{"id":"https://openalex.org/W175016766","doi":null,"title":"Ehlers-Danlos syndrome type IV with gastric adenocarcinoma.","display_name":"Ehlers-Danlos syndrome type IV with gastric adenocarcinoma.","publication_year":2008,"publication_date":"2008-01-01","ids":{"openalex":"https://openalex.org/W175016766","mag":"175016766","pmid":"https://pubmed.ncbi.nlm.nih.gov/18672610"},"language":"en","primary_location":{"id":"pmid:18672610","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/18672610","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of the Medical Association of Thailand = Chotmaihet thangphaet","raw_type":"Case Reports"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5012786821","display_name":"Rajyani Kanechorn Na Ayuthaya","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210087968","display_name":"Phramongkutklao Hospital","ror":"https://ror.org/007h1qz76","country_code":"TH","type":"healthcare","lineage":["https://openalex.org/I4210087968"]}],"countries":["TH"],"is_corresponding":false,"raw_author_name":"Rajyani Kanechorn Na Ayuthaya","raw_affiliation_strings":["Department ofDermatology, Phramongkutklao Hospital, Thailand"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department ofDermatology, Phramongkutklao Hospital, Thailand","institution_ids":["https://openalex.org/I4210087968"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5006581287","display_name":"Nonthaya Patthamapasphong","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nonthaya Patthamapasphong","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5026314721","display_name":"Thanyachai Sura","orcid":"https://orcid.org/0000-0002-5558-781X","observed_orcids":["https://orcid.org/0000-0002-5558-781X"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Thanyachai Sura","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5091287652","display_name":"Nucha Niumpradit","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Nucha Niumpradit","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5062186145","display_name":"Objoon Trachoo","orcid":"https://orcid.org/0000-0001-7867-3238","observed_orcids":["https://orcid.org/0000-0001-7867-3238"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Objoon Trachoo","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":2,"citation_normalized_percentile":{"value":0.0,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"91 Suppl 1","issue":null,"first_page":"S166","last_page":"71"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11310","display_name":"Connective tissue disorders research","score":0.9839000105857849,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T11310","display_name":"Connective tissue disorders research","score":0.9839000105857849,"subfield":{"id":"https://openalex.org/subfields/1311","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/13","display_name":"Biochemistry, Genetics and Molecular Biology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T10696","display_name":"Gastric Cancer Management and Outcomes","score":0.009200000204145908,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11378","display_name":"Gastrointestinal Bleeding Diagnosis and Treatment","score":0.000699999975040555,"subfield":{"id":"https://openalex.org/subfields/2715","display_name":"Gastroenterology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/ehlers-danlos-syndrome-type-iv","display_name":"Ehlers-Danlos syndrome type IV","score":0.9940000176429749},{"id":"https://openalex.org/keywords/vascular-ehlers-danlos-syndrome","display_name":"vascular Ehlers-Danlos syndrome","score":0.9929999709129333},{"id":"https://openalex.org/keywords/gastric-adenocarcinoma","display_name":"gastric adenocarcinoma","score":0.9980000257492065},{"id":"https://openalex.org/keywords/gastric-cancer","display_name":"gastric cancer","score":0.5419999957084656},{"id":"https://openalex.org/keywords/abdominal-aortic-aneurysm","display_name":"abdominal aortic aneurysm","score":0.800000011920929},{"id":"https://openalex.org/keywords/upper-gastrointestinal-bleeding","display_name":"upper gastrointestinal bleeding","score":0.8579999804496765},{"id":"https://openalex.org/keywords/neurogenic-claudication","display_name":"neurogenic claudication","score":0.8600000143051147},{"id":"https://openalex.org/keywords/compression-fractures","display_name":"compression fractures","score":0.6620000004768372},{"id":"https://openalex.org/keywords/chronic-gastritis","display_name":"chronic gastritis","score":0.7400000095367432},{"id":"https://openalex.org/keywords/cerebral-hemorrhage","display_name":"cerebral hemorrhage","score":0.9049999713897705},{"id":"https://openalex.org/keywords/gastrectomy","display_name":"gastrectomy","score":0.7080000042915344},{"id":"https://openalex.org/keywords/easy-bruising","display_name":"easy bruising","score":0.625},{"id":"https://openalex.org/keywords/cutaneous-pain","display_name":"skin pain","score":0.5920000076293945}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9758106470108032},{"id":"https://openalex.org/C2781143854","wikidata":"https://www.wikidata.org/wiki/Q938957","display_name":"Esophagogastroduodenoscopy","level":3,"score":0.6363034248352051},{"id":"https://openalex.org/C2780470880","wikidata":"https://www.wikidata.org/wiki/Q827390","display_name":"Gastrectomy","level":3,"score":0.48711442947387695},{"id":"https://openalex.org/C2779422922","wikidata":"https://www.wikidata.org/wiki/Q1029907","display_name":"Stomach","level":2,"score":0.45772701501846313},{"id":"https://openalex.org/C2780955771","wikidata":"https://www.wikidata.org/wiki/Q183425","display_name":"Abdominal pain","level":2,"score":0.4477784037590027},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.44514673948287964},{"id":"https://openalex.org/C90924648","wikidata":"https://www.wikidata.org/wiki/Q120569","display_name":"Gastroenterology","level":1,"score":0.39431118965148926},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.34957677125930786},{"id":"https://openalex.org/C121608353","wikidata":"https://www.wikidata.org/wiki/Q12078","display_name":"Cancer","level":2,"score":0.2718208432197571},{"id":"https://openalex.org/C2778451229","wikidata":"https://www.wikidata.org/wiki/Q212809","display_name":"Endoscopy","level":2,"score":0.1920817792415619}],"mesh":[{"descriptor_ui":"D000230","descriptor_name":"Adenocarcinoma","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D000230","descriptor_name":"Adenocarcinoma","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D000230","descriptor_name":"Adenocarcinoma","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":false},{"descriptor_ui":"D004535","descriptor_name":"Ehlers-Danlos Syndrome","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D004535","descriptor_name":"Ehlers-Danlos Syndrome","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false},{"descriptor_ui":"D005743","descriptor_name":"Gastrectomy","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D013274","descriptor_name":"Stomach Neoplasms","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D013274","descriptor_name":"Stomach Neoplasms","qualifier_ui":"Q000503","qualifier_name":"physiopathology","is_major_topic":false},{"descriptor_ui":"D013274","descriptor_name":"Stomach Neoplasms","qualifier_ui":"Q000601","qualifier_name":"surgery","is_major_topic":false},{"descriptor_ui":"D017809","descriptor_name":"Fatal Outcome","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D024061","descriptor_name":"Collagen Type III","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":false}],"locations_count":1,"locations":[{"id":"pmid:18672610","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/18672610","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Journal of the Medical Association of Thailand = Chotmaihet thangphaet","raw_type":"Case Reports"}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":1.0}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"grobid_xml":false,"pdf":false},"content_urls":null,"referenced_works_count":24,"referenced_works":["https://openalex.org/W168175057","https://openalex.org/W190925064","https://openalex.org/W1277787609","https://openalex.org/W1483015270","https://openalex.org/W1531218076","https://openalex.org/W1858726777","https://openalex.org/W1971345346","https://openalex.org/W1983040466","https://openalex.org/W1986503009","https://openalex.org/W2006919496","https://openalex.org/W2049479500","https://openalex.org/W2051176990","https://openalex.org/W2052656027","https://openalex.org/W2057831089","https://openalex.org/W2064680730","https://openalex.org/W2065786152","https://openalex.org/W2073976667","https://openalex.org/W2081956931","https://openalex.org/W2092030346","https://openalex.org/W2103758142","https://openalex.org/W2120771888","https://openalex.org/W2153707891","https://openalex.org/W2313594428","https://openalex.org/W4252197161"],"related_works":["https://openalex.org/W4385716164","https://openalex.org/W2029702023","https://openalex.org/W2129680123","https://openalex.org/W2408448584","https://openalex.org/W106740862","https://openalex.org/W2100884820","https://openalex.org/W2311151961","https://openalex.org/W2317430992","https://openalex.org/W2401892987","https://openalex.org/W2011623879"],"abstract_inverted_index":{"BACKGROUND:":[0],"Ehlers-Danlos":[1],"syndrome":[2],"has":[3],"many":[4],"subtypes.":[5],"The":[6],"vascular":[7,35,144],"type":[8,53,146],"(type":[9],"IV)":[10],"is":[11],"characterized":[12],"by":[13],"thin,":[14],"translucent":[15],"skin,":[16],"easy":[17,136],"bruising,":[18],"characteristic":[19],"facial":[20],"appearance,":[21],"and":[22,44,64,109,124,140,157,164],"arterial,":[23],"intestinal,":[24],"and/or":[25],"uterine":[26],"fragility.":[27],"OBJECTIVES:":[28],"To":[29],"encourage":[30],"a":[31,38],"better":[32],"understanding":[33],"of":[34,46,51,57,79,83,92,119,121],"EDS":[36,52,145],"as":[37],"basis":[39],"for":[40],"early":[41],"diagnosis,":[42],"prevention,":[43],"management":[45],"complications.":[47],"A":[48,69,143],"first":[49],"case":[50],"IV":[54,147],"with":[55,86,99],"adeno-carcinoma":[56],"the":[58,122,153],"stomach":[59,123],"in":[60,75,112],"Thailand":[61],"was":[62,66,73,117,126,148],"reported":[63],"literature":[65],"reviewed.":[67],"RESULT:":[68],"62-year-old":[70],"Thai":[71],"priest":[72],"admitted":[74],"Priest":[76],"Hospital":[77],"because":[78],"progressive":[80],"muscle":[81],"weakness":[82],"both":[84],"legs":[85],"neurogenic":[87],"claudication":[88],"from":[89,159],"compression":[90],"fracture":[91],"L1-2.":[93],"Abdominal":[94],"aortic":[95],"aneurysm":[96],"were":[97,129],"detected":[98],"upper":[100],"gastrointestinal":[101],"hemorrhage,":[102],"esophagogastroduodenoscopy":[103],"showed":[104],"diffuse":[105],"gastric":[106],"body":[107],"swelling":[108],"erythema":[110],"resulting":[111],"chronic":[113],"gastritis.":[114],"Gastric":[115],"biopsy":[116],"indicative":[118],"adenocarcinoma":[120],"gastrectomy":[125],"done.":[127],"Dermatologists":[128],"consulted":[130],"due":[131],"to":[132],"generalized":[133],"cutaneous":[134],"pain,":[135],"bruising":[137],"following":[138],"venepuncture,":[139],"EKG":[141],"padding.":[142],"diagnosed.":[149],"CONCLUSION:":[150],"After":[151],"gastrectomy,":[152],"patient":[154],"became":[155],"drowsy":[156],"unconscious":[158],"profuse":[160],"recurrent":[161],"cerebral":[162],"hemorrhage":[163],"expired.":[165]},"counts_by_year":[{"year":2020,"cited_by_count":1},{"year":2019,"cited_by_count":1}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
