{"id":"https://openalex.org/W156106752","doi":null,"title":"[Investigation of the complement system in clinical practice].","display_name":"[Investigation of the complement system in clinical practice].","publication_year":2003,"publication_date":"2003-12-01","ids":{"openalex":"https://openalex.org/W156106752","mag":"156106752","pmid":"https://pubmed.ncbi.nlm.nih.gov/15037829"},"language":"fr","primary_location":{"id":"pmid:15037829","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/15037829","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annales de medecine interne","raw_type":"Comparative Study"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["pubmed"],"open_access":{"is_oa":false,"oa_status":"closed","oa_url":null,"any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5025683973","display_name":"V\u00e9ronique Fr\u00e9meaux\u2010Bacchi","orcid":"https://orcid.org/0000-0002-4865-8528","observed_orcids":["https://orcid.org/0000-0002-4865-8528"]},"institutions":[{"id":"https://openalex.org/I4210097159","display_name":"Assistance Publique \u2013 H\u00f4pitaux de Paris","ror":"https://ror.org/00pg5jh14","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159"]},{"id":"https://openalex.org/I4210102325","display_name":"H\u00f4pital Europ\u00e9en Georges-Pompidou","ror":"https://ror.org/016vx5156","country_code":"FR","type":"healthcare","lineage":["https://openalex.org/I4210097159","https://openalex.org/I4210102325","https://openalex.org/I4210120235"]}],"countries":["FR"],"is_corresponding":false,"raw_author_name":"V\u00e9ronique Fr\u00e9meaux-Bacchi","raw_affiliation_strings":["Service d'Immunologie Biologique, H\u00f4pital Europ\u00e9en Georges-Pompidou, Assistance Publique-H\u00f4pitaux de Paris, 20-40, rue Leblanc, 75908 Paris Cedex 15. veronique.fremeaux-bacchi@hop.egp.ap-hop-paris.fr"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Service d'Immunologie Biologique, H\u00f4pital Europ\u00e9en Georges-Pompidou, Assistance Publique-H\u00f4pitaux de Paris, 20-40, rue Leblanc, 75908 Paris Cedex 15. veronique.fremeaux-bacchi@hop.egp.ap-hop-paris.fr","institution_ids":["https://openalex.org/I4210097159","https://openalex.org/I4210102325"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5076339052","display_name":"Marie\u2010Agn\u00e8s Dragon\u2010Durey","orcid":"https://orcid.org/0000-0002-5809-8122","observed_orcids":["https://orcid.org/0000-0002-5809-8122"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Marie-Agn\u00e8s Dragon-Durey","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5063877307","display_name":"Jacques Blouin","orcid":null,"observed_orcids":[]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Jacques Blouin","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"middle","author":{"id":"https://openalex.org/A5007247451","display_name":"Luc Mouthon","orcid":"https://orcid.org/0000-0002-9838-246X","observed_orcids":["https://orcid.org/0000-0002-9838-246X","https://orcid.org/0000-0002-7021-9492"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Luc Mouthon","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]},{"author_position":"last","author":{"id":"https://openalex.org/A5075098122","display_name":"Wolf H. Fridman","orcid":"https://orcid.org/0000-0002-1332-0973","observed_orcids":["https://orcid.org/0000-0002-1332-0973"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"Wolf Herman Fridman","raw_affiliation_strings":[],"raw_orcid":null,"affiliations":[]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":null,"apc_paid":null,"fwci":0.2076,"has_fulltext":false,"cited_by_count":8,"citation_normalized_percentile":{"value":0.48349404,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":88,"max":93},"biblio":{"volume":"154","issue":"8","first_page":"529","last_page":"40"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},"topics":[{"id":"https://openalex.org/T10993","display_name":"Complement system in diseases","score":1.0,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}},{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T14245","display_name":"Biomarkers in Disease Mechanisms","score":0.0,"subfield":{"id":"https://openalex.org/subfields/2403","display_name":"Immunology"},"field":{"id":"https://openalex.org/fields/24","display_name":"Immunology and Microbiology"},"domain":{"id":"https://openalex.org/domains/1","display_name":"Life Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/complement-system","display_name":"complement system","score":1.0},{"id":"https://openalex.org/keywords/complement-deficiency","display_name":"complement deficiency","score":0.8640000224113464},{"id":"https://openalex.org/keywords/complement-activation","display_name":"complement activation","score":0.7329999804496765},{"id":"https://openalex.org/keywords/complement-c3","display_name":"complement C3","score":0.8149999976158142},{"id":"https://openalex.org/keywords/c4","display_name":"C4","score":0.9980000257492065},{"id":"https://openalex.org/keywords/classical-complement-pathway","display_name":"classical complement pathway","score":0.7289999723434448},{"id":"https://openalex.org/keywords/immune-complex-clearance","display_name":"immune complex clearance","score":0.7099999785423279},{"id":"https://openalex.org/keywords/autoimmunity","display_name":"autoimmunity","score":0.7609999775886536},{"id":"https://openalex.org/keywords/complement-consumption","display_name":"complement consumption","score":0.6119999885559082},{"id":"https://openalex.org/keywords/disease-diagnosis","display_name":"disease diagnosis","score":0.5059999823570251}],"concepts":[{"id":"https://openalex.org/C112313634","wikidata":"https://www.wikidata.org/wiki/Q7886648","display_name":"Complement (music)","level":5,"score":0.8722841739654541},{"id":"https://openalex.org/C111684460","wikidata":"https://www.wikidata.org/wiki/Q334848","display_name":"Complement system","level":3,"score":0.8212604522705078},{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.6876852512359619},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.6138461828231812},{"id":"https://openalex.org/C2777327493","wikidata":"https://www.wikidata.org/wiki/Q5156409","display_name":"Complement deficiency","level":4,"score":0.6108697652816772},{"id":"https://openalex.org/C8891405","wikidata":"https://www.wikidata.org/wiki/Q1059","display_name":"Immune system","level":2,"score":0.6057865023612976},{"id":"https://openalex.org/C2780942790","wikidata":"https://www.wikidata.org/wiki/Q372016","display_name":"Pathogenesis","level":2,"score":0.5215649008750916},{"id":"https://openalex.org/C189446657","wikidata":"https://www.wikidata.org/wiki/Q4736500","display_name":"Alternative complement pathway","level":4,"score":0.5159119367599487},{"id":"https://openalex.org/C2779134260","wikidata":"https://www.wikidata.org/wiki/Q12136","display_name":"Disease","level":2,"score":0.49916553497314453},{"id":"https://openalex.org/C171279029","wikidata":"https://www.wikidata.org/wiki/Q5128320","display_name":"Classical complement pathway","level":4,"score":0.48997679352760315},{"id":"https://openalex.org/C86803240","wikidata":"https://www.wikidata.org/wiki/Q420","display_name":"Biology","level":0,"score":0.17798811197280884},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.10316187143325806},{"id":"https://openalex.org/C54355233","wikidata":"https://www.wikidata.org/wiki/Q7162","display_name":"Genetics","level":1,"score":0.07534542679786682},{"id":"https://openalex.org/C104317684","wikidata":"https://www.wikidata.org/wiki/Q7187","display_name":"Gene","level":2,"score":0.06654277443885803},{"id":"https://openalex.org/C127716648","wikidata":"https://www.wikidata.org/wiki/Q104053","display_name":"Phenotype","level":3,"score":0.0},{"id":"https://openalex.org/C188082640","wikidata":"https://www.wikidata.org/wiki/Q1780899","display_name":"Complementation","level":4,"score":0.0}],"mesh":[{"descriptor_ui":"D000799","descriptor_name":"Angioedema","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D000799","descriptor_name":"Angioedema","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":true},{"descriptor_ui":"D001327","descriptor_name":"Autoimmune Diseases","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":true},{"descriptor_ui":"D001327","descriptor_name":"Autoimmune Diseases","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D003165","descriptor_name":"Complement System Proteins","qualifier_ui":"Q000172","qualifier_name":"deficiency","is_major_topic":true},{"descriptor_ui":"D003165","descriptor_name":"Complement System Proteins","qualifier_ui":"Q000235","qualifier_name":"genetics","is_major_topic":true},{"descriptor_ui":"D003165","descriptor_name":"Complement System Proteins","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":true},{"descriptor_ui":"D003167","descriptor_name":"Complement Activation","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003170","descriptor_name":"Complement Pathway, Alternative","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003171","descriptor_name":"Complement Pathway, Classical","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D003176","descriptor_name":"Complement C3","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D003181","descriptor_name":"Complement C4","qualifier_ui":"Q000032","qualifier_name":"analysis","is_major_topic":false},{"descriptor_ui":"D003449","descriptor_name":"Cryoglobulinemia","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D003449","descriptor_name":"Cryoglobulinemia","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D004797","descriptor_name":"Enzyme-Linked Immunosorbent Assay","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006463","descriptor_name":"Hemolytic-Uremic Syndrome","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D006463","descriptor_name":"Hemolytic-Uremic Syndrome","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":true},{"descriptor_ui":"D006579","descriptor_name":"Heterozygote","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006720","descriptor_name":"Homozygote","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D008180","descriptor_name":"Lupus Erythematosus, Systemic","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D008180","descriptor_name":"Lupus Erythematosus, Systemic","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":true},{"descriptor_ui":"D008589","descriptor_name":"Meningococcal Infections","qualifier_ui":"Q000175","qualifier_name":"diagnosis","is_major_topic":false},{"descriptor_ui":"D008589","descriptor_name":"Meningococcal Infections","qualifier_ui":"Q000276","qualifier_name":"immunology","is_major_topic":false},{"descriptor_ui":"D009345","descriptor_name":"Neisseria meningitidis","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D011414","descriptor_name":"Properdin","qualifier_ui":"Q000172","qualifier_name":"deficiency","is_major_topic":false},{"descriptor_ui":"D015941","descriptor_name":"Complement Hemolytic Activity Assay","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false}],"locations_count":2,"locations":[{"id":"pmid:15037829","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/15037829","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Annales de medecine interne","raw_type":"Comparative Study"},{"id":"mag:156106752","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/15037829","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":null,"is_accepted":false,"is_published":false,"raw_source_name":"PubMed","raw_type":null}],"best_oa_location":null,"sustainable_development_goals":[{"score":0.9391000270843506,"id":"https://metadata.un.org/sdg/3","display_name":"Good health and well-being"}],"study_designs":[],"awards":[],"funders":[],"has_content":{"pdf":false,"grobid_xml":false},"content_urls":null,"referenced_works_count":0,"referenced_works":[],"related_works":["https://openalex.org/W2002396776","https://openalex.org/W1970106147","https://openalex.org/W4255932435","https://openalex.org/W2052703083","https://openalex.org/W7203838940","https://openalex.org/W1539387514","https://openalex.org/W4388386516","https://openalex.org/W1628649756","https://openalex.org/W3106991146","https://openalex.org/W82252952"],"abstract_inverted_index":{"The":[0,46,101,126],"complement":[1,23,36,60,67,76,105,154],"system":[2],"plays":[3],"an":[4,54],"important":[5,57],"role":[6,65],"in":[7,15,22,61,68,78],"defence":[8],"of":[9,18,35,43,48,56,59,66,73,75,82,85,99,122,130,138,142],"the":[10,16,64,71,83,111,120],"host":[11],"against":[12],"infection":[13],"and":[14,41,70,80,95,119,124,156],"clearance":[17],"immune":[19],"complexes.":[20],"Defects":[21],"proteins":[24,77],"are":[25],"often":[26],"associated":[27,144],"with":[28,145,161],"infections":[29],"or":[30,107,128],"auto/immune":[31],"complex":[32],"diseases.":[33,45],"Investigation":[34],"is":[37,51,110,133,149,168],"useful":[38],"for":[39,104,153],"diagnosis":[40,79],"following":[42],"auto-immune":[44],"aim":[47],"this":[49],"Article":[50],"to":[52,136,164],"provide":[53],"overview":[55],"applications":[58,94],"medicine,":[62],"emphasizing":[63],"pathogenesis":[69],"usefulness":[72],"measurements":[74],"assessment":[81],"evolution":[84],"disease":[86],"states.":[87],"Emphasis":[88],"has":[89],"been":[90],"placed":[91],"on":[92],"practical":[93],"understanding":[96],"basic":[97],"mechanisms":[98],"disease.":[100],"best":[102],"screen":[103],"deficiencies":[106],"significant":[108],"activation":[109],"CH50,":[112],"which":[113,166],"measures":[114],"total":[115],"classical":[116],"pathway":[117],"activity":[118],"measurement":[121],"C3":[123,147],"C4.":[125],"absence":[127],"decrease":[129],"multiple":[131],"components":[132],"usually":[134],"due":[135],"consumption":[137],"complement.":[139],"Complete":[140],"lack":[141],"CH50":[143],"normal":[146],"antigen":[148],"a":[150],"strong":[151],"indication":[152],"deficiency":[155],"should":[157],"be":[158],"followed":[159],"up":[160],"further":[162],"tests":[163],"determine":[165],"component":[167],"missing.":[169]},"counts_by_year":[{"year":2017,"cited_by_count":1},{"year":2016,"cited_by_count":1}],"updated_date":"2026-11-04T10:54:05.112534","created_date":"2016-06-24T00:00:00"}
