited_by_count":8},{"year":2015,"cited_by_count":16},{"year":2014,"cited_by_count":9},{"year":2013,"cited_by_count":7},{"year":2012,"cited_by_count":9}],"updated_date":"2026-11-07T11:25:07.637180","created_date":"2016-06-24T00:00:00"}
