{"id":"https://openalex.org/W1497727675","doi":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","title":"Severe chronic active giftein\u2010Barr virus infection accompanied by virus\u2010associated hemophagocytic syndrome, cerebellar ataxia and encephalitis","display_name":"Severe chronic active giftein\u2010Barr virus infection accompanied by virus\u2010associated hemophagocytic syndrome, cerebellar ataxia and encephalitis","publication_year":1998,"publication_date":"1998-07-01","ids":{"openalex":"https://openalex.org/W1497727675","doi":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","mag":"1497727675","pmid":"https://pubmed.ncbi.nlm.nih.gov/9766697"},"language":"en","primary_location":{"id":"doi:10.1046/j.1440-1819.1998.00406.x","doi":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","is_oa":true,"landing_page_url":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1046/j.1440-1819.1998.00406.x","source":{"id":"https://openalex.org/S111042112","display_name":"Psychiatry and Clinical Neurosciences","issn_l":"1323-1316","issn":["1323-1316","1440-1819"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Psychiatry and Clinical Neurosciences","raw_type":"journal-article"},"volume":null,"type":"article","is_traditional":true,"indexed_in":["crossref","pubmed"],"open_access":{"is_oa":true,"oa_status":"bronze","oa_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1046/j.1440-1819.1998.00406.x","any_repository_has_fulltext":false},"authorships":[{"author_position":"first","author":{"id":"https://openalex.org/A5106038416","display_name":"Shu\u2010ichi Yamashita","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210161538","display_name":"Kokura Memorial Hospital","ror":"https://ror.org/056tqzr82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210161538"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"SHU\u2010ICHI YAMASHITA","raw_affiliation_strings":["Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan","institution_ids":["https://openalex.org/I4210161538"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5052262118","display_name":"Chisa Murakami","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210161538","display_name":"Kokura Memorial Hospital","ror":"https://ror.org/056tqzr82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210161538"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"CHISA MURAKAMI","raw_affiliation_strings":["Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan","institution_ids":["https://openalex.org/I4210161538"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5100869119","display_name":"Yoichiro Izumi","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210161538","display_name":"Kokura Memorial Hospital","ror":"https://ror.org/056tqzr82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210161538"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"YOICHIRO IZUMI","raw_affiliation_strings":["Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan","institution_ids":["https://openalex.org/I4210161538"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5053180761","display_name":"Hitoshi Sawada","orcid":"https://orcid.org/0000-0003-4363-7696","observed_orcids":["https://orcid.org/0000-0003-4363-7696"]},"institutions":[{"id":"https://openalex.org/I4210161538","display_name":"Kokura Memorial Hospital","ror":"https://ror.org/056tqzr82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210161538"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"HITOSHI SAWADA","raw_affiliation_strings":["Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan","institution_ids":["https://openalex.org/I4210161538"]}]},{"author_position":"middle","author":{"id":null,"display_name":"YOSHIHIRO YAMAZAKI","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210161538","display_name":"Kokura Memorial Hospital","ror":"https://ror.org/056tqzr82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210161538"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"YOSHIHIRO YAMAZAKI","raw_affiliation_strings":["Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Kokura Memorial Hospital, Fukuoka, Japan","institution_ids":["https://openalex.org/I4210161538"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5071642539","display_name":"Tadaaki Yokota","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I4210161538","display_name":"Kokura Memorial Hospital","ror":"https://ror.org/056tqzr82","country_code":"JP","type":"healthcare","lineage":["https://openalex.org/I4210161538"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"TADA\u2010AKI YOKOTA","raw_affiliation_strings":["Department of Pathology, Kokura Memorial Hospital, Fukuoka, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Pathology, Kokura Memorial Hospital, Fukuoka, Japan","institution_ids":["https://openalex.org/I4210161538"]}]},{"author_position":"middle","author":{"id":"https://openalex.org/A5037129700","display_name":"Nobuhiro Matsumoto","orcid":"https://orcid.org/0000-0001-5581-5635","observed_orcids":["https://orcid.org/0000-0001-5581-5635"]},"institutions":[],"countries":[],"is_corresponding":false,"raw_author_name":"NOBUHIRO MATSUMOTO","raw_affiliation_strings":["Department of Internal Medicine, Miyazaki Shigun Ishikai Hospital, Miyazaki, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"Department of Internal Medicine, Miyazaki Shigun Ishikai Hospital, Miyazaki, Japan","institution_ids":[]}]},{"author_position":"last","author":{"id":"https://openalex.org/A5113566574","display_name":"Shigeru Matsukura","orcid":null,"observed_orcids":[]},"institutions":[{"id":"https://openalex.org/I118574687","display_name":"University of Miyazaki","ror":"https://ror.org/0447kww10","country_code":"JP","type":"education","lineage":["https://openalex.org/I118574687"]}],"countries":["JP"],"is_corresponding":false,"raw_author_name":"SHIGERU MATSUKURA","raw_affiliation_strings":["The Third Department of Internal Medicine, Miyazaki Medical College, Miyazaki, Japan"],"raw_orcid":null,"affiliations":[{"raw_affiliation_string":"The Third Department of Internal Medicine, Miyazaki Medical College, Miyazaki, Japan","institution_ids":["https://openalex.org/I118574687"]}]}],"institutions":[],"countries_distinct_count":1,"institutions_distinct_count":2,"corresponding_author_ids":[],"corresponding_institution_ids":[],"apc_list":{"value":3240,"currency":"USD","value_usd":3240},"apc_paid":null,"fwci":0.7402,"has_fulltext":true,"cited_by_count":28,"citation_normalized_percentile":{"value":0.71276924,"is_in_top_1_percent":false,"is_in_top_10_percent":false},"cited_by_percentile_year":{"min":87,"max":95},"biblio":{"volume":"52","issue":"4","first_page":"449","last_page":"452"},"is_retracted":false,"is_paratext":false,"is_xpac":false,"primary_topic":{"id":"https://openalex.org/T10685","display_name":"Viral-associated cancers and disorders","score":0.9038000106811523,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},"topics":[{"id":"https://openalex.org/T10685","display_name":"Viral-associated cancers and disorders","score":0.9038000106811523,"subfield":{"id":"https://openalex.org/subfields/2730","display_name":"Oncology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T10981","display_name":"Cytomegalovirus and herpesvirus research","score":0.048900000751018524,"subfield":{"id":"https://openalex.org/subfields/2713","display_name":"Epidemiology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}},{"id":"https://openalex.org/T11616","display_name":"Autoimmune and Inflammatory Disorders Research","score":0.011800000444054604,"subfield":{"id":"https://openalex.org/subfields/2720","display_name":"Hematology"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"}}],"keywords":[{"id":"https://openalex.org/keywords/chronic-active-epstein-barr-virus-infection","display_name":"chronic active Epstein-Barr virus infection","score":0.9710000157356262},{"id":"https://openalex.org/keywords/hemophagocytic-lymphohistiocytosis","display_name":"hemophagocytic lymphohistiocytosis","score":0.9580000042915344},{"id":"https://openalex.org/keywords/cerebellar-ataxia","display_name":"cerebellar ataxia","score":0.9369999766349792},{"id":"https://openalex.org/keywords/encephalitis","display_name":"encephalitis","score":0.8930000066757202},{"id":"https://openalex.org/keywords/panencephalitis","display_name":"panencephalitis","score":0.9039999842643738},{"id":"https://openalex.org/keywords/brain-abscess","display_name":"brain abscess","score":0.9279999732971191},{"id":"https://openalex.org/keywords/disseminated-intravascular-coagulation","display_name":"disseminated intravascular coagulation","score":0.9440000057220459},{"id":"https://openalex.org/keywords/rhabdomyolysis","display_name":"rhabdomyolysis","score":0.9139999747276306},{"id":"https://openalex.org/keywords/acute-kidney-injury","display_name":"acute kidney injury","score":0.8019999861717224},{"id":"https://openalex.org/keywords/chronic-hepatitis","display_name":"chronic hepatitis","score":0.550000011920929},{"id":"https://openalex.org/keywords/fever-of-unknown-origin","display_name":"fever of unknown origin","score":0.5440000295639038},{"id":"https://openalex.org/keywords/antiviral-treatment-failure","display_name":"antiviral treatment failure","score":0.5120000243186951}],"concepts":[{"id":"https://openalex.org/C71924100","wikidata":"https://www.wikidata.org/wiki/Q11190","display_name":"Medicine","level":0,"score":0.7558979988098145},{"id":"https://openalex.org/C83455156","wikidata":"https://www.wikidata.org/wiki/Q199615","display_name":"Encephalitis","level":3,"score":0.6507722735404968},{"id":"https://openalex.org/C2780906641","wikidata":"https://www.wikidata.org/wiki/Q213373","display_name":"Ataxia","level":2,"score":0.5882537961006165},{"id":"https://openalex.org/C2776715498","wikidata":"https://www.wikidata.org/wiki/Q11426176","display_name":"Prednisolone","level":2,"score":0.4464532434940338},{"id":"https://openalex.org/C203014093","wikidata":"https://www.wikidata.org/wiki/Q101929","display_name":"Immunology","level":1,"score":0.4416189193725586},{"id":"https://openalex.org/C2780494569","wikidata":"https://www.wikidata.org/wiki/Q5384031","display_name":"Epstein\u2013Barr virus infection","level":4,"score":0.4409577250480652},{"id":"https://openalex.org/C2522874641","wikidata":"https://www.wikidata.org/wiki/Q808","display_name":"Virus","level":2,"score":0.39767980575561523},{"id":"https://openalex.org/C142724271","wikidata":"https://www.wikidata.org/wiki/Q7208","display_name":"Pathology","level":1,"score":0.36798352003097534},{"id":"https://openalex.org/C159047783","wikidata":"https://www.wikidata.org/wiki/Q7215","display_name":"Virology","level":1,"score":0.3477841019630432},{"id":"https://openalex.org/C2781375147","wikidata":"https://www.wikidata.org/wiki/Q6900","display_name":"Epstein\u2013Barr virus","level":3,"score":0.2073773741722107},{"id":"https://openalex.org/C126322002","wikidata":"https://www.wikidata.org/wiki/Q11180","display_name":"Internal medicine","level":1,"score":0.20475682616233826},{"id":"https://openalex.org/C118552586","wikidata":"https://www.wikidata.org/wiki/Q7867","display_name":"Psychiatry","level":1,"score":0.0}],"mesh":[{"descriptor_ui":"D000328","descriptor_name":"Adult","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D001922","descriptor_name":"Brain Abscess","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D002524","descriptor_name":"Cerebellar Ataxia","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D002908","descriptor_name":"Chronic Disease","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D006801","descriptor_name":"Humans","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D007244","descriptor_name":"Infectious Mononucleosis","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false},{"descriptor_ui":"D008297","descriptor_name":"Male","qualifier_ui":null,"qualifier_name":null,"is_major_topic":false},{"descriptor_ui":"D015616","descriptor_name":"Histiocytosis, Non-Langerhans-Cell","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D018792","descriptor_name":"Encephalitis, Viral","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":true},{"descriptor_ui":"D020031","descriptor_name":"Epstein-Barr Virus Infections","qualifier_ui":"Q000150","qualifier_name":"complications","is_major_topic":true},{"descriptor_ui":"D058186","descriptor_name":"Acute Kidney Injury","qualifier_ui":"Q000209","qualifier_name":"etiology","is_major_topic":false}],"locations_count":2,"locations":[{"id":"doi:10.1046/j.1440-1819.1998.00406.x","doi":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","is_oa":true,"landing_page_url":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1046/j.1440-1819.1998.00406.x","source":{"id":"https://openalex.org/S111042112","display_name":"Psychiatry and Clinical Neurosciences","issn_l":"1323-1316","issn":["1323-1316","1440-1819"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Psychiatry and Clinical Neurosciences","raw_type":"journal-article"},{"id":"pmid:9766697","doi":null,"is_oa":false,"landing_page_url":"https://pubmed.ncbi.nlm.nih.gov/9766697","pdf_url":null,"source":{"id":"https://openalex.org/S4306525036","display_name":"PubMed","issn_l":null,"issn":null,"is_oa":false,"is_in_doaj":false,"is_core":false,"listed_in":[],"host_organization":"https://openalex.org/I1299303238","host_organization_name":"National Institutes of Health","host_organization_lineage":["https://openalex.org/I1299303238"],"host_organization_lineage_names":[],"type":"repository"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Psychiatry and clinical neurosciences","raw_type":"Case Reports"}],"best_oa_location":{"id":"doi:10.1046/j.1440-1819.1998.00406.x","doi":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","is_oa":true,"landing_page_url":"https://doi.org/10.1046/j.1440-1819.1998.00406.x","pdf_url":"https://onlinelibrary.wiley.com/doi/pdfdirect/10.1046/j.1440-1819.1998.00406.x","source":{"id":"https://openalex.org/S111042112","display_name":"Psychiatry and Clinical Neurosciences","issn_l":"1323-1316","issn":["1323-1316","1440-1819"],"is_oa":false,"is_in_doaj":false,"is_core":true,"listed_in":["cwts-core","dongbi-b","doyens","jufo-2","ki-jl-1","medline","norway-1","poland-100","russia-white-list-1","vabb-shw"],"host_organization":"https://openalex.org/P4310320595","host_organization_name":"Wiley","host_organization_lineage":["https://openalex.org/P4310320595"],"host_organization_lineage_names":["Wiley"],"type":"journal"},"license":null,"license_id":null,"version":"publishedVersion","is_accepted":true,"is_published":true,"raw_source_name":"Psychiatry and Clinical Neurosciences","raw_type":"journal-article"},"sustainable_development_goals":[{"display_name":"Good health and well-being","score":1.0,"id":"https://metadata.un.org/sdg/3"}],"study_designs":[{"display_name":"Case Report","id":"https://openalex.org/study-designs/case-report"}],"awards":[],"funders":[],"has_content":{"pdf":true,"grobid_xml":true},"content_urls":{"pdf":"https://content.openalex.org/works/W1497727675.pdf","grobid_xml":"https://content.openalex.org/works/W1497727675.grobid-xml"},"referenced_works_count":14,"referenced_works":["https://openalex.org/W132108989","https://openalex.org/W1971625462","https://openalex.org/W1986981741","https://openalex.org/W1990424528","https://openalex.org/W1991841540","https://openalex.org/W2001326592","https://openalex.org/W2019867373","https://openalex.org/W2054675409","https://openalex.org/W2058064769","https://openalex.org/W2078499703","https://openalex.org/W2094532693","https://openalex.org/W2145714404","https://openalex.org/W2163247444","https://openalex.org/W2329541778"],"related_works":["https://openalex.org/W2089997116","https://openalex.org/W3118786047","https://openalex.org/W2314863973","https://openalex.org/W2513063623","https://openalex.org/W186609631","https://openalex.org/W158736990","https://openalex.org/W1981428500","https://openalex.org/W2398956282","https://openalex.org/W2965159685","https://openalex.org/W2067377321"],"abstract_inverted_index":{"We":[0],"present":[1],"a":[2],"rare":[3],"case":[4],"of":[5,32,69,86],"chronic":[6,38,45,96],"active":[7,39],"Epstein-Barr":[8],"virus":[9,51],"(EBV)":[10],"infection":[11],"showing":[12],"various":[13],"clinical":[14],"outcomes.":[15],"A":[16],"26-year-old":[17],"man":[18],"was":[19,75],"admitted":[20],"to":[21,25,35,77,92],"our":[22],"hospital":[23],"due":[24],"persistent":[26],"fever":[27],"and":[28,64],"dyspnea.":[29],"Serologic":[30],"response":[31],"the":[33,83],"patient":[34],"EBV":[36,97],"indicated":[37],"infection.":[40,98],"He":[41],"showed":[42],"pleuritis,":[43],"parotitis,":[44],"hepatic":[46],"dysfunction,":[47],"disseminated":[48],"intravascular":[49],"coagulation,":[50],"associated":[52,94],"hemophaghocytic":[53],"syndrome,":[54],"acute":[55,57,60],"rhabdomyolysis,":[56],"renal":[58],"failure,":[59],"cerebellar":[61,88],"ataxia,":[62],"encephalitis":[63],"multiple":[65],"brain":[66],"abscesses.":[67],"None":[68],"acyclovir,":[70],"gancyclovir,":[71],"prednisolone":[72],"or":[73],"interleukin-2":[74],"effectual":[76],"abolish":[78],"those":[79],"abnormalities.":[80],"This":[81],"is":[82],"first":[84],"report":[85],"transient":[87],"ataxia":[89],"which":[90],"aggravated":[91],"panencephalitis":[93],"with":[95]},"counts_by_year":[{"year":2025,"cited_by_count":2},{"year":2024,"cited_by_count":2},{"year":2023,"cited_by_count":1},{"year":2021,"cited_by_count":1},{"year":2014,"cited_by_count":2},{"year":2013,"cited_by_count":2}],"updated_date":"2026-10-31T12:09:11.096373","created_date":"2016-06-24T00:00:00"}
