{"id":"https://openalex.org/W15849486","doi":null,"title":"Pancytopenia in tuberous sclerosis.","display_name":"Pancytopenia in tuberous sclerosis.","publication_year":2001,"publication_date":"2001-05-01","ids":{"openalex":"https://openalex.org/W15849486","mag":"15849486","pmid":"https://pubmed.ncbi.nlm.nih.gov/11386023"},"language":"en","primary_location":{"id":"pmid:11386023","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/11386023","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Medical science monitor : international medical journal of experimental and clinical research","raw_type":"Case Reports"},"volume":null,"type":"article","indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5101509613","display_name":"Manabu Tashiro","orcid":"https://orcid.org/0000-0002-8860-6917","observed_orcids":["https://orcid.org/0000-0002-8860-6917"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"M Tashiro","raw_affiliation_strings":["Department of Internal Medicine, Urawa Municipal Hospital, Urawa, Saitama, Japan. mtashiro@mail.cc.tohoku.ac.jp","Department of Internal Medicine, Urawa Municipal Hospital, Urawa, Saitama, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Urawa Municipal Hospital, Urawa, Saitama, Japan. mtashiro@mail.cc.tohoku.ac.jp","institution_ids":[]},{"raw_affiliation_string":"Department of Internal Medicine, Urawa Municipal Hospital, Urawa, Saitama, Japan","institution_ids":[]}]},{"author_position":"middle","author":{"id":null,"display_name":"W Hirose","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"W Hirose","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5105313572","display_name":"Hiroo Hanabusa","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"H Hanabusa","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":null,"display_name":"T Takahashi","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"T Takahashi","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":null,"display_name":"H Kanki","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"H Kanki","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076212262","display_name":"Yoshiaki Asaba","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Y Asaba","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":null,"display_name":"H Hieda","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"H Hieda","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5108429067","display_name":"T Sugi","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"T Sugi","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5111694384","display_name":"Yasuyuki Tokura","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Y Tokura","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5104363298","display_name":"Kiyoaki Watanabe","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I203951103","display_name":"Keio University","ror":"https://ror.org/02kn6nx58","country_code":"JP","type":"education","lineage":["https://openalex.org/I203951103"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"K Watanabe","raw_affiliation_strings":["Keio Univ"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Keio Univ","institution_ids":["https://openalex.org/I203951103"]}]},{"author_position":"last","author":{"id":null,"display_name":"M Kawagoe","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"M Kawagoe","raw_affiliation_strings":["Urawa Municipal Hospital"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Urawa Municipal Hospital","institution_ids":[]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":1,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.0,"has_fulltext":false,"cited_by_count":4,"citation_normalized_percentile":{"value":0.00131685,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":null,"biblio":{"volume":"7","issue":"3","first_page":"444","last_page":"7"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T12049","display_name":"Tuberous Sclerosis Complex Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T12049","display_name":"Tuberous Sclerosis Complex Research","score":0.9994999766349792,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10980","display_name":"Vascular Malformations and Hemangiomas","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2746","display_name":"Surgery"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11571","display_name":"Sarcoidosis and Beryllium Toxicity Research","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2737","display_name":"Physiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/tuberous-sclerosis-complex","display_name":"tuberous sclerosis complex","score":0.9679999947547913},{"id":"https://openalex.org/keywords/pancytopenia","display_name":"pancytopenia","score":1.0},{"id":"https://openalex.org/keywords/hypersplenism","display_name":"hypersplenism","score":0.9369999766349792},{"id":"https://openalex.org/keywords/splenectomy","display_name":"splenectomy","score":0.8410000205039978},{"id":"https://openalex.org/keywords/anemia","display_name":"anemia","score":0.6069999933242798},{"id":"https://openalex.org/keywords/edema","display_name":"edema","score":0.847000002861023},{"id":"https://openalex.org/keywords/bone-hyperostosis","display_name":"bone hyperostosis","score":0.5379999876022339},{"id":"https://openalex.org/keywords/hematologic-complications","display_name":"hematologic complications","score":0.8550000190734863}],"concepts":[{"id":"https://openalex.org/C2779382419","wikidata":"https://www.wikidata.org/wiki/Q1757427","display_name":"Pancytopenia","level":3,"score":0.9356293678283691},{"id":"https://openalex.org/C2778980267","wikidata":"https://www.wikidata.org/wiki/Q1362721","display_name":"Tuberous sclerosis","level":2,"score":0.8760823607444763},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.8139740228652954},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.4845673143863678},{"id":"https://openalex.org/C2780886150","wikidata":"https://www.wikidata.org/wiki/Q152234","display_name":"Edema","level":2,"score":0.4160793423652649},{"id":"https://openalex.org/C2780007613","wikidata":"https://www.wikidata.org/wiki/Q546523","display_name":"Bone marrow","level":2,"score":0.22831672430038452},{"id":"https://openalex.org/C141071460","wikidata":"https://www.wikidata.org/wiki/Q40821","display_name":"Surgery","level":1,"score":0.20240885019302368}],"mesh":[{"descriptor_ui":"D001921","descriptor_name":"Brain","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D004487","descriptor_name":"Edema","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":false},{"descriptor_ui":"D005260","descriptor_name":"Female","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D005360","descriptor_name":"Fibula","qualifier_ui":"Q000000981","qualifier_name":"diagnostic imaging","is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007668","descriptor_name":"Kidney","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D008875","descriptor_name":"Middle Aged","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D010198","descriptor_name":"Pancytopenia","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D013154","descriptor_name":"Spleen","qualifier_ui":"Q000473","qualifier_name":"pathology","is_major_topic":false},{"descriptor_ui":"D013977","descriptor_name":"Tibia","qualifier_ui":"Q000000981","qualifier_name":"diagnostic imaging","is_major_topic":false},{"descriptor_ui":"D014057","descriptor_name":"Tomography, X-Ray Computed","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D014402","descriptor_name":"Tuberous Sclerosis","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D014402","descriptor_name":"Tuberous Sclerosis","qualifier_ui":"Q000628","qualifier_name":"therapy","is_major_topic":true},{"descriptor_ui":"D019066","descriptor_name":"Facies","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:11386023","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/11386023","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Medical science monitor : international medical journal of experimental and clinical research","raw_type":"Case Reports"},{"id":"mag:15849486","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/11386023","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"sustainable_development_goals_aurora":[{"display_name":"Good health and well-being","score":0.6899999976158142,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2403554470","https://openalex.org/W1493980018","https://openalex.org/W140444294","https://openalex.org/W2410722021","https://openalex.org/W2396687040","https://openalex.org/W2400159075","https://openalex.org/W2421023626","https://openalex.org/W2423867630","https://openalex.org/W2110112984","https://openalex.org/W2056032477"],"abstract_inverted_index":{"A":[0],"46-year-old":[1],"woman":[2],"with":[3,18],"edema":[4,36],"and":[5,27,32,105],"pancytopenia":[6,97],"was":[7,13,71,89,98],"referred":[8],"for":[9],"further":[10],"evaluation.":[11],"She":[12],"diagnosed":[14],"as":[15,22,59,61],"tuberous":[16,112,130],"sclerosis":[17,131],"clinical":[19],"manifestations":[20],"such":[21],"facial":[23],"adenoma":[24],"sebaceous,":[25],"ungual":[26],"periungual":[28],"fibroma,":[29],"subependymal":[30],"nodules":[31],"renal":[33],"angiomyolipoma.":[34],"Her":[35],"seemed":[37,93],"due":[38],"to":[39,87,123],"hypercardiac":[40],"function":[41],"induced":[42,99],"by":[43,100],"massive":[44,96],"anemia.":[45],"X-ray":[46],"revealed":[47,80],"extraordinary":[48],"thickening":[49],"of":[50,53,56,103,129],"the":[51,57,126,133],"cortex":[52],"long":[54],"bones":[55],"extremities":[58],"well":[60],"patchy":[62],"osteosclerotic":[63],"findings":[64],"in":[65,108],"vertebra,":[66],"suggesting":[67],"that":[68,94],"hematopoietic":[69],"space":[70],"significantly":[72],"reduced.":[73],"Pancytopenia":[74],"improved":[75],"after":[76],"splenectomy.":[77],"Histological":[78],"examination":[79],"several":[81],"intrasplenic":[82],"hemangiomas":[83],"but":[84],"its":[85],"relationship":[86],"hypersplenism":[88,104],"not":[90],"clear.":[91],"It":[92],"her":[95],"a":[101],"combination":[102],"significant":[106],"reduction":[107],"hematopoetic":[109],"space.":[110],"In":[111],"sclerosis,":[113],"various":[114],"systemic":[115],"complications":[116],"sometimes":[117],"induce":[118],"severe":[119],"hematological":[120,136],"abnormalities.":[121],"According":[122],"previous":[124],"literatures,":[125],"present":[127],"case":[128],"manifested":[132],"most":[134],"outstanding":[135],"complications.":[137]},"counts_by_year":[],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
