{"id":"https://openalex.org/W1982960588","doi":"https://doi.org/10.1002/ppul.1950170102","title":"Chronic respiratory failure of infancy and childhood: Clinical outcomes based on underlying etiology","display_name":"Chronic respiratory failure of infancy and childhood: Clinical outcomes based on underlying etiology","publication_year":1994,"publication_date":"1994-01-01","ids":{"openalex":"https://openalex.org/W1982960588","doi":"https://doi.org/10.1002/ppul.1950170102","mag":"1982960588","pmid":"https://pubmed.ncbi.nlm.nih.gov/7509054"},"language":"en","primary_location":{"id":"doi:10.1002/ppul.1950170102","doi":"https://doi.org/10.1002/ppul.1950170102","is_oa":false,"landing_page_url":"https://doi.org/10.1002/ppul.1950170102","pdf_url":null,"source":{"id":"https://openalex.org/S144578311","display_name":"Pediatric Pulmonology","issn_l":"1099-0496","issn":["1099-0496","8755-6863"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Pulmonology","raw_type":"journal-article"},"volume":null,"type":"article","indexed_in":["crossref","pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"William B. Wheeler","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":true,"raw_author_name":"William B. Wheeler","raw_affiliation_strings":["Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minnesota","Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minnesota","institution_ids":[]},{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5108198947","display_name":"Eleanor L. Maguire","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Eleanor L. Maguire","raw_affiliation_strings":["Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5035034327","display_name":"Stephen C. Kurachek","orcid":"https://orcid.org/0000-0002-5165-1888","observed_orcids":["https://orcid.org/0000-0002-5165-1888"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Stephen C. Kurachek","raw_affiliation_strings":["Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5029895108","display_name":"Jeffrey G. Lobas","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jeffrey G. Lobas","raw_affiliation_strings":["Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5061589792","display_name":"John H. Fugate","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"John H. Fugate","raw_affiliation_strings":["Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5051055602","display_name":"John McNamara","orcid":"https://orcid.org/0000-0001-5893-5536","observed_orcids":["https://orcid.org/0000-0001-5893-5536"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"John J. McNamara","raw_affiliation_strings":["Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Division of Pulmonary and Critical Care Medicine, Minneapolis Children's Medical Center, Minneapolis, Minnesota","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":0,"institutions_distinct_count":0,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":4740,"currency":"USD","value_usd":4740},"apc_paid":null,"fwci":2.9595,"has_fulltext":false,"cited_by_count":43,"citation_normalized_percentile":{"value":0.90326276,"is_in_top_1_percent":false,"is_in_top_10_percent":true},"cited_by_percentile_year":{"min":89,"max":98},"biblio":{"volume":"17","issue":"1","first_page":"1","last_page":"5"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10549","display_name":"Neonatal Respiratory Health Research","score":0.8726000189781189,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10549","display_name":"Neonatal Respiratory Health Research","score":0.8726000189781189,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10322","display_name":"Respiratory Support and Mechanisms","score":0.04809999838471413,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11260","display_name":"Tracheal and airway disorders","score":0.039900001138448715,"subfield":{"id":"https://openalex.org/subfields/2740","display_name":"Pulmonary and Respiratory Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/chronic-respiratory-failure","display_name":"chronic respiratory failure","score":0.9679999947547913},{"id":"https://openalex.org/keywords/infancy","display_name":"infancy","score":0.531000018119812},{"id":"https://openalex.org/keywords/childhood","display_name":"childhood","score":0.9779999852180481},{"id":"https://openalex.org/keywords/chronic-lung-disease","display_name":"chronic lung disease","score":0.8510000109672546},{"id":"https://openalex.org/keywords/neuromuscular-disorders","display_name":"neuromuscular disorders","score":0.9129999876022339},{"id":"https://openalex.org/keywords/mortality","display_name":"mortality","score":0.5920000076293945},{"id":"https://openalex.org/keywords/morbidity","display_name":"morbidity","score":0.9139999747276306},{"id":"https://openalex.org/keywords/weaning-from-mechanical-ventilation","display_name":"weaning from mechanical ventilation","score":0.7639999985694885},{"id":"https://openalex.org/keywords/tracheostomy","display_name":"tracheostomy","score":0.9470000267028809},{"id":"https://openalex.org/keywords/tracheomalacia","display_name":"tracheomalacia","score":0.9700000286102295},{"id":"https://openalex.org/keywords/feeding-disorders","display_name":"feeding disorders","score":0.8970000147819519},{"id":"https://openalex.org/keywords/hypogammaglobulinemia","display_name":"hypogammaglobulinemia","score":0.9700000286102295},{"id":"https://openalex.org/keywords/neurodevelopmental-outcomes","display_name":"neurodevelopmental outcomes","score":0.9139999747276306},{"id":"https://openalex.org/keywords/family-dysfunction","display_name":"family dysfunction","score":0.7900000214576721}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9492015838623047},{"id":"https://openalex.org/C2778974821","wikidata":"https://www.wikidata.org/wiki/Q910455","display_name":"Tracheomalacia","level":3,"score":0.7668215036392212},{"id":"https://openalex.org/C2776888751","wikidata":"https://www.wikidata.org/wiki/Q767485","display_name":"Respiratory failure","level":2,"score":0.6663443446159363},{"id":"https://openalex.org/C137627325","wikidata":"https://www.wikidata.org/wiki/Q156318","display_name":"Etiology","level":2,"score":0.6424918174743652},{"id":"https://openalex.org/C2777080012","wikidata":"https://www.wikidata.org/wiki/Q3766250","display_name":"Mechanical ventilation","level":2,"score":0.632721483707428},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.587713897228241},{"id":"https://openalex.org/C2776356578","wikidata":"https://www.wikidata.org/wiki/Q2246789","display_name":"Neuromuscular disease","level":3,"score":0.5467908382415771},{"id":"https://openalex.org/C534529494","wikidata":"https://www.wikidata.org/wiki/Q7891","display_name":"Respiratory system","level":2,"score":0.5340468287467957},{"id":"https://openalex.org/C2780655333","wikidata":"https://www.wikidata.org/wiki/Q333203","display_name":"Weaning","level":2,"score":0.5065606832504272},{"id":"https://openalex.org/C2777805810","wikidata":"https://www.wikidata.org/wiki/Q1047559","display_name":"Hypogammaglobulinemia","level":3,"score":0.4922081530094147},{"id":"https://openalex.org/C2776178081","wikidata":"https://www.wikidata.org/wiki/Q3286546","display_name":"Respiratory disease","level":3,"score":0.44078636169433594},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.3758677542209625},{"id":"https://openalex.org/C177713679","wikidata":"https://www.wikidata.org/wiki/Q679690","display_name":"Intensive care medicine","level":1,"score":0.325178325176239},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.30141445994377136},{"id":"https://openalex.org/C2777714996","wikidata":"https://www.wikidata.org/wiki/Q7886","display_name":"Lung","level":2,"score":0.23705586791038513},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.18002161383628845},{"id":"https://openalex.org/C105922876","wikidata":"https://www.wikidata.org/wiki/Q1423981","display_name":"Airway","level":2,"score":0.09162050485610962},{"id":"https://openalex.org/C159654299","wikidata":"https://www.wikidata.org/wiki/Q79460","display_name":"Antibody","level":2,"score":0.0},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000013","descriptor_name":"Congenital Abnormalities","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002658","descriptor_name":"Developmental Disabilities","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D002675","descriptor_name":"Child, Preschool","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005500","descriptor_name":"Follow-Up Studies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007223","descriptor_name":"Infant","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008171","descriptor_name":"Lung Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D008171","descriptor_name":"Lung Diseases","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009017","descriptor_name":"Morbidity","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D009422","descriptor_name":"Nervous System Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D009422","descriptor_name":"Nervous System Diseases","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D009468","descriptor_name":"Neuromuscular Diseases","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D009468","descriptor_name":"Neuromuscular Diseases","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":false},{"descriptor_ui":"D012121","descriptor_name":"Respiration, Artificial","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D012131","descriptor_name":"Respiratory Insufficiency","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D012131","descriptor_name":"Respiratory Insufficiency","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":true},{"descriptor_ui":"D013997","descriptor_name":"Time Factors","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1002/ppul.1950170102","doi":"https://doi.org/10.1002/ppul.1950170102","is_oa":false,"landing_page_url":"https://doi.org/10.1002/ppul.1950170102","pdf_url":null,"source":{"id":"https://openalex.org/S144578311","display_name":"Pediatric Pulmonology","issn_l":"1099-0496","issn":["1099-0496","8755-6863"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["anvur-scientific","cwts-core","dongbi-d","doyens","jufo-1","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric Pulmonology","raw_type":"journal-article"},{"id":"pmid:7509054","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/7509054","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Pediatric pulmonology","raw_type":"Journal Article"}],"best_oa_location":null,"sustainable_development_goals":[{"score":1.0,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"sustainable_development_goals_aurora":[{"score":0.8899999856948853,"display_name":"Good health and well-being","id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Observational Study","id":"https://openalex.org/study-designs/observational-study"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":13,"referenced_works":["https://openalex.org/W211412019","https://openalex.org/W589156713","https://openalex.org/W1515587151","https://openalex.org/W1535788833","https://openalex.org/W1991340046","https://openalex.org/W2014830091","https://openalex.org/W2017668626","https://openalex.org/W2019187892","https://openalex.org/W2036338043","https://openalex.org/W2044778975","https://openalex.org/W2116308305","https://openalex.org/W2129759906","https://openalex.org/W2409463383"],"related_works":["https://openalex.org/W4250817770","https://openalex.org/W2899947961","https://openalex.org/W4280554961","https://openalex.org/W1545856886","https://openalex.org/W6980550470","https://openalex.org/W1964355788","https://openalex.org/W7202184469","https://openalex.org/W105779591","https://openalex.org/W2029359042","https://openalex.org/W7213552180"],"abstract_inverted_index":{"To":[0],"assess":[1],"whether":[2],"underlying":[3,188],"diagnosis":[4],"affects":[5],"morbidity":[6,181],"and":[7,26,137,154],"mortality":[8,105],"outcomes":[9,182],"in":[10,104,122],"patients":[11,19,32,175],"with":[12,20,33,106,112,118,141,176],"chronic":[13,21,34,64],"respiratory":[14,22,35,84,165],"failure,":[15],"we":[16],"studied":[17],"55":[18],"failure":[23,36],"of":[24,93,124,128,131,148],"infancy":[25],"childhood":[27],"(CRFIC).":[28],"Entry":[29],"criteria":[30],"included":[31],"due":[37],"to":[38,46,52],"static":[39],"neurologic":[40,71],"or":[41,44,54,72,79,120,167],"neuromuscular":[42,73],"conditions":[43],"secondary":[45],"other":[47],"disease":[48,66],"processes":[49],"considered":[50],"likely":[51],"improve":[53],"resolve":[55],"over":[56],"time.":[57],"Subjects":[58,140],"were":[59,99,159],"grouped":[60],"into":[61],"those":[62,117],"having":[63],"lung":[65],"(CLD,":[67],"n":[68,76,87],"=":[69,77,88],"22),":[70],"diseases":[74],"(NM,":[75],"21),":[78],"congenital":[80],"abnormalities":[81],"affecting":[82],"the":[83,187],"system":[85],"(CA,":[86],"12).":[89],"The":[90],"average":[91],"duration":[92,123,127],"follow-up":[94],"was":[95],"21.3":[96],"months.":[97],"There":[98,158],"no":[100,160],"differences":[101,161],"between":[102,162],"groups":[103,163],"only":[107],"four":[108],"deaths":[109],"(7%).":[110],"Patients":[111],"CLD":[113,142],"fared":[114],"better":[115],"than":[116],"NM":[119],"CA":[121],"ventilatory":[125],"support,":[126],"tracheostomy,":[129],"percentage":[130],"successful":[132],"weaning":[133],"from":[134],"mechanical":[135],"ventilation,":[136],"neurodevelopmental":[138],"outcomes.":[139],"had":[143],"a":[144],"significantly":[145],"greater":[146],"frequency":[147],"tracheomalacia":[149],"(86%),":[150,153],"feeding":[151],"disorders":[152],"hypogammaglobulinemia":[155],"G":[156],"(77%).":[157],"for":[164],"readmissions":[166],"family":[168],"dysfunction.":[169],"We":[170],"conclude":[171],"that":[172],"almost":[173],"all":[174],"CRFIC":[177],"will":[178,183],"survive,":[179],"but":[180],"vary":[184],"based":[185],"on":[186],"diagnosis.":[189]},"counts_by_year":[{"year":2025,"cited_by_count":1},{"year":2024,"cited_by_count":3},{"year":2023,"cited_by_count":1},{"year":2020,"cited_by_count":3},{"year":2019,"cited_by_count":1},{"year":2018,"cited_by_count":2},{"year":2015,"cited_by_count":1},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":3},{"year":2012,"cited_by_count":5}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
