{"id":"https://openalex.org/T12199","display_name":"Vascular Anomalies and Treatments","description":"This cluster of papers focuses on the diagnosis and management of hereditary hemorrhagic telangiectasia (HHT), a genetic disorder characterized by vascular malformations. It covers topics such as genetics, pulmonary arteriovenous malformations, embolization, epistaxis, liver involvement, SMAD4 mutations, and vascular anomalies.","keywords":[{"id":"https://openalex.org/keywords/hereditary-hemorrhagic-telangiectasia","display_name":"hereditary hemorrhagic telangiectasia","score":0.7164},{"id":"https://openalex.org/keywords/pulmonary-arteriovenous-malformation","display_name":"pulmonary arteriovenous malformation","score":0.7371},{"id":"https://openalex.org/keywords/bronchial-artery-embolization","display_name":"bronchial artery embolization","score":0.4177},{"id":"https://openalex.org/keywords/massive-hemoptysis","display_name":"massive hemoptysis","score":0.282},{"id":"https://openalex.org/keywords/alk1","display_name":"ALK1","score":0.2495},{"id":"https://openalex.org/keywords/recurrent-epistaxis","display_name":"recurrent epistaxis","score":0.3839},{"id":"https://openalex.org/keywords/posterior-epistaxis","display_name":"posterior epistaxis","score":0.5473},{"id":"https://openalex.org/keywords/epistaxis-management","display_name":"epistaxis management","score":0.555},{"id":"https://openalex.org/keywords/nasal-telangiectasia","display_name":"nasal telangiectasia","score":0.8573},{"id":"https://openalex.org/keywords/recurrent-hemoptysis","display_name":"recurrent hemoptysis","score":0.2655},{"id":"https://openalex.org/keywords/hepatic-arteriovenous-malformations","display_name":"hepatic arteriovenous malformations","score":0.6308},{"id":"https://openalex.org/keywords/curacao-criteria","display_name":"Cura\u00e7ao criteria","score":0.959},{"id":"https://openalex.org/keywords/nasal-hemorrhage","display_name":"nasal hemorrhage","score":0.2702},{"id":"https://openalex.org/keywords/bronchial-artery-aneurysm","display_name":"bronchial artery aneurysm","score":0.3224},{"id":"https://openalex.org/keywords/epistaxis-treatment","display_name":"epistaxis treatment","score":0.4893},{"id":"https://openalex.org/keywords/refractory-epistaxis","display_name":"refractory epistaxis","score":0.5797},{"id":"https://openalex.org/keywords/vascular-dysplasia","display_name":"vascular dysplasia","score":0.4385},{"id":"https://openalex.org/keywords/osler-s-disease","display_name":"Osler's disease","score":0.3859},{"id":"https://openalex.org/keywords/pulmonary-vascular-malformation","display_name":"pulmonary vascular malformation","score":0.4686},{"id":"https://openalex.org/keywords/bronchial-arteriography","display_name":"bronchial arteriography","score":0.2893},{"id":"https://openalex.org/keywords/intractable-epistaxis","display_name":"intractable epistaxis","score":0.6474},{"id":"https://openalex.org/keywords/anterior-epistaxis","display_name":"anterior epistaxis","score":0.4976},{"id":"https://openalex.org/keywords/embolotherapy","display_name":"embolotherapy","score":0.2229},{"id":"https://openalex.org/keywords/hereditary-telangiectasia","display_name":"hereditary telangiectasia","score":0.4542},{"id":"https://openalex.org/keywords/hemoptysis-recurrence","display_name":"hemoptysis recurrence","score":0.5183}],"legacy_keywords":"Hereditary Hemorrhagic Telangiectasia; Diagnosis; Management; Genetics; Pulmonary Arteriovenous Malformations; Embolization; Epistaxis; Liver Involvement; SMAD4 Mutations; Vascular Anomalies","ids":{"openalex":"https://openalex.org/T12199","wikipedia":"https://en.wikipedia.org/wiki/Hereditary_hemorrhagic_telangiectasia"},"subfield":{"id":"https://openalex.org/subfields/2716","display_name":"Genetics"},"field":{"id":"https://openalex.org/fields/27","display_name":"Medicine"},"domain":{"id":"https://openalex.org/domains/4","display_name":"Health Sciences"},"siblings":[{"id":"https://openalex.org/T10129","display_name":"Glioma Diagnosis and Treatment"},{"id":"https://openalex.org/T10176","display_name":"Mesenchymal stem cell research"},{"id":"https://openalex.org/T10554","display_name":"Hemoglobinopathies and Related Disorders"},{"id":"https://openalex.org/T11157","display_name":"Chronic Lymphocytic Leukemia Research"},{"id":"https://openalex.org/T11628","display_name":"Myeloproliferative Neoplasms: Diagnosis and Treatment"},{"id":"https://openalex.org/T11917","display_name":"Coagulation, Bradykinin, Polyphosphates, and Angioedema"},{"id":"https://openalex.org/T12400","display_name":"Neurogenetic and Muscular Disorders Research"},{"id":"https://openalex.org/T13738","display_name":"Congenital Ear and Nasal Anomalies"}],"works_count":17240,"cited_by_count":163251,"works_api_url":"https://api.openalex.org/works?filter=topics.id:T12199","updated_date":"2026-10-21T03:01:35","created_date":"2024-01-23T15:27:13"}
