{"id":"https://openalex.org/W1967421571","doi":"https://doi.org/10.1253/jcj.59.589","title":"Familial Aggregation of Dilated Cardiomyopathy. Evaluation of Clinical Characteristics and Prognosis.","display_name":"Familial Aggregation of Dilated Cardiomyopathy. Evaluation of Clinical Characteristics and Prognosis.","publication_year":1995,"publication_date":"1995-01-01","ids":{"openalex":"https://openalex.org/W1967421571","doi":"https://doi.org/10.1253/jcj.59.589","mag":"1967421571","pmid":"https://pubmed.ncbi.nlm.nih.gov/7500542"},"language":"en","primary_location":{"id":"doi:10.1253/jcj.59.589","doi":"https://doi.org/10.1253/jcj.59.589","is_oa":true,"landing_page_url":"https://doi.org/10.1253/jcj.59.589","pdf_url":"https://www.jstage.jst.go.jp/article/circj1960/59/9/59_9_589/_pdf","source":{"id":"https://openalex.org/S150042853","display_name":"Japanese Circulation Journal-english Edition","issn_l":"0047-1828","issn":["0047-1828","1347-4839"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310313287","host_organization_name":"Japanese Circulation Society","host_organization_lineage":["https://openalex.org/P4310313287"],"host_organization_lineage_names":["Japanese Circulation Society"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Japanese Circulation Journal","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://www.jstage.jst.go.jp/article/circj1960/59/9/59_9_589/_pdf","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":null,"display_name":"Yuka Honda","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I65837984","display_name":"Kobe University","ror":"https://ror.org/03tgsfw79","country_code":"JP","type":"education","lineage":["https://openalex.org/I65837984"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"Yuka Honda","raw_affiliation_strings":["First Department of Internal Medicine, Kobe University School of Medicine, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"First Department of Internal Medicine, Kobe University School of Medicine, Japan","institution_ids":["https://openalex.org/I65837984"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111444599","display_name":"Yoshiyuki Yokota","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Yoshiyuki Yokota","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5111616696","display_name":"Mitsuhiro Yokoyama","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Mitsuhiro Yokoyama","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":13,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"59","issue":"9","first_page":"589","last_page":"598"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10882","display_name":"Cardiomyopathy and Myosin Studies","score":0.9940999746322632,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10882","display_name":"Cardiomyopathy and Myosin Studies","score":0.9940999746322632,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11112","display_name":"Viral Infections and Immunology Research","score":0.0017999999690800905,"subfield":{"id":"https://openalex.org/subfields/2725","display_name":"Infectious Diseases"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11922","display_name":"Cardiovascular Effects of Exercise","score":0.0017999999690800905,"subfield":{"id":"https://openalex.org/subfields/2705","display_name":"Cardiology and Cardiovascular Medicine"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/idiopathic-dilated-cardiomyopathy","display_name":"idiopathic dilated cardiomyopathy","score":0.9509999752044678},{"id":"https://openalex.org/keywords/familial-aggregation","display_name":"familial aggregation","score":0.972000002861023},{"id":"https://openalex.org/keywords/family-screening","display_name":"family screening","score":0.7409999966621399},{"id":"https://openalex.org/keywords/prognosis","display_name":"prognosis","score":0.9380000233650208},{"id":"https://openalex.org/keywords/survival-rate","display_name":"survival rate","score":0.8849999904632568},{"id":"https://openalex.org/keywords/sudden-death","display_name":"sudden death","score":0.7910000085830688},{"id":"https://openalex.org/keywords/congestive-heart-failure","display_name":"congestive heart failure","score":0.9980000257492065},{"id":"https://openalex.org/keywords/nyha-functional-class","display_name":"NYHA functional class","score":0.9309999942779541},{"id":"https://openalex.org/keywords/left-ventricular-end-diastolic-pressure","display_name":"left ventricular end-diastolic pressure","score":0.9660000205039978},{"id":"https://openalex.org/keywords/cardiac-index","display_name":"cardiac index","score":0.9430000185966492},{"id":"https://openalex.org/keywords/early-diagnosis","display_name":"early diagnosis","score":0.7979999780654907}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8991354703903198},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.653225839138031},{"id":"https://openalex.org/C164705383","wikidata":"https://www.wikidata.org/wiki/Q10379","display_name":"Cardiology","level":1,"score":0.569876492023468},{"id":"https://openalex.org/C2776383484","wikidata":"https://www.wikidata.org/wiki/Q283656","display_name":"Dilated cardiomyopathy","level":3,"score":0.5445449948310852},{"id":"https://openalex.org/C2993353509","wikidata":"https://www.wikidata.org/wiki/Q411867","display_name":"Sudden death","level":2,"score":0.5119191408157349},{"id":"https://openalex.org/C2778198053","wikidata":"https://www.wikidata.org/wiki/Q181754","display_name":"Heart failure","level":2,"score":0.4887361526489258},{"id":"https://openalex.org/C2779962030","wikidata":"https://www.wikidata.org/wiki/Q2151267","display_name":"Restrictive cardiomyopathy","level":4,"score":0.4846237599849701},{"id":"https://openalex.org/C2775935837","wikidata":"https://www.wikidata.org/wiki/Q202837","display_name":"Sudden cardiac death","level":2,"score":0.47367388010025024},{"id":"https://openalex.org/C2778797674","wikidata":"https://www.wikidata.org/wiki/Q847583","display_name":"Cardiomyopathy","level":3,"score":0.4630233645439148},{"id":"https://openalex.org/C57900726","wikidata":"https://www.wikidata.org/wiki/Q492905","display_name":"Diastole","level":3,"score":0.4194835424423218},{"id":"https://openalex.org/C29374701","wikidata":"https://www.wikidata.org/wiki/Q1931388","display_name":"Cause of death","level":3,"score":0.4176766574382782},{"id":"https://openalex.org/C187212893","wikidata":"https://www.wikidata.org/wiki/Q123028","display_name":"Pediatrics","level":1,"score":0.3283594846725464},{"id":"https://openalex.org/C84393581","wikidata":"https://www.wikidata.org/wiki/Q82642","display_name":"Blood pressure","level":2,"score":0.3085154592990875},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.18025809526443481}],"mesh":[{"descriptor_ui":"D000293","descriptor_name":"Adolescent","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000368","descriptor_name":"Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D002311","descriptor_name":"Cardiomyopathy, Dilated","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":true},{"descriptor_ui":"D002311","descriptor_name":"Cardiomyopathy, Dilated","qualifier_ui":"Q000401","qualifier_name":"mortality","is_major_topic":false},{"descriptor_ui":"D002311","descriptor_name":"Cardiomyopathy, Dilated","qualifier_ui":"Q000453","qualifier_name":"epidemiology","is_major_topic":true},{"descriptor_ui":"D002423","descriptor_name":"Cause of Death","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D011379","descriptor_name":"Prognosis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015982","descriptor_name":"Bias","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015995","descriptor_name":"Prevalence","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015996","descriptor_name":"Survival Rate","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D016757","descriptor_name":"Death, Sudden, Cardiac","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1253/jcj.59.589","doi":"https://doi.org/10.1253/jcj.59.589","is_oa":true,"landing_page_url":"https://doi.org/10.1253/jcj.59.589","pdf_url":"https://www.jstage.jst.go.jp/article/circj1960/59/9/59_9_589/_pdf","source":{"id":"https://openalex.org/S150042853","display_name":"Japanese Circulation Journal-english Edition","issn_l":"0047-1828","issn":["0047-1828","1347-4839"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310313287","host_organization_name":"Japanese Circulation Society","host_organization_lineage":["https://openalex.org/P4310313287"],"host_organization_lineage_names":["Japanese Circulation Society"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Japanese Circulation Journal","raw_type":"journal-article"},{"id":"pmid:7500542","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/7500542","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Japanese circulation journal","raw_type":"Journal Article"}],"best_oa_location":{"id":"doi:10.1253/jcj.59.589","doi":"https://doi.org/10.1253/jcj.59.589","is_oa":true,"landing_page_url":"https://doi.org/10.1253/jcj.59.589","pdf_url":"https://www.jstage.jst.go.jp/article/circj1960/59/9/59_9_589/_pdf","source":{"id":"https://openalex.org/S150042853","display_name":"Japanese Circulation Journal-english Edition","issn_l":"0047-1828","issn":["0047-1828","1347-4839"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core"],"host_organization":"https://openalex.org/P4310313287","host_organization_name":"Japanese Circulation Society","host_organization_lineage":["https://openalex.org/P4310313287"],"host_organization_lineage_names":["Japanese Circulation Society"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Japanese Circulation Journal","raw_type":"journal-article"},"sustainable_development_goals":[{"score":1.0,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[{"id":"https://openalex.org/study-designs/observational-study","display_name":"Observational Study"}],"awards":[],"funders":[],"has_content":{"grobid_xml":true,"pdf":true},"content_urls":{"pdf":"https://content.openalex.org/works/W1967421571.pdf","grobid_xml":"https://content.openalex.org/works/W1967421571.grobid-xml"},"referenced_works_count":36,"referenced_works":["https://openalex.org/W1968218179","https://openalex.org/W1969892915","https://openalex.org/W1975365436","https://openalex.org/W1976300217","https://openalex.org/W1985404739","https://openalex.org/W1985658056","https://openalex.org/W1986879185","https://openalex.org/W1991345110","https://openalex.org/W1993492475","https://openalex.org/W1999251970","https://openalex.org/W2017767802","https://openalex.org/W2020321325","https://openalex.org/W2023322190","https://openalex.org/W2023971572","https://openalex.org/W2029659822","https://openalex.org/W2033537899","https://openalex.org/W2037271145","https://openalex.org/W2038632266","https://openalex.org/W2046195322","https://openalex.org/W2050150324","https://openalex.org/W2064104523","https://openalex.org/W2068239367","https://openalex.org/W2075808123","https://openalex.org/W2090141086","https://openalex.org/W2090321768","https://openalex.org/W2091080240","https://openalex.org/W2092150142","https://openalex.org/W2096073058","https://openalex.org/W2110506549","https://openalex.org/W2113983646","https://openalex.org/W2150739339","https://openalex.org/W2159721919","https://openalex.org/W2257021663","https://openalex.org/W2315633478","https://openalex.org/W2398652350","https://openalex.org/W2410493543"],"related_works":["https://openalex.org/W166589975","https://openalex.org/W2066544645","https://openalex.org/W2150739339","https://openalex.org/W4243146640","https://openalex.org/W2889836520","https://openalex.org/W2894071419","https://openalex.org/W1973063329","https://openalex.org/W2588316564","https://openalex.org/W2116412004","https://openalex.org/W2971408331"],"abstract_inverted_index":{"To":[0],"investigate":[1],"the":[2,48,58,65,73,78,96,110,119,124,131,138,145,152,162,170,176,192],"prevalence,":[3],"clinical":[4,88],"characteristics,":[5],"and":[6,25,64,105,112,169,208],"prognosis":[7,193],"of":[8,11,60,135,149,178,194],"familial":[9,74,120,153,156,195],"cases":[10],"idiopathic":[12],"dilated":[13],"cardiomyopathy":[14],"(IDC),":[15],"family":[16],"screenings":[17],"were":[18,42,83,108,116,160,185],"carried":[19],"out":[20],"in":[21,32,72,77,86,95,118,123,137,151,182],"117":[22],"IDC":[23,157,196],"patients":[24,41,107,158,183,197],"their":[26,201],"relatives.":[27],"Familial":[28],"occurrence":[29],"was":[30,62,91,130,144,167,173],"suspected":[31],"29":[33],"families":[34,37,51],"(25%).":[35],"Ten":[36],"(9%)":[38],"with":[39],"24":[40],"confirmed":[43],"to":[44,69],"be":[45,70],"familial,":[46],"but":[47,81],"other":[49,87],"19":[50],"(16%)":[52],"remained":[53],"suspected.":[54],"The":[55],"age":[56],"at":[57,175],"time":[59,177],"diagnosis":[61,179,207],"lower":[63,117,174],"cardiac":[66,171,202],"symptoms":[67,203],"tended":[68],"milder":[71],"group":[75,121],"than":[76,122,180],"non-familial":[79,125,139],"group,":[80,140],"there":[82],"no":[84,93],"differences":[85],"parameters.":[89],"There":[90],"also":[92],"difference":[94],"survival":[97,114],"rate.":[98],"However,":[99],"when":[100],"only":[101],"NYHA":[102],"class":[103],"III":[104],"IV":[106],"selected,":[109],"1-year":[111],"5-year":[113],"rates":[115],"group.":[126,154],"Congestive":[127],"heart":[128],"failure":[129],"most":[132,146],"common":[133,147],"cause":[134,148],"death":[136,143,150],"while":[141],"sudden":[142],"Among":[155],"who":[159,184],"deceased,":[161],"left":[163],"ventricular":[164],"end-diastolic":[165],"pressure":[166],"higher":[168],"index":[172],"those":[181],"still":[186],"alive.":[187],"We":[188],"conclude":[189],"that,":[190],"since":[191],"is":[198],"poor":[199],"once":[200],"become":[204],"severe,":[205],"early":[206],"treatment":[209],"are":[210],"extremely":[211],"important.":[212]},"counts_by_year":[{"year":2019,"cited_by_count":1}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
