{"id":"https://openalex.org/W1608024398","doi":null,"title":"Glomerulonephritis and hereditary angioedema: report of 2 cases.","display_name":"Glomerulonephritis and hereditary angioedema: report of 2 cases.","publication_year":1989,"publication_date":"1989-05-01","ids":{"openalex":"https://openalex.org/W1608024398","mag":"1608024398","pmid":"https://pubmed.ncbi.nlm.nih.gov/2736814"},"language":"en","primary_location":{"id":"pmid:2736814","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/2736814","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical nephrology","raw_type":"Case Reports"},"volume":null,"type":"article","indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5019505104","display_name":"Bernard Hory","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210087978","display_name":"Centre Hospitalier Universitaire de Besan\u00e7on","ror":"https://ror.org/0084te143","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210087978"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"B Hory","raw_affiliation_strings":["Unit of Nephrology and Internal Medicine, Chu Besan\u00e7on, France"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Unit of Nephrology and Internal Medicine, Chu Besan\u00e7on, France","institution_ids":["https://openalex.org/I4210087978"]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5024648239","display_name":"Jean Jacques Haultier","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"J J Haultier","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":1.2291,"has_fulltext":false,"cited_by_count":18,"citation_normalized_percentile":{"value":0.77617576,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":95},"biblio":{"volume":"31","issue":"5","first_page":"259","last_page":"63"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","score":0.5214999914169312,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","score":0.5214999914169312,"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":0.4187000095844269,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11029","display_name":"Renal Diseases and Glomerulopathies","score":0.05290000140666962,"subfield":{"id":"https://openalex.org/subfields/2727","display_name":"Nephrology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/hereditary-angioedema","display_name":"hereditary angioedema","score":0.9340000152587891},{"id":"https://openalex.org/keywords/c1-inhibitor-deficiency","display_name":"C1 inhibitor deficiency","score":0.8939999938011169},{"id":"https://openalex.org/keywords/glomerulonephritis","display_name":"glomerulonephritis","score":0.9599999785423279},{"id":"https://openalex.org/keywords/hereditary-complement-deficiency","display_name":"hereditary complement deficiency","score":0.7540000081062317},{"id":"https://openalex.org/keywords/immune-complex-disease","display_name":"immune complex disease","score":0.7400000095367432},{"id":"https://openalex.org/keywords/membranoproliferative-glomerulonephritis","display_name":"membranoproliferative glomerulonephritis","score":0.9490000009536743},{"id":"https://openalex.org/keywords/chronic-kidney-disease","display_name":"chronic kidney disease","score":0.7590000033378601},{"id":"https://openalex.org/keywords/kidney-transplantation","display_name":"kidney transplantation","score":0.9049999713897705},{"id":"https://openalex.org/keywords/lupus-erythematosus","display_name":"lupus erythematosus","score":0.8690000176429749},{"id":"https://openalex.org/keywords/complement-receptors","display_name":"complement receptors","score":0.44699999690055847}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.9275925159454346},{"id":"https://openalex.org/C2777788586","wikidata":"https://www.wikidata.org/wiki/Q2096745","display_name":"Hereditary angioedema","level":2,"score":0.8978597521781921},{"id":"https://openalex.org/C2781036514","wikidata":"https://www.wikidata.org/wiki/Q2299379","display_name":"Membranoproliferative glomerulonephritis","level":4,"score":0.8723042607307434},{"id":"https://openalex.org/C2777327493","wikidata":"https://www.wikidata.org/wiki/Q5156409","display_name":"Complement deficiency","level":4,"score":0.6370254755020142},{"id":"https://openalex.org/C2780368995","wikidata":"https://www.wikidata.org/wiki/Q605006","display_name":"Glomerulonephritis","level":3,"score":0.5507085919380188},{"id":"https://openalex.org/C2777995640","wikidata":"https://www.wikidata.org/wiki/Q1129007","display_name":"Angioedema","level":2,"score":0.5235354900360107},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.4655139446258545},{"id":"https://openalex.org/C2778653478","wikidata":"https://www.wikidata.org/wiki/Q1054718","display_name":"Kidney disease","level":2,"score":0.42681148648262024},{"id":"https://openalex.org/C2780091579","wikidata":"https://www.wikidata.org/wiki/Q9377","display_name":"Kidney","level":2,"score":0.41137802600860596},{"id":"https://openalex.org/C111684460","wikidata":"https://www.wikidata.org/wiki/Q334848","display_name":"Complement system","level":3,"score":0.39932864904403687},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.38449162244796753},{"id":"https://openalex.org/C16005928","wikidata":"https://www.wikidata.org/wiki/Q171171","display_name":"Dermatology","level":1,"score":0.33110707998275757},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.3254680037498474},{"id":"https://openalex.org/C8891405","wikidata":"https://www.wikidata.org/wiki/Q1059","display_name":"Immune system","level":2,"score":0.23742324113845825}],"mesh":[{"descriptor_ui":"D000293","descriptor_name":"Adolescent","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D000799","descriptor_name":"Angioedema","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D000799","descriptor_name":"Angioedema","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":true},{"descriptor_ui":"D002648","descriptor_name":"Child","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003174","descriptor_name":"Complement C1 Inactivator Proteins","qualifier_ui":"Q000172","qualifier_name":"deficiency","is_major_topic":true},{"descriptor_ui":"D005921","descriptor_name":"Glomerulonephritis","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010375","descriptor_name":"Pedigree","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:2736814","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/2736814","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Clinical nephrology","raw_type":"Case Reports"},{"id":"mag:1608024398","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/2736814","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being","score":0.9537000060081482}],"study_designs":[{"id":"https://openalex.org/study-designs/case-report","display_name":"Case Report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2049001447","https://openalex.org/W2029785303","https://openalex.org/W7096012491","https://openalex.org/W1923984612","https://openalex.org/W2000079510","https://openalex.org/W2075036685","https://openalex.org/W2045961012","https://openalex.org/W2752755020","https://openalex.org/W2906158295","https://openalex.org/W4410249277"],"abstract_inverted_index":{"Hereditary":[0],"deficiency":[1,115],"of":[2,38,55,59,103,116,129,137],"C1":[3,40],"esterase":[4],"inhibitor":[5],"(C1":[6],"INH)":[7],"responsible":[8],"for":[9],"hereditary":[10,17],"angioedema":[11],"(HAE)":[12],"is":[13],"the":[14,60,76,93,110,119,127,135],"most":[15],"common":[16],"complement":[18,117,130],"deficiency.":[19,42],"HAE":[20,108],"has":[21],"occasionally":[22],"been":[23,46],"reported":[24],"in":[25,89,105,134],"association":[26],"with":[27,31,67,107],"lupus":[28],"erythematosus":[29],"and":[30,70,92,126,131],"glomerulonephritis":[32],"(GN).":[33],"We":[34],"report":[35],"2":[36],"cases":[37,91],"GN-associated":[39],"INH":[41],"Renal":[43],"manifestations":[44],"have":[45],"discovered":[47],"respectively":[48],"6":[49],"to":[50,121],"17":[51],"years":[52],"before":[53],"onset":[54,102],"attacks.":[56],"Kidney":[57],"biopsy":[58],"1st":[61],"patient":[62,78,95],"showed":[63],"diffuse":[64],"proliferative":[65],"GN":[66,104],"a":[68,80,98,113],"rare":[69],"scattered":[71],"wire":[72],"loop":[73],"pattern":[74],"whereas":[75],"2nd":[77,94],"displayed":[79],"type":[81],"I":[82],"membranoproliferative":[83],"GN.":[84],"Chronic":[85],"renal":[86],"failure":[87],"appeared":[88],"both":[90],"recently":[96],"received":[97],"kidney":[99],"transplant.":[100],"The":[101],"patients":[106],"outline":[109],"relationship":[111],"between":[112],"genetic":[114],"components,":[118],"susceptibility":[120],"immune":[122],"complex":[123],"(IC)":[124],"disease":[125],"role":[128],"its":[132],"receptors":[133],"elimination":[136],"IC.":[138]},"counts_by_year":[{"year":2022,"cited_by_count":2},{"year":2020,"cited_by_count":1},{"year":2018,"cited_by_count":1}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}